Extrarenal retroperitoneal Wilms' tumor with subsequent pulmonary and peritoneal metastasis in a 4 year-old girl: A case report and review of literature
This report describes an extremely rare case of extrarenal Wilms' tumor in a 4 year-old girl who presented with abdominal mass and pain. Computed tomography (CT) scanning revealed a well-defined mass lesion measuring 10 cm on the right side of her lower abdomen and pelvic cavity. The mass was s...
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Format: | Article |
Language: | English |
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Elsevier
2016-05-01
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Series: | Journal of Pediatric Surgery Case Reports |
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Online Access: | http://www.sciencedirect.com/science/article/pii/S2213576616300392 |
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author | Jinyoung Park |
author_facet | Jinyoung Park |
author_sort | Jinyoung Park |
collection | DOAJ |
description | This report describes an extremely rare case of extrarenal Wilms' tumor in a 4 year-old girl who presented with abdominal mass and pain. Computed tomography (CT) scanning revealed a well-defined mass lesion measuring 10 cm on the right side of her lower abdomen and pelvic cavity. The mass was surgically removed. Histologically, the tumor showed a triphasic pattern, consisting of stromal, epithelial and blastemal components. Immunohistochemistry showed that the tumor was positive for cytokeratin, vimentin and CD99. The histopathological diagnosis was extrarenal Wilms' tumor arising in the retroperitoneum and inguinal canal. The patient was administered adjuvant chemoradiotherapy due to subsequent pulmonary and peritoneal metastases. Follow-up 4 years later showed that she was doing well, with no recurrence of the tumor. |
first_indexed | 2024-04-12T17:30:46Z |
format | Article |
id | doaj.art-051ee715f39a4f26bef874ff1c20bfe3 |
institution | Directory Open Access Journal |
issn | 2213-5766 |
language | English |
last_indexed | 2024-04-12T17:30:46Z |
publishDate | 2016-05-01 |
publisher | Elsevier |
record_format | Article |
series | Journal of Pediatric Surgery Case Reports |
spelling | doaj.art-051ee715f39a4f26bef874ff1c20bfe32022-12-22T03:23:09ZengElsevierJournal of Pediatric Surgery Case Reports2213-57662016-05-018C192110.1016/j.epsc.2016.03.007Extrarenal retroperitoneal Wilms' tumor with subsequent pulmonary and peritoneal metastasis in a 4 year-old girl: A case report and review of literatureJinyoung ParkThis report describes an extremely rare case of extrarenal Wilms' tumor in a 4 year-old girl who presented with abdominal mass and pain. Computed tomography (CT) scanning revealed a well-defined mass lesion measuring 10 cm on the right side of her lower abdomen and pelvic cavity. The mass was surgically removed. Histologically, the tumor showed a triphasic pattern, consisting of stromal, epithelial and blastemal components. Immunohistochemistry showed that the tumor was positive for cytokeratin, vimentin and CD99. The histopathological diagnosis was extrarenal Wilms' tumor arising in the retroperitoneum and inguinal canal. The patient was administered adjuvant chemoradiotherapy due to subsequent pulmonary and peritoneal metastases. Follow-up 4 years later showed that she was doing well, with no recurrence of the tumor.http://www.sciencedirect.com/science/article/pii/S2213576616300392Extrarenal Wilms' tumorRetroperitoneumGirl |
spellingShingle | Jinyoung Park Extrarenal retroperitoneal Wilms' tumor with subsequent pulmonary and peritoneal metastasis in a 4 year-old girl: A case report and review of literature Journal of Pediatric Surgery Case Reports Extrarenal Wilms' tumor Retroperitoneum Girl |
title | Extrarenal retroperitoneal Wilms' tumor with subsequent pulmonary and peritoneal metastasis in a 4 year-old girl: A case report and review of literature |
title_full | Extrarenal retroperitoneal Wilms' tumor with subsequent pulmonary and peritoneal metastasis in a 4 year-old girl: A case report and review of literature |
title_fullStr | Extrarenal retroperitoneal Wilms' tumor with subsequent pulmonary and peritoneal metastasis in a 4 year-old girl: A case report and review of literature |
title_full_unstemmed | Extrarenal retroperitoneal Wilms' tumor with subsequent pulmonary and peritoneal metastasis in a 4 year-old girl: A case report and review of literature |
title_short | Extrarenal retroperitoneal Wilms' tumor with subsequent pulmonary and peritoneal metastasis in a 4 year-old girl: A case report and review of literature |
title_sort | extrarenal retroperitoneal wilms tumor with subsequent pulmonary and peritoneal metastasis in a 4 year old girl a case report and review of literature |
topic | Extrarenal Wilms' tumor Retroperitoneum Girl |
url | http://www.sciencedirect.com/science/article/pii/S2213576616300392 |
work_keys_str_mv | AT jinyoungpark extrarenalretroperitonealwilmstumorwithsubsequentpulmonaryandperitonealmetastasisina4yearoldgirlacasereportandreviewofliterature |