Abnormal functional lymphoid tolerance and enhanced myeloid exocytosis are characteristics of resting and stimulated PBMCs in cystic fibrosis patients by Clémence Gaudin, Reem Ghinnagow, Flora Lemaire, Bérengère Villeret, Isabelle Sermet-Gaudelus, Isabelle Sermet-Gaudelus, Isabelle Sermet-Gaudelus, Isabelle Sermet-Gaudelus, Jean-Michel Sallenave

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Ivacaftor treatment in patients with cystic fibrosis and the G551D-CFTR mutation by Isabelle Sermet-Gaudelus

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Emerging Therapeutic Approaches for Cystic Fibrosis. From Gene Editing to Personalized Medicine by Iwona Pranke, Anita Golec, Alexandre Hinzpeter, Aleksander Edelman, Isabelle Sermet-Gaudelus, Isabelle Sermet-Gaudelus, Isabelle Sermet-Gaudelus

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Airway Surface Liquid pH Regulation in Airway Epithelium Current Understandings and Gaps in Knowledge by Miroslaw Zajac, Elise Dreano, Aurelie Edwards, Gabrielle Planelles, Isabelle Sermet-Gaudelus

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Sweat Chloride Testing and Nasal Potential Difference (NPD) Are Primary Outcome Parameters in Treatment with Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Modulators by Isabelle Sermet-Gaudelus, Thao Nguyen-Khoa, Aurélie Hatton, Kate Hayes, Iwona Pranke

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Characterization of nasal potential difference in cftr knockout and F508del-CFTR mice. by Emilie Lyne Saussereau, Delphine Roussel, Siradiou Diallo, Laurent Debarbieux, Aleksander Edelman, Isabelle Sermet-Gaudelus

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Determinants of refusal of A/H1N1 pandemic vaccination in a high risk population: a qualitative approach. by Eugenie d'Alessandro, Dominique Hubert, Odile Launay, Laurence Bassinet, Olivier Lortholary, Yannick Jaffre, Isabelle Sermet-Gaudelus

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Plasma lipidomics reveals potential prognostic signatures within a cohort of cystic fibrosis patients by Mario Ollero, Giuseppe Astarita, Ida Chiara Guerrera, Isabelle Sermet-Gaudelus, Stéphanie Trudel, Daniele Piomelli, Aleksander Edelman

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Representation and quantification of module activity from omics data with rROMA by Matthieu Najm, Matthieu Cornet, Luca Albergante, Andrei Zinovyev, Isabelle Sermet-Gaudelus, Véronique Stoven, Laurence Calzone, Loredana Martignetti

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Putting bicarbonate on the spot: pharmacological insights for CFTR correction in the airway epithelium by Miroslaw Zajac, Miroslaw Zajac, Miroslaw Zajac, Miroslaw Zajac, Agathe Lepissier, Agathe Lepissier, Agathe Lepissier, Elise Dréano, Elise Dréano, Elise Dréano, Benoit Chevalier, Benoit Chevalier, Benoit Chevalier, Aurélie Hatton, Aurélie Hatton, Aurélie Hatton, Mairead Kelly-Aubert, Mairead Kelly-Aubert, Mairead Kelly-Aubert, Daniela Guidone, Gabrielle Planelles, Aleksander Edelman, Aleksander Edelman, Aleksander Edelman, Emmanuelle Girodon, Emmanuelle Girodon, Alexandre Hinzpeter, Alexandre Hinzpeter, Alexandre Hinzpeter, Gilles Crambert, Iwona Pranke, Iwona Pranke, Iwona Pranke, Luis. J. V. Galietta, Isabelle Sermet-Gaudelus, Isabelle Sermet-Gaudelus, Isabelle Sermet-Gaudelus, Isabelle Sermet-Gaudelus

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Acting on the CFTR Membrane-Spanning Domains Interface Rescues Some Misfolded Mutants by Nesrine Baatallah, Ahmad Elbahnsi, Benoit Chevalier, Solène Castanier, Jean-Paul Mornon, Iwona Pranke, Aleksander Edelman, Isabelle Sermet-Gaudelus, Isabelle Callebaut, Alexandre Hinzpeter

