Management of Patients with Vascular Ehlers-Danlos Syndrome and Acute Coronary Syndrome: a Case Report
Background: Ehlers-Danlos syndrome (EDS) is a hereditary collagen vascular disorder characterized by joint hypermobility, skin hyperextensibility, and tissue fragility. Vascular EDS (vEDS) is a subtype of EDS which is characterized by vascular fragility.Case presentation: This is a case report of a...
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| Format: | Article |
| Language: | English |
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Vesnu Publications
2023-02-01
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| Series: | ARYA Atherosclerosis |
| Subjects: | |
| Online Access: | https://arya.mui.ac.ir/article_30973_f5404fcdb24e228dbdd4ad51a4a7e299.pdf |
| _version_ | 1797682708241973248 |
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| author | Ilenia Di Liberto Gerlando Pilato Giuseppe Caramanno |
| author_facet | Ilenia Di Liberto Gerlando Pilato Giuseppe Caramanno |
| author_sort | Ilenia Di Liberto |
| collection | DOAJ |
| description | Background: Ehlers-Danlos syndrome (EDS) is a hereditary collagen vascular disorder characterized by joint hypermobility, skin hyperextensibility, and tissue fragility. Vascular EDS (vEDS) is a subtype of EDS which is characterized by vascular fragility.Case presentation: This is a case report of a young man with vEDS hospitalized for myocardial infarction. He was presented with a coronary dissection and developed aortic dissection, coronary rupture, and cardiac tamponade until death. Conclusion: This case report highlights how patients with vEDS and acute coronary syndrome show a higher risk of vascular complications compared with other patients, and their admission to the institution with a cardiac surgery room could be helpful and safe for better management of the complications. Non-invasive methods could be useful to exclude other vascular diseases, before the emergency coronary intervention. |
| first_indexed | 2024-03-12T00:03:45Z |
| format | Article |
| id | doaj.art-00f16ff842644660892ec9c630bd135f |
| institution | Directory Open Access Journal |
| issn | 1735-3955 2251-6638 |
| language | English |
| last_indexed | 2024-03-12T00:03:45Z |
| publishDate | 2023-02-01 |
| publisher | Vesnu Publications |
| record_format | Article |
| series | ARYA Atherosclerosis |
| spelling | doaj.art-00f16ff842644660892ec9c630bd135f2023-09-17T06:27:02ZengVesnu PublicationsARYA Atherosclerosis1735-39552251-66382023-02-01192616410.48305/arya.2022.11722.234330973Management of Patients with Vascular Ehlers-Danlos Syndrome and Acute Coronary Syndrome: a Case ReportIlenia Di Liberto0Gerlando Pilato1Giuseppe Caramanno2Department of Interventional Cardiology, San Giovanni Di Dio Hospital, Agrigento, ItalyDepartment of Interventional Cardiology, San Giovanni Di Dio Hospital, Agrigento, ItalyDepartment of Interventional Cardiology, San Giovanni Di Dio Hospital, Agrigento, ItalyBackground: Ehlers-Danlos syndrome (EDS) is a hereditary collagen vascular disorder characterized by joint hypermobility, skin hyperextensibility, and tissue fragility. Vascular EDS (vEDS) is a subtype of EDS which is characterized by vascular fragility.Case presentation: This is a case report of a young man with vEDS hospitalized for myocardial infarction. He was presented with a coronary dissection and developed aortic dissection, coronary rupture, and cardiac tamponade until death. Conclusion: This case report highlights how patients with vEDS and acute coronary syndrome show a higher risk of vascular complications compared with other patients, and their admission to the institution with a cardiac surgery room could be helpful and safe for better management of the complications. Non-invasive methods could be useful to exclude other vascular diseases, before the emergency coronary intervention.https://arya.mui.ac.ir/article_30973_f5404fcdb24e228dbdd4ad51a4a7e299.pdfvascular ehlers-danlos syndromeacute coronary syndromecoronary dissectionaortic dissectioncoronary rupturecardiac tamponade |
| spellingShingle | Ilenia Di Liberto Gerlando Pilato Giuseppe Caramanno Management of Patients with Vascular Ehlers-Danlos Syndrome and Acute Coronary Syndrome: a Case Report ARYA Atherosclerosis vascular ehlers-danlos syndrome acute coronary syndrome coronary dissection aortic dissection coronary rupture cardiac tamponade |
| title | Management of Patients with Vascular Ehlers-Danlos Syndrome and Acute Coronary Syndrome: a Case Report |
| title_full | Management of Patients with Vascular Ehlers-Danlos Syndrome and Acute Coronary Syndrome: a Case Report |
| title_fullStr | Management of Patients with Vascular Ehlers-Danlos Syndrome and Acute Coronary Syndrome: a Case Report |
| title_full_unstemmed | Management of Patients with Vascular Ehlers-Danlos Syndrome and Acute Coronary Syndrome: a Case Report |
| title_short | Management of Patients with Vascular Ehlers-Danlos Syndrome and Acute Coronary Syndrome: a Case Report |
| title_sort | management of patients with vascular ehlers danlos syndrome and acute coronary syndrome a case report |
| topic | vascular ehlers-danlos syndrome acute coronary syndrome coronary dissection aortic dissection coronary rupture cardiac tamponade |
| url | https://arya.mui.ac.ir/article_30973_f5404fcdb24e228dbdd4ad51a4a7e299.pdf |
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