| Summary: | One of the more infrequent congenital diseases with a wide spectrum of symptoms and more complications of the right side of pulmonary artery (63% according to Ten Harkel) is unilateral pulmonary artery agenesis (UPAA). The clinical presentation is variable, and many patients can be asymptomatic for many years and even throughout their lives. Although the disease more frequently appears in childhood with moderate to severe respiratory symptoms, some patients continue living with the disease up to adulthood. The abnormality is sometimes concurrent with cardiac anomalies. Patients with UAPA may be asymptomatic or may present with recurrent pulmonary infections. In a report, a 25-year old woman who had inductional termination of pregnancy at 35 week last menstrual period (LMP) in a rural hospital due to preeclampsia reported as the UAPA patient.
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