Ivacaftor treatment of cystic fibrosis patients with the G551D mutation: a review of the evidence by Kavitha Kotha, John P. Clancy

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Flexible semiparametric joint modeling: an application to estimate individual lung function decline and risk of pulmonary exacerbations in cystic fibrosis by Dan Li, Ruth Keogh, John P. Clancy, Rhonda D. Szczesniak

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CFTR dysfunction in smooth muscle drives TGFβ dependent airway hyperreactivity by Elizabeth L. Kramer, Kristin M. Hudock, Cynthia R. Davidson, John P. Clancy

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2045 The role of TGFβ in driving early cystic fibrosis lung disease by Elizabeth L. Kramer, William Hardie, Kristin Hudock, Cynthia Davidson, Alicia Ostmann, John P. Clancy

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Improving Detection of Rapid Cystic Fibrosis Disease Progression–Early Translation of a Predictive Algorithm Into a Point-of-Care Tool by Rhonda D. Szczesniak, Cole Brokamp, Weiji Su, Gary L. Mcphail, John Pestian, John P. Clancy

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3123 TGFbeta, Early Cytokine Dysregulation, and Airway Smooth Muscle Dysfunction in Cystic Fibrosis by Elizabeth L Kramer, Rhonda Szczesniak, Weiji Su, Satish Madala, Kristin Hudock, Cynthia Davidson, Alicia Ostmann, Lauren Strecker, John P. Clancy

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Data driven decision making to characterize clinical personas of parents of children with cystic fibrosis: a mixed methods study by Rhonda D. Szczesniak, Teresa Pestian, Leo L. Duan, Dan Li, Sophia Stamper, Brycen Ferrara, Elizabeth Kramer, John P. Clancy, Daniel Grossoehme

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Tgf-beta downregulation of distinct chloride channels in cystic fibrosis-affected epithelia. by Hongtao Sun, William T Harris, Stephanie Kortyka, Kavitha Kotha, Alicia J Ostmann, Amir Rezayat, Anusha Sridharan, Yan Sanders, Anjaparavanda P Naren, John P Clancy

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Optimizing nasal potential difference analysis for CFTR modulator development: assessment of ivacaftor in CF subjects with the G551D-CFTR mutation. by Steven M Rowe, Bo Liu, Aubrey Hill, Heather Hathorne, Morty Cohen, John R Beamer, Frank J Accurso, Qunming Dong, Claudia L Ordoñez, Anne J Stone, Eric R Olson, John P Clancy, VX06-770-101 Study Group

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Social-environmental phenotypes of rapid cystic fibrosis lung disease progression in adolescents and young adults living in the United States by Anushka K. Palipana, Andrew Vancil, Emrah Gecili, Erika Rasnick, Daniel Ehrlich, Teresa Pestian, Eleni-Rosalina Andrinopoulou, Pedro M. Afonso, Ruth H. Keogh, Yizhao Ni, Judith W. Dexheimer, John P. Clancy, Patrick Ryan, Cole Brokamp, Rhonda D. Szczesniak

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Pharmacologic improvement of CFTR function rapidly decreases sputum pathogen density, but lung infections generally persist by David P. Nichols, Sarah J. Morgan, Michelle Skalland, Anh T. Vo, Jill M. Van Dalfsen, Sachinkumar B.P. Singh, Wendy Ni, Lucas R. Hoffman, Kailee McGeer, Sonya L. Heltshe, John P. Clancy, Steven M. Rowe, Peter Jorth, Pradeep K. Singh, the PROMISE-Micro Study Group

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Multicenter intestinal current measurements in rectal biopsies from CF and non-CF subjects to monitor CFTR function. by John P Clancy, Rhonda D Szczesniak, Melissa A Ashlock, Sarah E Ernst, Lijuan Fan, Douglas B Hornick, Philip H Karp, Umer Khan, James Lymp, Alicia J Ostmann, Amir Rezayat, Timothy D Starner, Shajan P Sugandha, Hongtao Sun, Nancy Quinney, Scott H Donaldson, Steven M Rowe, Sherif E Gabriel

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Prospective multicenter randomized patient recruitment and sample collection to enable future measurements of sputum biomarkers of inflammation in an observational study of cystic... by Theodore G. Liou, Frederick R. Adler, Natalia Argel, Fadi Asfour, Perry S. Brown, Barbara A. Chatfield, Cori L. Daines, Dixie Durham, Jessica A. Francis, Barbara Glover, Theresa Heynekamp, John R. Hoidal, Judy L. Jensen, Ruth Keogh, Carol M. Kopecky, Noah Lechtzin, Yanping Li, Jerimiah Lysinger, Osmara Molina, Craig Nakamura, Kristyn A. Packer, Katie R. Poch, Alexandra L. Quittner, Peggy Radford, Abby J. Redway, Scott D. Sagel, Shawna Sprandel, Jennifer L. Taylor-Cousar, Jane B. Vroom, Ryan Yoshikawa, John P. Clancy, J. Stuart Elborn, Kenneth N. Olivier, David R. Cox

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Airway inflammation accelerates pulmonary exacerbations in cystic fibrosis by Theodore G. Liou, Natalia Argel, Fadi Asfour, Perry S. Brown, Barbara A. Chatfield, David R. Cox, Cori L. Daines, Dixie Durham, Jessica A. Francis, Barbara Glover, My Helms, Theresa Heynekamp, John R. Hoidal, Judy L. Jensen, Christiana Kartsonaki, Ruth Keogh, Carol M. Kopecky, Noah Lechtzin, Yanping Li, Jerimiah Lysinger, Osmara Molina, Craig Nakamura, Kristyn A. Packer, Robert Paine, III, Katie R. Poch, Alexandra L. Quittner, Peggy Radford, Abby J. Redway, Scott D. Sagel, Rhonda D. Szczesniak, Shawna Sprandel, Jennifer L. Taylor-Cousar, Jane B. Vroom, Ryan Yoshikawa, John P. Clancy, J. Stuart Elborn, Kenneth N. Olivier, Frederick R. Adler

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