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An unexpected effect of TNF-α on F508del-CFTR maturation and function [v2; ref status: indexed, http://f1000r.es/5tv] by Sara Bitam, Iwona Pranke, Monika Hollenhorst, Nathalie Servel, Christelle Moquereau, Danielle Tondelier, Aurélie Hatton, Valérie Urbach, Isabelle Sermet-Gaudelus, Alexandre Hinzpeter, Aleksander Edelman

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An unexpected effect of TNF-α on F508del-CFTR maturation and function [v1; ref status: indexed, http://f1000r.es/5jf] by Sara Bitam, Iwona Pranke, Monika Hollenhorst, Nathalie Servel, Christelle Moquereau, Danielle Tondelier, Aurélie Hatton, Valérie Urbach, Isabelle Sermet-Gaudelus, Alexandre Hinzpeter, Aleksander Edelman

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Bothnian Palmoplantar Keratoderma: Further Delineation of the Associated Phenotype by Laura Fertitta, Fabienne Charbit-Henrion, Stéphanie Leclerc-Mercier, Thao Nguyen-Khoa, Robert Baran, Caroline Alby, Julie Steffann, Isabelle Sermet-Gaudelus, Smail Hadj-Rabia

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A novel lipidomic strategy reveals plasma phospholipid signatures associated with respiratory disease severity in cystic fibrosis patients. by Ida Chiara Guerrera, Giuseppe Astarita, Jean-Philippe Jais, Dorota Sands, Anna Nowakowska, Julien Colas, Isabelle Sermet-Gaudelus, Martin Schuerenberg, Daniele Piomelli, Aleksander Edelman, Mario Ollero

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Urinary Exosomes of Patients with Cystic Fibrosis Unravel CFTR-Related Renal Disease by Sebastien Gauthier, Iwona Pranke, Vincent Jung, Loredana Martignetti, Véronique Stoven, Thao Nguyen-Khoa, Michaela Semeraro, Alexandre Hinzpeter, Aleksander Edelman, Ida Chiara Guerrera, Isabelle Sermet-Gaudelus

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Proteomic profiling of sweat in patients with cystic fibrosis provides new insights into epidermal homoeostasis by Matthieu Cornet, Thao Nguyen‐Khoa, Mairead Kelly‐Aubert, Vincent Jung, Frédérique Chedevergne, Muriel Le Bourgeois, Laura Aoust, Kévin Roger, Chiara Ida Guerrera, Isabelle Sermet‐Gaudelus

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Unsolved severe chronic rhinosinusitis elucidated by extensive CFTR genotyping by Fanny Degrugillier, Stéphanie Simon, Abdel Aissat, Natascha Remus, Chadia Mekki, Xavier Decrouy, Aurélie Hatton, Alexandre Hinzpeter, Brice Hoffmann, Isabelle Sermet‐Gaudelus, Isabelle Callebaut, Pascale Fanen, Virginie Prulière‐Escabasse

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Differential CFTR-Interactome Proximity Labeling Procedures Identify Enrichment in Multiple SLC Transporters by Benoît Chevalier, Nesrine Baatallah, Matthieu Najm, Solène Castanier, Vincent Jung, Iwona Pranke, Anita Golec, Véronique Stoven, Stefano Marullo, Fabrice Antigny, Ida Chiara Guerrera, Isabelle Sermet-Gaudelus, Aleksander Edelman, Alexandre Hinzpeter

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Characterization of two rat models of cystic fibrosis—KO and F508del CFTR—Generated by Crispr‐Cas9 by Elise Dreano, Marc Bacchetta, Juliette Simonin, Louise Galmiche, Claire Usal, Lotfi Slimani, Jérémy Sadoine, Laurent Tesson, Ignacio Anegon, Jean‐Paul Concordet, Aurélie Hatton, Lucile Vignaud, Danielle Tondelier, Isabelle Sermet‐Gaudelus, Marc Chanson, Charles‐Henry Cottart

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