In vitro functional rescue by ivacaftor of an ABCB11 variant involved in PFIC2 and intrahepatic cholestasis of pregnancy per Elodie Mareux, Martine Lapalus, Amel Ben-Saad, Isabelle Callebaut, Thomas Falguières, Emmanuel Gonzales, Emmanuel Jacquemin

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Increased incidence of seronegative autoimmune hepatitis in children during SARS-CoV-2 pandemia period per Muriel Schmutz, Suzanne Chartier, Thierry Leblanc, Charlotte Mussini, Antoine Gardin, Antoine Gardin, Antoine Gardin, Emmanuel Gonzales, Emmanuel Gonzales, Emmanuel Gonzales, Anne-Marie Roque-Afonso, Anne-Marie Roque-Afonso, Solene Le Cam, Geraldine Hery, Benedicte Neven, Benedicte Neven, Ramy Charbel, Jean-Pierre Vartanian, Emmanuel Jacquemin, Emmanuel Jacquemin, Emmanuel Jacquemin, Guillaume Morelle, Guillaume Morelle, Marion Almes, Marion Almes, Marion Almes

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CD25 appears non essential for human peripheral T(reg) maintenance in vivo. per Marie-Ghislaine de Goër de Herve, Emmanuel Gonzales, Houria Hendel-Chavez, Jean-Luc Décline, Olivia Mourier, Karim Abbed, Emmanuel Jacquemin, Yassine Taoufik

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Cholic acid for primary bile acid synthesis defects: a life-saving therapy allowing a favorable outcome in adulthood per Emmanuel Gonzales, Lorenza Matarazzo, Stéphanie Franchi-Abella, Alain Dabadie, Joseph Cohen, Dalila Habes, Sophie Hillaire, Catherine Guettier, Anne-Marie Taburet, Anne Myara, Emmanuel Jacquemin

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Long-term outcome of combined radiologic and surgical strategy for the management of biliary complications after pediatric liver transplantation per Ana M. Calinescu, Sébastien Monluc, Stephanie Franchi-Abella, Dalila Habes, Gabrielle Weber, Marion F. Almes, Jerome Waguet, Emmanuel Jacquemin, Virginie Fouquet, Jordi Miatello, Geraldine Hery, Catherine Baujard, Emmanuel Gonzales, Sophie Branchereau, Florent Guérin

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Identification of new correctors for traffic-defective ABCB4 variants by a high-content screening approach per Mounia Lakli, Julie Dumont, Virginie Vauthier, Julie Charton, Veronica Crespi, Manon Banet, Yosra Riahi, Amel Ben Saad, Elodie Mareux, Martine Lapalus, Emmanuel Gonzales, Emmanuel Jacquemin, Florent Di Meo, Benoit Deprez, Florence Leroux, Thomas Falguières

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Placental growth factor modulates endothelial NO production and exacerbates experimental hepatopulmonary syndrome per Fabien Robert, Feriel Benchenouf, My Ngoc Ha, Alessandra Cuomo, Mina Ottaviani, Maxime Surbier, Raphaël Thuillet, Corinne Normand, Florent Dumont, Céline Verstuyft, Frederic Fiore, Frederic Guinut, Marc Humbert, Audrey Coilly, Emmanuel Gonzales, Olivier Sitbon, Ly Tu, Christophe Guignabert, Laurent Savale

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Targeted-Capture Next-Generation Sequencing in Diagnosis Approach of Pediatric Cholestasis per Marion Almes, Anne Spraul, Mathias Ruiz, Muriel Girard, Bertrand Roquelaure, Nolwenn Laborde, Fréderic Gottrand, Anne Turquet, Thierry Lamireau, Alain Dabadie, Marjorie Bonneton, Alice Thebaut, Babara Rohmer, Florence Lacaille, Pierre Broué, Alexandre Fabre, Karine Mention-Mulliez, Jérôme Bouligand, Emmanuel Jacquemin, Emmanuel Gonzales

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Outcomes of 38 patients with PFIC3: Impact of genotype and of response to ursodeoxycholic acid therapy per Emmanuel Gonzales, Antoine Gardin, Marion Almes, Amaria Darmellah-Remil, Hanh Seguin, Charlotte Mussini, Stéphanie Franchi-Abella, Mathieu Duché, Oanez Ackermann, Alice Thébaut, Dalila Habes, Bogdan Hermeziu, Martine Lapalus, Thomas Falguières, Jean-Philippe Combal, Bernard Benichou, Sonia Valero, Anne Davit-Spraul, Emmanuel Jacquemin

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International registry of congenital porto-systemic shunts: a multi-centre, retrospective and prospective registry of neonates, children and adults with congenital porto-systemic s... per Simona Korff, Khaled Mostaguir, Maurice Beghetti, Lorenzo D’Antiga, Dominique Debray, Stéphanie Franchi-Abella, Emmanuel Gonzales, Florent Guerin, Anne-Lise Hachulla, Virginie Lambert, Periklis Makrythanasis, Nicolas Roduit, Laurent Savale, Marie-Victoire Senat, Joël Spaltenstein, Frank van Steenbeek, Barbara E. Wildhaber, Marcel Zwahlen, Valérie A. McLin

