Ecchordosis physaliphora: Case report and brief review of the literature
Ecchordosis physaliphora is a rare congenital benign hamartomatous lesion originating from nodal cord remnants. This is histopathologically indistinguishable from chordoma, and hence imaging plays a key role in diagnosis. These lesions are hypointense on T1-weighted and hyperintense on T2-weighted i...
| Main Authors: | , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Elsevier
2021-12-01
|
| Series: | Radiology Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S1930043321006981 |
| _version_ | 1819116885080276992 |
|---|---|
| author | Dhairya A Lakhani, MD Daniel Martin, MD |
| author_facet | Dhairya A Lakhani, MD Daniel Martin, MD |
| author_sort | Dhairya A Lakhani, MD |
| collection | DOAJ |
| description | Ecchordosis physaliphora is a rare congenital benign hamartomatous lesion originating from nodal cord remnants. This is histopathologically indistinguishable from chordoma, and hence imaging plays a key role in diagnosis. These lesions are hypointense on T1-weighted and hyperintense on T2-weighted images, and follow CSF signal. In contrast to chordoma, Ecchordosis Physaliphora does not demonstrate contrast enhancement. Here, we present a case of 32–year-old male with no prior medical history, who presented to an outside facility for chronic headache workup and incidentally detected indeterminate lytic defect in the bony clivus with a well demarcated smoothly corticated margin. Further assessment with MRI brain showed findings characteristic of Ecchordosis physaliphora, a benign congenital hamartomatous lesion originating from nodal cord remnants requiring no additional follow-up imaging or intervention. |
| first_indexed | 2024-12-22T05:24:11Z |
| format | Article |
| id | doaj.art-03dc46276e614ae1aa72a70e9cd451b2 |
| institution | Directory Open Access Journal |
| issn | 1930-0433 |
| language | English |
| last_indexed | 2024-12-22T05:24:11Z |
| publishDate | 2021-12-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Radiology Case Reports |
| spelling | doaj.art-03dc46276e614ae1aa72a70e9cd451b22022-12-21T18:37:38ZengElsevierRadiology Case Reports1930-04332021-12-01161239373939Ecchordosis physaliphora: Case report and brief review of the literatureDhairya A Lakhani, MD0Daniel Martin, MD1Department of Radiology, West Virginia University, 1 Medical Center Drive, Morgantown, WV 26506Corresponding author.; Department of Radiology, West Virginia University, 1 Medical Center Drive, Morgantown, WV 26506Ecchordosis physaliphora is a rare congenital benign hamartomatous lesion originating from nodal cord remnants. This is histopathologically indistinguishable from chordoma, and hence imaging plays a key role in diagnosis. These lesions are hypointense on T1-weighted and hyperintense on T2-weighted images, and follow CSF signal. In contrast to chordoma, Ecchordosis Physaliphora does not demonstrate contrast enhancement. Here, we present a case of 32–year-old male with no prior medical history, who presented to an outside facility for chronic headache workup and incidentally detected indeterminate lytic defect in the bony clivus with a well demarcated smoothly corticated margin. Further assessment with MRI brain showed findings characteristic of Ecchordosis physaliphora, a benign congenital hamartomatous lesion originating from nodal cord remnants requiring no additional follow-up imaging or intervention.http://www.sciencedirect.com/science/article/pii/S1930043321006981ChordomaEcchordosis PhysaliphoraNotochord |
| spellingShingle | Dhairya A Lakhani, MD Daniel Martin, MD Ecchordosis physaliphora: Case report and brief review of the literature Radiology Case Reports Chordoma Ecchordosis Physaliphora Notochord |
| title | Ecchordosis physaliphora: Case report and brief review of the literature |
| title_full | Ecchordosis physaliphora: Case report and brief review of the literature |
| title_fullStr | Ecchordosis physaliphora: Case report and brief review of the literature |
| title_full_unstemmed | Ecchordosis physaliphora: Case report and brief review of the literature |
| title_short | Ecchordosis physaliphora: Case report and brief review of the literature |
| title_sort | ecchordosis physaliphora case report and brief review of the literature |
| topic | Chordoma Ecchordosis Physaliphora Notochord |
| url | http://www.sciencedirect.com/science/article/pii/S1930043321006981 |
| work_keys_str_mv | AT dhairyaalakhanimd ecchordosisphysaliphoracasereportandbriefreviewoftheliterature AT danielmartinmd ecchordosisphysaliphoracasereportandbriefreviewoftheliterature |