A Novel G542X CFTR Rat Model of Cystic Fibrosis Is Sensitive to Nonsense Mediated Decay 由 Jyoti Sharma, Jyoti Sharma, Joseph Abbott, Lauren Klaskala, Guojun Zhao, Susan E. Birket, Susan E. Birket, Steven M. Rowe, Steven M. Rowe

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CFTR targeted therapies: recent advances in cystic fibrosis and possibilities in other diseases of the airways 由 Sheylan D. Patel, Taylor R. Bono, Steven M. Rowe, George M. Solomon

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An ex vivo rat trachea model reveals abnormal airway physiology and a gland secretion defect in cystic fibrosis. 由 Elex Harris, Molly Easter, Janna Ren, Stefanie Krick, Jarrod Barnes, Steven M Rowe

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Roflumilast reverses CFTR-mediated ion transport dysfunction in cigarette smoke-exposed mice 由 S. Vamsee Raju, Lawrence Rasmussen, Peter A. Sloane, Li Ping Tang, Emily Falk Libby, Steven M. Rowe

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ΔF508 CFTR surface stability is regulated by DAB2 and CHIP-mediated ubiquitination in post-endocytic compartments. 由 Lianwu Fu, Andras Rab, Li ping Tang, Zsuzsa Bebok, Steven M Rowe, Rafal Bartoszewski, James F Collawn

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Fibroblast Growth Factor Receptor 4 Deficiency Mediates Airway Inflammation in the Adult Healthy Lung? 由 Molly Easter, Jaleesa Garth, Elex S. Harris, Elex S. Harris, Ren-Jay Shei, Eric S. Helton, Yuhua Wei, Rebecca Denson, Rennan Zaharias, Steven M. Rowe, Steven M. Rowe, Patrick Geraghty, Christian Faul, Jarrod W. Barnes, Jarrod W. Barnes, Stefanie Krick, Stefanie Krick

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IP-10 is a potential biomarker of cystic fibrosis acute pulmonary exacerbations. 由 George M Solomon, Carla Frederick, Shaoyan Zhang, Amit Gaggar, Tom Harris, Bradford A Woodworth, Chad Steele, Steven M Rowe

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Haemophilus influenzae persists in biofilm communities in a smoke-exposed ferret model of COPD 由 Benjamin C. Hunt, Denise Stanford, Xin Xu, Jindong Li, Amit Gaggar, Steven M. Rowe, S. Vamsee Raju, W. Edward Swords

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Sinus Microanatomy and Microbiota in a Rabbit Model of Rhinosinusitis 由 Do-Yeon Cho, Do-Yeon Cho, Calvin Mackey, William J. Van Der Pol, Daniel Skinner, Casey D. Morrow, Trenton R. Schoeb, Steven M. Rowe, Steven M. Rowe, William E. Swords, William E. Swords, Guillermo J. Tearney, Guillermo J. Tearney, Bradford A. Woodworth, Bradford A. Woodworth

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Use of ferrets for electrophysiologic monitoring of ion transport. 由 Niroop Kaza, S Vamsee Raju, Joan M Cadillac, John A Trombley, Lawrence Rasmussen, Liping Tang, Erik Dohm, Kevin S Harrod, Steven M Rowe

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Protective and antifungal properties of Nanodisk-Amphotericin B over commercially available Amphotericin B 由 Do-Yeon Cho, Kyle J. Hoffman, Gobind S. Gill, Dong-Jin Lim, Daniel Skinner, Calvin Mackey, Steven M. Rowe, Bradford A. Woodworth

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Contribution of Short Chain Fatty Acids to the Growth of Pseudomonas aeruginosa in Rhinosinusitis 由 Do-Yeon Cho, Do-Yeon Cho, Do-Yeon Cho, Daniel Skinner, Ryan C. Hunter, Christopher Weeks, Dong Jin Lim, Harrison Thompson, Christopher R. Walz, Shaoyan Zhang, Jessica W. Grayson, William E. Swords, William E. Swords, Steven M. Rowe, Steven M. Rowe, Bradford A. Woodworth, Bradford A. Woodworth

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Longitudinal improvements in clinical and functional outcomes following initiation of elexacaftor/tezacaftor/ivacaftor in patients with cystic fibrosis 由 Kadambari Vijaykumar, Hui Min Leung, Amilcar Barrios, Justin Wade, Heather Y. Hathorne, David P. Nichols, Guillermo J. Tearney, Steven M. Rowe, George M. Solomon

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Reduced sialylation of airway mucin impairs mucus transport by altering the biophysical properties of mucin 由 Elex S. Harris, Hannah J. McIntire, Marina Mazur, Hinnerk Schulz-Hildebrandt, Hui Min Leung, Guillermo J. Tearney, Stefanie Krick, Steven M. Rowe, Jarrod W. Barnes

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Implementation of a successful eradication protocol for Burkholderia Cepacia complex in cystic fibrosis patients 由 Bryan A. Garcia, Jacque L. Carden, Dana L. Goodwin, Tim A. Smith, Amit Gaggar, Kevin Leon, Veena B. Antony, Steven M. Rowe, George M. Solomon

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Comparative transcriptomics in human COPD reveals dysregulated genes uniquely expressed in ferrets 由 Shah S. Hussain, Yvonne J. K. Edwards, Emily Falk Libby, Denise Stanford, Stephen A. Byzek, Don D. Sin, Merry-Lynn McDonald, S. Vamsee Raju, Steven M. Rowe

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The unfolded protein response affects readthrough of premature termination codons 由 Yifat S Oren, Michelle L McClure, Steven M Rowe, Eric J Sorscher, Assaf C Bester, Miriam Manor, Eitan Kerem, Joseph Rivlin, Fouad Zahdeh, Matthias Mann, Tamar Geiger, Batsheva Kerem

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Minimally Invasive Image-Guided Gut Transport Function Measurement Probe 由 David O. Otuya, David O. Otuya, Evangelia Gavgiotaki, Evangelia Gavgiotaki, Camella J. Carlson, Serena Q. Shi, Ariel J. Lee, Alexander A. Krall, Anita Chung, Catriona G. Grant, Nitasha M. Bhat, Peter Choy, Sarah L. Giddings, Joseph A. Gardecki, Joseph A. Gardecki, Jay R. Thiagarajah, Jay R. Thiagarajah, Steven M. Rowe, Steven M. Rowe, Guillermo J. Tearney, Guillermo J. Tearney, Guillermo J. Tearney, Guillermo J. Tearney

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LPS decreases CFTR open probability and mucociliary transport through generation of reactive oxygen species 由 Do Yeon Cho, Shaoyan Zhang, Ahmed Lazrak, Daniel Skinner, Harrison M. Thompson, Jessica Grayson, Purushotham Guroji, Saurabh Aggarwal, Zsuzsanna Bebok, Steven M. Rowe, Sadis Matalon, Eric J. Sorscher, Bradford A. Woodworth

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Prime editing-mediated correction of the CFTR W1282X mutation in iPSCs and derived airway epithelial cells 由 Chao Li, Zhong Liu, Justin Anderson, Zhongyu Liu, Liping Tang, Yao Li, Ning Peng, Jianguo Chen, Xueming Liu, Lianwu Fu, Tim M. Townes, Steven M. Rowe, David M. Bedwell, Jennifer Guimbellot, Rui Zhao

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