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∆4-3-oxo-5β-reductase deficiency: favorable outcome in 16 patients treated with cholic acid per Antoine Gardin, Mathias Ruiz, Jan Beime, Mara Cananzi, Margarete Rathert, Barbara Rohmer, Enke Grabhorn, Marion Almes, Veena Logarajah, Luis Peña-Quintana, Thomas Casswall, Amaria Darmellah-Remil, Ana Reyes-Domínguez, Emna Barkaoui, Loreto Hierro, Carolina Baquero-Montoya, Ulrich Baumann, Björn Fischler, Emmanuel Gonzales, Anne Davit-Spraul, Sophie Laplanche, Emmanuel Jacquemin

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Single-cell multiomics reveals the interplay of clonal evolution and cellular plasticity in hepatoblastoma per Amélie Roehrig, Theo Z. Hirsch, Aurore Pire, Guillaume Morcrette, Barkha Gupta, Charles Marcaillou, Sandrine Imbeaud, Christophe Chardot, Emmanuel Gonzales, Emmanuel Jacquemin, Masahiro Sekiguchi, Junko Takita, Genta Nagae, Eiso Hiyama, Florent Guérin, Monique Fabre, Isabelle Aerts, Sophie Taque, Véronique Laithier, Sophie Branchereau, Catherine Guettier, Laurence Brugières, Brice Fresneau, Jessica Zucman-Rossi, Eric Letouzé

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Expert management of congenital portosystemic shunts and their complicationsKey points per Valérie Anne McLin, Stéphanie Franchi-Abella, Timothée Brütsch, Atessa Bahadori, Valeria Casotti, Jean de Ville de Goyet, Grégoire Dumery, Emmanuel Gonzales, Florent Guérin, Sebastien Hascoet, Nigel Heaton, Béatrice Kuhlmann, Frédéric Lador, Virginie Lambert, Paolo Marra, Aurélie Plessier, Alberto Quaglia, Anne-Laure Rougemont, Laurent Savale, Moinak Sen Sarma, Olivier Sitbon, Riccardo Antonio Superina, Hajime Uchida, Mirjam van Albada, Hubert Petrus Johannes van der Doef, Valérie Vilgrain, Julie Wacker, Nitash Zwaveling, Dominique Debray, Barbara Elisabeth Wildhaber

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Interim results from an ongoing, open-label, single-arm trial of odevixibat in progressive familial intrahepatic cholestasis per Richard J. Thompson, Reha Artan, Ulrich Baumann, Pier Luigi Calvo, Piotr Czubkowski, Buket Dalgic, Lorenzo D’Antiga, Angelo Di Giorgio, Özlem Durmaz, Emmanuel Gonzalès, Tassos Grammatikopoulos, Girish Gupte, Winita Hardikar, Roderick H.J. Houwen, Binita M. Kamath, Saul J. Karpen, Florence Lacaille, Alain Lachaux, Elke Lainka, Kathleen M. Loomes, Cara L. Mack, Jan P. Mattsson, Patrick McKiernan, Quanhong Ni, Hasan Özen, Sanjay R. Rajwal, Bertrand Roquelaure, Eyal Shteyer, Etienne Sokal, Ronald J. Sokol, Nisreen Soufi, Ekkehard Sturm, Mary Elizabeth Tessier, Wendy L. van der Woerd, Henkjan J. Verkade, Jennifer M. Vittorio, Terese Wallefors, Natalie Warholic, Qifeng Yu, Patrick Horn, Lise Kjems

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Prevalence, management and efficacy of treatment in portal vein obstruction after paediatric liver transplantation: protocol of the retrospective international multicentre PORTAL r... per Barbara E Wildhaber, Martin de Santibañes, Victoria Ardiles, Ruben H J de Kleine, Raj Prasad, Bhargava Mullapudi, Jai Patel, Reinoud P H Bokkers, Ekkehard Sturm, Simon McGuirk, Girish Gupte, John McCall, Richard J Hendrickson, Winita Hardikar, Helen Evans, Khalid Sharif, Marumbo Mtegha, Amar Mukund, David Duncan, Emmanuel Gonzales, Marco Spada, Mureo Kasahara, Denise Aldrian, Bader A Alfares, Hubert P J van der Doef, Thomas Casswall, Greg Nowak, Martin Delle, Valeria Berchtold, Georg F Vogel, Piotr Kaliciński, Malgorzata Markiewicz-Kijewska, Adam Kolesnik, Jesús Q Bernabeu, María Mercadal Hally, Mauricio Larrarte K, Paolo Marra, Michela Bravi, Domenico Pinelli, Seisuke Sakamoto, Hajime Uchida, Vidyadhar Mali, Marion Aw, Stéphanie Franchi-Abella, Florent Guérin, Guillermo Cervio, Julia Minetto, Sergio Sierre, Jimmy Walker Uno, Steffen Hartleif, Cristina T Ferreira, Luiza S Nader, Marco Farina, Catalina Jaramillo, Manuel I Rodriguez-Davalos, Peter Feola, Amit A Shah, Phoebe M Wood, Michael R Acord, Ryan T Fischer, Rajeev Khanna, Viniyendra Pamecha, Gilda Porta, Tommaso Alterio, Giuseppe Maggiore, Marisa Beretta, Rudi Dierckx

