Parry-Romberg Syndrome Associated with Localized Scleroderma

Parry-Romberg syndrome is a rare neurocutaneous disorder of unknown origin. It is characterized by progressive facial hemiatrophy and frequently overlaps with a condition known as linear scleroderma ‘en coup de sabre’. Neurological involvement is frequently described in these patients, including mig...

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Main Authors: Jelena Maletic, Vassiliki Tsirka, Panos Ioannides, Dimitrios Karacostas, Nikolaos Taskos
Format: Article
Language:English
Published: Karger Publishers 2010-06-01
Series:Case Reports in Neurology
Subjects:
Online Access:http://www.karger.com/Article/FullText/314927
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author Jelena Maletic
Vassiliki Tsirka
Panos Ioannides
Dimitrios Karacostas
Nikolaos Taskos
author_facet Jelena Maletic
Vassiliki Tsirka
Panos Ioannides
Dimitrios Karacostas
Nikolaos Taskos
author_sort Jelena Maletic
collection DOAJ
description Parry-Romberg syndrome is a rare neurocutaneous disorder of unknown origin. It is characterized by progressive facial hemiatrophy and frequently overlaps with a condition known as linear scleroderma ‘en coup de sabre’. Neurological involvement is frequently described in these patients, including migraine, facial pain and epilepsy, which represent the commonest neurological conditions, sometimes associated with brain abnormalities ipsilaterally to the skin lesions. We present a case of Parry-Romberg syndrome with neurological involvement in a patient with diagnosed localized scleroderma (morphea).
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spelling doaj.art-05eb26fc14144918b6f2039f34e4fe7c2022-12-22T02:25:45ZengKarger PublishersCase Reports in Neurology1662-680X2010-06-0122576210.1159/000314927314927Parry-Romberg Syndrome Associated with Localized SclerodermaJelena MaleticVassiliki TsirkaPanos IoannidesDimitrios KaracostasNikolaos TaskosParry-Romberg syndrome is a rare neurocutaneous disorder of unknown origin. It is characterized by progressive facial hemiatrophy and frequently overlaps with a condition known as linear scleroderma ‘en coup de sabre’. Neurological involvement is frequently described in these patients, including migraine, facial pain and epilepsy, which represent the commonest neurological conditions, sometimes associated with brain abnormalities ipsilaterally to the skin lesions. We present a case of Parry-Romberg syndrome with neurological involvement in a patient with diagnosed localized scleroderma (morphea).http://www.karger.com/Article/FullText/314927Parry-Romberg syndromeLocalized sclerodermaNeurocutaneous diseaseMorphea
spellingShingle Jelena Maletic
Vassiliki Tsirka
Panos Ioannides
Dimitrios Karacostas
Nikolaos Taskos
Parry-Romberg Syndrome Associated with Localized Scleroderma
Case Reports in Neurology
Parry-Romberg syndrome
Localized scleroderma
Neurocutaneous disease
Morphea
title Parry-Romberg Syndrome Associated with Localized Scleroderma
title_full Parry-Romberg Syndrome Associated with Localized Scleroderma
title_fullStr Parry-Romberg Syndrome Associated with Localized Scleroderma
title_full_unstemmed Parry-Romberg Syndrome Associated with Localized Scleroderma
title_short Parry-Romberg Syndrome Associated with Localized Scleroderma
title_sort parry romberg syndrome associated with localized scleroderma
topic Parry-Romberg syndrome
Localized scleroderma
Neurocutaneous disease
Morphea
url http://www.karger.com/Article/FullText/314927
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AT vassilikitsirka parryrombergsyndromeassociatedwithlocalizedscleroderma
AT panosioannides parryrombergsyndromeassociatedwithlocalizedscleroderma
AT dimitrioskaracostas parryrombergsyndromeassociatedwithlocalizedscleroderma
AT nikolaostaskos parryrombergsyndromeassociatedwithlocalizedscleroderma