International registry of congenital porto-systemic shunts: a multi-centre, retrospective and prospective registry of neonates, children and adults with congenital porto-systemic shunts

International registry of congenital porto-systemic shunts: a multi-centre, retrospective and prospective registry of neonates, children and adults with congenital porto-systemic shunts

Abstract Background Congenital portosystemic shunts (CPSS) are rare vascular malformations associated with the risk of life-threatening systemic conditions, which remain underdiagnosed and often are identified after considerable diagnostic delay. CPSS are characterized by multiple signs and symptoms...

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Main Authors: Simona Korff, Khaled Mostaguir, Maurice Beghetti, Lorenzo D’Antiga, Dominique Debray, Stéphanie Franchi-Abella, Emmanuel Gonzales, Florent Guerin, Anne-Lise Hachulla, Virginie Lambert, Periklis Makrythanasis, Nicolas Roduit, Laurent Savale, Marie-Victoire Senat, Joël Spaltenstein, Frank van Steenbeek, Barbara E. Wildhaber, Marcel Zwahlen, Valérie A. McLin
Format: Article
Language:English
Published: BMC 2022-07-01
Series:Orphanet Journal of Rare Diseases
Subjects:
Congenital
Portosystemic
Shunt
Registry
Liver
Rare disease
Online Access:https://doi.org/10.1186/s13023-022-02412-8

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