Disseminated juvenile xanthogranulomas with systemic involvement: A rare presentation
Juvenile xanthogranuloma is a self-healing non-Langerhans cell histiocytosis. It primarily manifests with cutaneous lesions which may have systemic associations. We report a case of a 6-month-old child who presented with multiple orangish papules and nodules all over the body with eye and liver invo...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2019-01-01
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| Series: | Indian Journal of Paediatric Dermatology |
| Subjects: | |
| Online Access: | http://www.ijpd.in/article.asp?issn=2319-7250;year=2019;volume=20;issue=3;spage=271;epage=275;aulast=Sheth |
| _version_ | 1818263422835359744 |
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| author | Preeti K Sheth Resham Vasani Deepak Parikh Manish Shah Rajesh Jadhav |
| author_facet | Preeti K Sheth Resham Vasani Deepak Parikh Manish Shah Rajesh Jadhav |
| author_sort | Preeti K Sheth |
| collection | DOAJ |
| description | Juvenile xanthogranuloma is a self-healing non-Langerhans cell histiocytosis. It primarily manifests with cutaneous lesions which may have systemic associations. We report a case of a 6-month-old child who presented with multiple orangish papules and nodules all over the body with eye and liver involvement, which is a rare entity. The diagnosis was confirmed with dermoscopy and histopathological assessment, including immunohistochemical study. He responded to medical line of therapy. |
| first_indexed | 2024-12-12T19:18:46Z |
| format | Article |
| id | doaj.art-002bebcbe01e42bb916c2179e04479ab |
| institution | Directory Open Access Journal |
| issn | 2319-7250 |
| language | English |
| last_indexed | 2024-12-12T19:18:46Z |
| publishDate | 2019-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Indian Journal of Paediatric Dermatology |
| spelling | doaj.art-002bebcbe01e42bb916c2179e04479ab2022-12-22T00:14:40ZengWolters Kluwer Medknow PublicationsIndian Journal of Paediatric Dermatology2319-72502019-01-0120327127510.4103/ijpd.IJPD_121_18Disseminated juvenile xanthogranulomas with systemic involvement: A rare presentationPreeti K ShethResham VasaniDeepak ParikhManish ShahRajesh JadhavJuvenile xanthogranuloma is a self-healing non-Langerhans cell histiocytosis. It primarily manifests with cutaneous lesions which may have systemic associations. We report a case of a 6-month-old child who presented with multiple orangish papules and nodules all over the body with eye and liver involvement, which is a rare entity. The diagnosis was confirmed with dermoscopy and histopathological assessment, including immunohistochemical study. He responded to medical line of therapy.http://www.ijpd.in/article.asp?issn=2319-7250;year=2019;volume=20;issue=3;spage=271;epage=275;aulast=ShethJuvenile xanthogranulomanon-Langerhans cell histiocytosisxanthogranulomas with systemic involvement |
| spellingShingle | Preeti K Sheth Resham Vasani Deepak Parikh Manish Shah Rajesh Jadhav Disseminated juvenile xanthogranulomas with systemic involvement: A rare presentation Indian Journal of Paediatric Dermatology Juvenile xanthogranuloma non-Langerhans cell histiocytosis xanthogranulomas with systemic involvement |
| title | Disseminated juvenile xanthogranulomas with systemic involvement: A rare presentation |
| title_full | Disseminated juvenile xanthogranulomas with systemic involvement: A rare presentation |
| title_fullStr | Disseminated juvenile xanthogranulomas with systemic involvement: A rare presentation |
| title_full_unstemmed | Disseminated juvenile xanthogranulomas with systemic involvement: A rare presentation |
| title_short | Disseminated juvenile xanthogranulomas with systemic involvement: A rare presentation |
| title_sort | disseminated juvenile xanthogranulomas with systemic involvement a rare presentation |
| topic | Juvenile xanthogranuloma non-Langerhans cell histiocytosis xanthogranulomas with systemic involvement |
| url | http://www.ijpd.in/article.asp?issn=2319-7250;year=2019;volume=20;issue=3;spage=271;epage=275;aulast=Sheth |
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