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Genotype-phenotype relationships of truncating mutations, p.E297G and p.D482G in bile salt export pump deficiency per Antonia Felzen, Daan B.E. van Wessel, Emmanuel Gonzales, Richard J. Thompson, Irena Jankowska, Benjamin L. Shneider, Etienne Sokal, Tassos Grammatikopoulos, Agustina Kadaristiana, Emmanuel Jacquemin, Anne Spraul, Patryk Lipiński, Piotr Czubkowski, Nathalie Rock, Mohammad Shagrani, Dieter Broering, Emanuele Nicastro, Deirdre Kelly, Gabriella Nebbia, Henrik Arnell, Björn Fischler, Jan B.F. Hulscher, Daniele Serranti, Cigdem Arikan, Esra Polat, Dominique Debray, Florence Lacaille, Cristina Goncalves, Loreto Hierro, Gema Muñoz Bartolo, Yael Mozer-Glassberg, Amer Azaz, Jernej Brecelj, Antal Dezsőfi, Pier Luigi Calvo, Enke Grabhorn, Steffen Hartleif, Wendy J. van der Woerd, Binita M. Kamath, Jian-She Wang, Liting Li, Özlem Durmaz, Nanda Kerkar, Marianne Hørby Jørgensen, Ryan Fischer, Carolina Jimenez-Rivera, Seema Alam, Mara Cananzi, Noemie Laverdure, Cristina Targa Ferreira, Felipe Ordoñez Guerrero, Heng Wang, Valerie Sency, Kyung Mo Kim, Huey-Ling Chen, Elisa de Carvalho, Alexandre Fabre, Jesus Quintero Bernabeu, Aglaia Zellos, Estella M. Alonso, Ronald J. Sokol, Frederick J. Suchy, Kathleen M. Loomes, Patrick J. McKiernan, Philip Rosenthal, Yumirle Turmelle, Simon Horslen, Kathleen Schwarz, Jorge A. Bezerra, Kasper Wang, Bettina E. Hansen, Henkjan J. Verkade

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Incidence, management and outcomes in hepatic artery complications after paediatric liver transplantation: protocol of the retrospective, international, multicentre HEPATIC Registr... per Barbara E Wildhaber, Wei Zhang, Martin de Santibañes, Victoria Ardiles, Xueli Bai, Mukesh Kumar, Mohamed Rela, Reinoud P H Bokkers, Ekkehard Sturm, Simon McGuirk, Girish Gupte, Esteban Frauca, Francisco Hernández-Oliveros, Winita Hardikar, Helen Evans, Khalid Sharif, Jiří Froněk, David Duncan, Emmanuel Gonzales, Carl Jorns, Alessandro Parente, Ulrich Baumann, Lidia Monti, Marco Spada, Denise Aldrian, Hubert P J van der Doef, Thomas Casswall, Martin Delle, Georg F Vogel, Adam Kolesnik, Mauricio Larrarte K, Paolo Marra, Michela Bravi, Domenico Pinelli, Hajime Uchida, Vidyadhar Mali, Marion Aw, Stéphanie Franchi-Abella, Florent Guérin, Julia Minetto, Sergio Sierre, Jimmy Walker Uno, Steffen Hartleif, Cristina T Ferreira, Luiza S Nader, Catalina Jaramillo, Amit A Shah, Michael R Acord, Tommaso Alterio, Marisa Beretta, Haritha Rajakrishnan, Sudhindran Surendran, Weihao Li, Marcelo Dip, Sue Bates, Lynette Goh, Jonathan Seisenbacher, Joao Seda Neto, Eduardo Antunes da Fonseca, Carolina Magalhães Costa, Marco A Farina, Khaled Z Dajani, David L Bigam, Ting-Bo Liang, Lucie Gonsorčíková, Šimon Bohuš, Norman Junge, Nicolas Richter, Muthukumarassamy Rajakannu, Kumar Palaniappan, Arti Pawaria, Shaleen Agarwal, Subhash Gupta, Sonal Asthana, Vaishnavi Bandewar, Karthik Raichurkar, Yusuke Yanagi, Ryuji Komine, Peter Carr-Boyd, Marek Stefanowicz, Julita Latka-Grot, Dieter C Broering, Dimitri A Raptis, Kris Ann H Marquez, Francisca Van der Schyff, Jesús Quintero-Bernabeu, Maria Mercadal-Hally, Ane M Andres, Riccardo Superina, Juan Carlos Caicedo, Leandra Bitterfeld, Zachary Kastenberg, Bryanna Domenick, George V Mazariegos, Kyle Soltys, Joseph DiNorcia, Swanti Antala, Sander S Florman, Bettina M Buchholz, Uta Herden, Lutz Fischer, Rudi A J O Dierckx, Hermien Hartog

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