Lipid composition of microdomains is altered in a cell model of Gaucher disease* by Leanne K. Hein, Stephen Duplock, John J. Hopwood, Maria Fuller

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Variables influencing fluorimetric N-sulfoglucosamine sulfohydrolase (SGSH) activity measurement in brain homogenates by Lauren S. Whyte, John J. Hopwood, Kim M. Hemsley, Adeline A. Lau

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Glycosphingolipid analysis in a naturally occurring ovine model of acute neuronopathic Gaucher disease by Litsa Karageorgos, Leanne Hein, Tina Rozaklis, Melissa Adams, Stephen Duplock, Marten Snel, Kim Hemsley, Tim Kuchel, Nicholas Smith, John J. Hopwood

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Embryonic Stem Cell-Derived Glial Precursors as a Vehicle for Sulfamidase Production in the MPS-IIIA Mouse Brain by Aaron J. Robinson, Guoying Zhao, Joy Rathjen, Peter D. Rathjen, Rhonda G. Hutchinson, Helen J. Eyre, Kim M. Hemsley, John J. Hopwood

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Enzyme replacement reduces neuropathology in MPS IIIA dogs by Allison C. Crawley, Neil Marshall, Helen Beard, Sofia Hassiotis, Vicki Walsh, Barbara King, Nicola Hucker, Maria Fuller, Robert D. Jolly, John J. Hopwood, Kim M. Hemsley

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Lysosomal gene Hexb displays haploinsufficiency in a knock-in mouse model of Alzheimer’s disease by Lauren S. Whyte, Célia Fourrier, Sofia Hassiotis, Adeline A. Lau, Paul J. Trim, Leanne K. Hein, Kathryn J. Hattersley, Julien Bensalem, John J. Hopwood, Kim M. Hemsley, Timothy J. Sargeant

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A Comparative Effectiveness Study of Newborn Screening Methods for Four Lysosomal Storage Disorders by Karen A. Sanders, Dimitar K. Gavrilov, Devin Oglesbee, Kimiyo M. Raymond, Silvia Tortorelli, John J. Hopwood, Fred Lorey, Ramanath Majumdar, Charles A. Kroll, Amber M. McDonald, Jean M. Lacey, Coleman T. Turgeon, Justin N. Tucker, Hao Tang, Robert Currier, Grazia Isaya, Piero Rinaldo, Dietrich Matern

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