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H3K36 Methylation in Neural Development and Associated Diseases por Mattia Zaghi, Vania Broccoli, Vania Broccoli, Alessandro Sessa
Publicado 2020-01-01
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GABAergic Neuronal Precursor Grafting: Implications in Brain Regeneration and Plasticity por Manuel Alvarez Dolado, Vania Broccoli
Publicado 2011-01-01
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Exploiting hiPSCs in Leber's Hereditary Optic Neuropathy (LHON): Present Achievements and Future Perspectives por Camille Peron, Alessandra Maresca, Andrea Cavaliere, Angelo Iannielli, Angelo Iannielli, Vania Broccoli, Vania Broccoli, Valerio Carelli, Valerio Carelli, Ivano Di Meo, Valeria Tiranti
Publicado 2021-06-01
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Mitochondrial iron and energetic dysfunction distinguish fibroblasts and induced neurons from pantothenate kinase-associated neurodegeneration patients por Paolo Santambrogio, Sabrina Dusi, Michela Guaraldo, Luisa Ida Rotundo, Vania Broccoli, Barbara Garavaglia, Valeria Tiranti, Sonia Levi
Publicado 2015-09-01
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Generation of two human iPSC lines, FINCBi002-A and FINCBi003-A, carrying heteroplasmic macrodeletion of mitochondrial DNA causing Pearson’s syndrome por Camille Peron, Roberta Mauceri, Angelo Iannielli, Andrea Cavaliere, Andrea Legati, Ambra Rizzo, Francesca L. Sciacca, Vania Broccoli, Valeria Tiranti
Publicado 2021-01-01
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Generation of a human iPSC line, FINCBi001-A, carrying a homoplasmic m.G3460A mutation in MT-ND1 associated with Leber’s Hereditary optic Neuropathy (LHON) por Camille Peron, Roberta Mauceri, Tommaso Cabassi, Alice Segnali, Alessandra Maresca, Angelo Iannielli, Ambra Rizzo, Francesca L. Sciacca, Vania Broccoli, Valerio Carelli, Valeria Tiranti
Publicado 2020-10-01
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Transdifferentiation of Mouse Embryonic Fibroblasts into Dopaminergic Neurons Reactivates LINE-1 Repetitive Elements por Francesco Della Valle, Manjula P. Thimma, Massimiliano Caiazzo, Salvatore Pulcrano, Mirko Celii, Sabir A. Adroub, Peng Liu, Gregorio Alanis-Lobato, Vania Broccoli, Valerio Orlando
Publicado 2020-01-01
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A Human Stem Cell-Derived Neurosensory–Epithelial Circuitry on a Chip to Model Herpes Simplex Virus Reactivation por Pietro Giuseppe Mazzara, Elena Criscuolo, Marco Rasponi, Luca Massimino, Sharon Muggeo, Cecilia Palma, Matteo Castelli, Massimo Clementi, Roberto Burioni, Nicasio Mancini, Vania Broccoli, Nicola Clementi
Publicado 2022-08-01
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Direct Conversion of Fibroblasts into Functional Astrocytes by Defined Transcription Factors por Massimiliano Caiazzo, Serena Giannelli, Pierluigi Valente, Gabriele Lignani, Annamaria Carissimo, Alessandro Sessa, Gaia Colasante, Rosa Bartolomeo, Luca Massimino, Stefano Ferroni, Carmine Settembre, Fabio Benfenati, Vania Broccoli
Publicado 2015-01-01
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An ES-like pluripotent state in FGF-dependent murine iPS cells. por Bruno Di Stefano, Christa Buecker, Federica Ungaro, Alessandro Prigione, Hsu-Hsin Chen, Maaike Welling, Maureen Eijpe, Gustavo Mostoslavsky, Paul Tesar, James Adjaye, Niels Geijsen, Vania Broccoli
Publicado 2010-12-01
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SETD5 haploinsufficiency affects mitochondrial compartment in neural cells por Mattia Zaghi, Fabiana Longo, Luca Massimino, Alicia Rubio, Simone Bido, Pietro Giuseppe Mazzara, Edoardo Bellini, Federica Banfi, Paola Podini, Francesca Maltecca, Alessio Zippo, Vania Broccoli, Alessandro Sessa
Publicado 2023-06-01
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Whole brain delivery of an instability-prone Mecp2 transgene improves behavioral and molecular pathological defects in mouse models of Rett syndrome por Mirko Luoni, Serena Giannelli, Marzia Tina Indrigo, Antonio Niro, Luca Massimino, Angelo Iannielli, Laura Passeri, Fabio Russo, Giuseppe Morabito, Piera Calamita, Silvia Gregori, Benjamin Deverman, Vania Broccoli
Publicado 2020-03-01
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Generation of iPSCs from identical twin, one affected by LHON and one unaffected, both carrying a combination of two mitochondrial variants: m.14484 T>C and m.10680G>A por Camille Peron, Andrea Cavaliere, Chiara Fasano, Angelo Iannielli, Manuela Spagnolo, Andrea Legati, Maria Nicol Colombo, Ambra Rizzo, Francesca L. Sciacca, Valerio Carelli, Vania Broccoli, Costanza Lamperti, Valeria Tiranti
Publicado 2024-06-01
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Modeling native and seeded Synuclein aggregation and related cellular dysfunctions in dopaminergic neurons derived by a new set of isogenic iPSC lines with SNCA multiplications por Angelo Iannielli, Mirko Luoni, Serena Gea Giannelli, Rosangela Ferese, Gabriele Ordazzo, Matteo Fossati, Andrea Raimondi, Felipe Opazo, Olga Corti, Jochen H. M. Prehn, Stefano Gambardella, Ronald Melki, Vania Broccoli
Publicado 2022-10-01
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Scn1a gene reactivation after symptom onset rescues pathological phenotypes in a mouse model of Dravet syndrome por Nicholas Valassina, Simone Brusco, Alessia Salamone, Linda Serra, Mirko Luoni, Serena Giannelli, Simone Bido, Luca Massimino, Federica Ungaro, Pietro Giuseppe Mazzara, Patrizia D’Adamo, Gabriele Lignani, Vania Broccoli, Gaia Colasante
Publicado 2022-01-01
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Acid-sensing ion channel 3 is a new potential therapeutic target for the control of glioblastoma cancer stem cells growth por Andrea Balboni, Camilla D’Angelo, Nicoletta Collura, Simone Brusco, Claudia Di Berardino, Altea Targa, Beatrice Massoti, Eloise Mastrangelo, Mario Milani, Pierfausto Seneci, Vania Broccoli, Luca Muzio, Rossella Galli, Andrea Menegon
Publicado 2024-09-01
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Increasing cell culture density during a developmental window prevents fated rod precursors derailment toward hybrid rod-glia cells por Ivana Barravecchia, Chiara De Cesari, Viviana Guadagni, Giovanni Signore, Edoardo Bertolini, Serena Gea Giannelli, Francesca Scebba, Davide Martini, Mario Enrico Pè, Vania Broccoli, Massimiliano Andreazzoli, Debora Angeloni, Gian Carlo Demontis
Publicado 2023-04-01
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