Systemic Sclerosis with Multiple Pulmonary Manifestations
Systemic sclerosis (SSc) is a chronic autoimmune multisystem disorder characterized by endothelial dysfunction and fibroblast dysfunction, which results in progressive fibrosis of the skin and internal organs more frequently the lungs and gastro intestinal tract. Pulmonary involvement is common in...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
JCDR Research and Publications Private Limited
2016-06-01
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| Series: | Journal of Clinical and Diagnostic Research |
| Subjects: | |
| Online Access: | https://jcdr.net/articles/PDF/8032/18781_CE(RA1)_F(T)_PF1(SWAK)_PFA(AK)_PF2(PAG).pdf |
| Summary: | Systemic sclerosis (SSc) is a chronic autoimmune multisystem disorder characterized by endothelial dysfunction and fibroblast
dysfunction, which results in progressive fibrosis of the skin and internal organs more frequently the lungs and gastro intestinal tract.
Pulmonary involvement is common in the course of SSc, with Interstitial Lung Disease (ILD) and Pulmonary Arterial Hypertension
(PAH) being the leading causes of death. Here we report, case of an elderly female patient presenting with Diffuse SSc with multiple
uncommon pulmonary manifestations like ILD with Usual Interstitial Pneumonia (UIP) pattern (usually less common), PAH and right
sided pleural effusion. |
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| ISSN: | 2249-782X 0973-709X |