Stevens–Johnson syndrome complicated by pneumomediastinum and cerebral venous sinus thrombosis in a 10-year-old girl: A case Report

Stevens–Johnson syndrome (SJS) is a life-threatening condition with severe mucocutaneous reaction in response to an offending medication. We report a case of SJS complicated with pneumomediastinum and cerebral sinus venous thrombosis in a girl. These two complications occurring simultaneously in a p...

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Main Authors: Pawan Jain, Rakesh Singh, Shriyanka Jain, Ankur Saxena, Ujjwala Verma, Vikash Kumar Bhojasiya
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2021-01-01
Series:Journal of Pediatric Critical Care
Subjects:
Online Access:http://www.jpcc.org.in/article.asp?issn=2349-6592;year=2021;volume=8;issue=6;spage=291;epage=294;aulast=Jain
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author Pawan Jain
Rakesh Singh
Shriyanka Jain
Ankur Saxena
Ujjwala Verma
Vikash Kumar Bhojasiya
author_facet Pawan Jain
Rakesh Singh
Shriyanka Jain
Ankur Saxena
Ujjwala Verma
Vikash Kumar Bhojasiya
author_sort Pawan Jain
collection DOAJ
description Stevens–Johnson syndrome (SJS) is a life-threatening condition with severe mucocutaneous reaction in response to an offending medication. We report a case of SJS complicated with pneumomediastinum and cerebral sinus venous thrombosis in a girl. These two complications occurring simultaneously in a pediatric patient with SJS are hitherto unreported. Laboratory workup pointed underlying connective tissue disease in her. She received supportive care along with steroids, antimicrobials, and anticoagulant under supervision of a multidisciplinary team. She recovered well at discharge and is on follow-up. Clinical vigilance identifies rare but important complications of SJS early, mitigating severe morbidity and mortality.
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spelling doaj.art-04df74e4e2964b038a42d03bcc07c4992022-12-22T04:30:20ZengWolters Kluwer Medknow PublicationsJournal of Pediatric Critical Care2349-65922455-70992021-01-018629129410.4103/jpcc.jpcc_57_21Stevens–Johnson syndrome complicated by pneumomediastinum and cerebral venous sinus thrombosis in a 10-year-old girl: A case ReportPawan JainRakesh SinghShriyanka JainAnkur SaxenaUjjwala VermaVikash Kumar BhojasiyaStevens–Johnson syndrome (SJS) is a life-threatening condition with severe mucocutaneous reaction in response to an offending medication. We report a case of SJS complicated with pneumomediastinum and cerebral sinus venous thrombosis in a girl. These two complications occurring simultaneously in a pediatric patient with SJS are hitherto unreported. Laboratory workup pointed underlying connective tissue disease in her. She received supportive care along with steroids, antimicrobials, and anticoagulant under supervision of a multidisciplinary team. She recovered well at discharge and is on follow-up. Clinical vigilance identifies rare but important complications of SJS early, mitigating severe morbidity and mortality.http://www.jpcc.org.in/article.asp?issn=2349-6592;year=2021;volume=8;issue=6;spage=291;epage=294;aulast=Jaincerebral venous sinus thrombosispneumomediastinumstevens–johnson syndrome
spellingShingle Pawan Jain
Rakesh Singh
Shriyanka Jain
Ankur Saxena
Ujjwala Verma
Vikash Kumar Bhojasiya
Stevens–Johnson syndrome complicated by pneumomediastinum and cerebral venous sinus thrombosis in a 10-year-old girl: A case Report
Journal of Pediatric Critical Care
cerebral venous sinus thrombosis
pneumomediastinum
stevens–johnson syndrome
title Stevens–Johnson syndrome complicated by pneumomediastinum and cerebral venous sinus thrombosis in a 10-year-old girl: A case Report
title_full Stevens–Johnson syndrome complicated by pneumomediastinum and cerebral venous sinus thrombosis in a 10-year-old girl: A case Report
title_fullStr Stevens–Johnson syndrome complicated by pneumomediastinum and cerebral venous sinus thrombosis in a 10-year-old girl: A case Report
title_full_unstemmed Stevens–Johnson syndrome complicated by pneumomediastinum and cerebral venous sinus thrombosis in a 10-year-old girl: A case Report
title_short Stevens–Johnson syndrome complicated by pneumomediastinum and cerebral venous sinus thrombosis in a 10-year-old girl: A case Report
title_sort stevens johnson syndrome complicated by pneumomediastinum and cerebral venous sinus thrombosis in a 10 year old girl a case report
topic cerebral venous sinus thrombosis
pneumomediastinum
stevens–johnson syndrome
url http://www.jpcc.org.in/article.asp?issn=2349-6592;year=2021;volume=8;issue=6;spage=291;epage=294;aulast=Jain
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