Trehalose enhances mitochondria deficits in human NPC1 mutant fibroblasts but disrupts mouse Purkinje cell dendritic growth ex vivo

Trehalose enhances mitochondria deficits in human NPC1 mutant fibroblasts but disrupts mouse Purkinje cell dendritic growth ex vivo

Show other versions (1)

Bibliographic Details
Main Authors:	Collin M. MacLeod, Fawad A. K. Yousufzai, Liam T. Spencer, Sarah Kim, Lucianne A. Rivera-Rosario, Zerian D. Barrera, Lindsay Walsh, Claude Krummenacher, Benjamin Carone, Ileana Soto
Format:	Article
Language:	English
Published:	Public Library of Science (PLoS) 2023-01-01
Series:	PLoS ONE
Online Access:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10688965/?tool=EBI

Similar Items

Trehalose enhances mitochondria deficits in human NPC1 mutant fibroblasts but disrupts mouse Purkinje cell dendritic growth ex vivo.
by: Collin M MacLeod, et al.
Published: (2023-01-01)

Disruptive lysosomal-metabolic signaling and neurodevelopmental deficits that precede Purkinje cell loss in a mouse model of Niemann-Pick Type-C disease
by: Sarah Kim, et al.
Published: (2023-04-01)

Human Purkinje cells outperform mouse Purkinje cells in dendritic complexity and computational capacity
by: Stefano Masoli, et al.
Published: (2024-01-01)

Dendritic coincidence detection in Purkinje neurons of awake mice
by: Christopher J Roome, et al.
Published: (2020-12-01)

CTCF loss induces giant lamellar bodies in Purkinje cell dendrites
by: Teruyoshi Hirayama, et al.
Published: (2022-11-01)

Trehalose improves the movement ability of Aβarc Drosophila by restoring the damaged mitochondria
by: Li Liangxian, et al.
Published: (2024-04-01)

Inhibition gates supralinear Ca2+ signaling in Purkinje cell dendrites during practiced movements
by: Michael A Gaffield, et al.
Published: (2018-08-01)

Myocyte enhancer factor 2c regulates dendritic complexity and connectivity of cerebellar purkinje cells
by: Kamath, Sandhya Prakash, et al.
Published: (2020)

Direct translation of climbing fiber burst-mediated sensory coding into post-synaptic Purkinje cell dendritic calcium
by: Seung-Eon Roh, et al.
Published: (2020-09-01)

Gjd2b-mediated gap junctions promote glutamatergic synapse formation and dendritic elaboration in Purkinje neurons
by: Sahana Sitaraman, et al.
Published: (2021-08-01)

Characterization of cold-active trehalose synthase from Pseudarthrobacter sp. for trehalose bioproduction
by: Srisakul Trakarnpaiboon, et al.
Published: (2023-09-01)

Postsynaptic mitochondria are positioned to support functional diversity of dendritic spines
by: Connon I Thomas, et al.
Published: (2023-12-01)

Dendritic mitochondria reach stable positions during circuit development
by: Michelle C Faits, et al.
Published: (2016-01-01)

Optimizing Optogenetic Activation of Purkinje Cell Axons to Investigate the Purkinje Cell – DCN Synapse
by: Kim M. Gruver, et al.
Published: (2019-11-01)

Elimination of purkinje fibers by electroporation reduces ventricular fibrillation vulnerability
by: Livia, C, et al.
Published: (2018)

VAP spatially stabilizes dendritic mitochondria to locally support synaptic plasticity
by: Ojasee Bapat, et al.
Published: (2024-01-01)

Water structure around trehalose
by: Pagnotta, SE, et al.
Published: (2008)

Trehalose for Ocular Surface Health
by: Jarmo Laihia, et al.
Published: (2020-05-01)

About the role of trehalose in plants
by: Tjaša GORJANC, et al.
Published: (2018-04-01)

Viewpoint: spinocerebellar ataxias as diseases of Purkinje cell dysfunction rather than Purkinje cell loss
by: Josef P. Kapfhammer, et al.
Published: (2023-06-01)

Synaptic Activation of a Detailed Purkinje Cell Model Predicts Voltage-Dependent Control of Burst-Pause Responses in Active Dendrites
by: Stefano Masoli, et al.
Published: (2017-09-01)

All Purkinje cells are not created equal
by: Catarina Albergaria, et al.
Published: (2014-06-01)

Multiplexed coding by cerebellar Purkinje neurons
by: Sungho Hong, et al.
Published: (2016-07-01)

The NPC pathway and persistence of intracellular pathogens
by: Weng, Y
Published: (2023)

LMP-1 and Nasopharyngeal Carcinoma (NPC)
by: Anggun Indah Budiningrum, et al.
Published: (2014-06-01)

Clearance of Trehalose Lyophilized Platelets in Mice
by: Kim Mu-Young, et al.
Published: (2023-12-01)

Dietary Trehalose as a Bioactive Nutrient
by: Anqi Chen, et al.
Published: (2023-03-01)

Trehalose dihydrate from Tremella fuciformis
by: Wei Liu, et al.
Published: (2012-08-01)

Structure of glycosylated NPC1 luminal domain C reveals insights into NPC2 and Ebola virus interactions.
by: Zhao, Y, et al.
Published: (2016)

Trehalose-6-phosphate synthase 1, which catalyses the first step in trehalose synthesis, is essential for Arabidopsis embryo maturation.
by: Eastmond, P, et al.
Published: (2002)

A mathematical model of the Purkinje−Muscle Junctions
by: Turpault, N
Published: (2011)

Correction: Stimulus Discrimination in Cerebellar Purkinje Neurons
Published: (2014-01-01)

Mathematical model of bursting in dissociated purkinje neurons.
by: Michael D Forrest
Published: (2013-01-01)

Determinants of pattern recognition by cerebellar Purkinje cells
by: Steuber Volker, et al.
Published: (2008-07-01)

Nasopharyngeal carcinoma (NPC) with liver metastasis in pregnancy
by: Zakaria, Atiqah Farah, et al.
Published: (2016)

Targeting NPC1 in Renal Cell Carcinoma
by: Rushaniya Fazliyeva, et al.
Published: (2024-01-01)

New Active-Stacked-NPC Multilevel Converter
by: Dan Floricau, et al.
Published: (2009-10-01)

The role of NPC1L1 in cancer
by: Renshuai Zhang, et al.
Published: (2022-08-01)

Evaluation of the osmoprotective and bioprotective effect of trehalose 3%
by: Victor Sendra, et al.
Published: (2023-01-01)

Trehalose promotes atherosclerosis regression in female mice
by: Sabrina Robichaud, et al.
Published: (2024-02-01)