How to mitigate neurological and cardiac decompensation in Leigh syndrome: Can nicotinamide riboside be an answer? by Alessandro Prigione, Carlo Viscomi

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Mitochondrial Neurodegeneration by Massimo Zeviani, Carlo Viscomi

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Molecular Research on Mitochondrial Dysfunction by Carlo Viscomi, Maria Eugenia Soriano

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Mitochondrial Neurodegeneration: Lessons from <i>Drosophila melanogaster</i> Models by Michele Brischigliaro, Erika Fernandez-Vizarra, Carlo Viscomi

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Measurement of mitochondrial respiratory chain enzymatic activities in Drosophila melanogaster samples by Michele Brischigliaro, Elena Frigo, Erika Fernandez-Vizarra, Paolo Bernardi, Carlo Viscomi

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A Single Intravenous Injection of AAV-PHP.B-hNDUFS4 Ameliorates the Phenotype of Ndufs4−/− Mice by Pedro Silva-Pinheiro, Raffaele Cerutti, Marta Luna-Sanchez, Massimo Zeviani, Carlo Viscomi

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Structural rather than catalytic role for mitochondrial respiratory chain supercomplexes by Michele Brischigliaro, Alfredo Cabrera-Orefice, Susanne Arnold, Carlo Viscomi, Massimo Zeviani, Erika Fernández-Vizarra

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Role of PITRM1 in Mitochondrial Dysfunction and Neurodegeneration by Dario Brunetti, Alessia Catania, Carlo Viscomi, Michela Deleidi, Laurence A. Bindoff, Daniele Ghezzi, Massimo Zeviani

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Data on cytochrome c oxidase assembly in mice and human fibroblasts or tissues induced by SURF1 defect by Nikola Kovářová, Petr Pecina, Hana Nůsková, Marek Vrbacký, Massimo Zeviani, Tomáš Mráček, Carlo Viscomi, Josef Houštěk

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Rapamycin rescues mitochondrial myopathy via coordinated activation of autophagy and lysosomal biogenesis by Gabriele Civiletto, Sukru Anil Dogan, Raffaele Cerutti, Gigliola Fagiolari, Maurizio Moggio, Costanza Lamperti, Cristiane Benincá, Carlo Viscomi, Massimo Zeviani

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The homeostatic dynamics of feeding behaviour identify novel mechanisms of anorectic agents. by Thomas M McGrath, Eleanor Spreckley, Aina Fernandez Rodriguez, Carlo Viscomi, Amin Alamshah, Elina Akalestou, Kevin G Murphy, Nick S Jones

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Evolution meets disease: penetrance and functional epistasis of mitochondrial tRNA mutations. by Raquel Moreno-Loshuertos, Gustavo Ferrín, Rebeca Acín-Pérez, M Esther Gallardo, Carlo Viscomi, Acisclo Pérez-Martos, Massimo Zeviani, Patricio Fernández-Silva, José Antonio Enríquez

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Mitochondrial Cytochrome c Oxidase Defects Alter Cellular Homeostasis of Transition Metals by Michele Brischigliaro, Michele Brischigliaro, Denis Badocco, Rodolfo Costa, Rodolfo Costa, Rodolfo Costa, Carlo Viscomi, Massimo Zeviani, Massimo Zeviani, Paolo Pastore, Erika Fernández-Vizarra, Erika Fernández-Vizarra

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APOPT1/COA8 assists COX assembly and is oppositely regulated by UPS and ROS by Alba Signes, Raffaele Cerutti, Anna S Dickson, Cristiane Benincá, Elizabeth C Hinchy, Daniele Ghezzi, Rosalba Carrozzo, Enrico Bertini, Michael P Murphy, James A Nathan, Carlo Viscomi, Erika Fernandez‐Vizarra, Massimo Zeviani

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Exploiting pyocyanin to treat mitochondrial disease due to respiratory complex III dysfunction by Roberta Peruzzo, Samantha Corrà, Roberto Costa, Michele Brischigliaro, Tatiana Varanita, Lucia Biasutto, Chiara Rampazzo, Daniele Ghezzi, Luigi Leanza, Mario Zoratti, Massimo Zeviani, Cristiano De Pittà, Carlo Viscomi, Rodolfo Costa, Ildikò Szabò

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Drosophila Mpv17 forms an ion channel and regulates energy metabolism by Samantha Corrà, Vanessa Checchetto, Michele Brischigliaro, Chiara Rampazzo, Emanuela Bottani, Cristina Gagliani, Katia Cortese, Cristiano De Pittà, Marco Roverso, Diego De Stefani, Sara Bogialli, Massimo Zeviani, Carlo Viscomi, Ildiko Szabò, Rodolfo Costa

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Zebrafish polg2 knock-out recapitulates human POLG-disorders; implications for drug treatment by Raquel Brañas Casas, Alessandro Zuppardo, Giovanni Risato, Alberto Dinarello, Rudy Celeghin, Camilla Fontana, Eleonora Grelloni, Alexandru Ionut Gilea, Carlo Viscomi, Andrea Rasola, Luisa Dalla Valle, Tiziana Lodi, Enrico Baruffini, Nicola Facchinello, Francesco Argenton, Natascia Tiso

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NAD+ repletion with niacin counteracts cancer cachexia by Marc Beltrà, Noora Pöllänen, Claudia Fornelli, Kialiina Tonttila, Myriam Y. Hsu, Sandra Zampieri, Lucia Moletta, Samantha Corrà, Paolo E. Porporato, Riikka Kivelä, Carlo Viscomi, Marco Sandri, Juha J. Hulmi, Roberta Sartori, Eija Pirinen, Fabio Penna

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PPAR-gamma agonist pioglitazone recovers mitochondrial quality control in fibroblasts from PITRM1-deficient patients by Alessia Di Donfrancesco, Christian Berlingieri, Marta Giacomello, Marta Giacomello, Chiara Frascarelli, Ana Paula Magalhaes Rebelo, Laurence A. Bindoff, Segel Reeval, Paul Renbaum, Filippo M. Santorelli, Giulia Massaro, Carlo Viscomi, Massimo Zeviani, Daniele Ghezzi, Daniele Ghezzi, Emanuela Bottani, Dario Brunetti, Dario Brunetti

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Metabolic effects of bezafibrate in mitochondrial disease by Hannah Steele, Aurora Gomez‐Duran, Angela Pyle, Sila Hopton, Jane Newman, Renae J Stefanetti, Sarah J Charman, Jehill D Parikh, Langping He, Carlo Viscomi, Djordje G Jakovljevic, Kieren G Hollingsworth, Alan J Robinson, Robert W Taylor, Leonardo Bottolo, Rita Horvath, Patrick F Chinnery

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