Modified pediatric Bentall procedure: A novel technique in a rare case
Aneurysms of ascending aorta are rarely seen in pediatric age group. Only few cases with Marfans syndrome have been reported in the literature. Preferred treatment for these children has been the standard Bentall procedure (aortic root replacement with composite graft prosthesis). We report a 4-year...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2016-01-01
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| Series: | Annals of Pediatric Cardiology |
| Subjects: | |
| Online Access: | http://www.annalspc.com/article.asp?issn=0974-2069;year=2016;volume=9;issue=3;spage=244;epage=247;aulast=Salve |
| _version_ | 1818838137995001856 |
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| author | Gananjay G Salve Satish R Javali Bharat V Dalvi Shivaprakash Krishnanaik |
| author_facet | Gananjay G Salve Satish R Javali Bharat V Dalvi Shivaprakash Krishnanaik |
| author_sort | Gananjay G Salve |
| collection | DOAJ |
| description | Aneurysms of ascending aorta are rarely seen in pediatric age group. Only few cases with Marfans syndrome have been reported in the literature. Preferred treatment for these children has been the standard Bentall procedure (aortic root replacement with composite graft prosthesis). We report a 4-year-old male child with huge aneurysm of ascending aorta and aortic root dilation with severe aortic regurgitation, having phenotypic features of Loeys-Dietz syndrome type I. He underwent Bentall procedure with a novel modification (medial trap-door technique for coronary reimplantation). Short-term result of this procedure is encouraging and he is asymptomatic for the last 14 months of follow-up. |
| first_indexed | 2024-12-19T03:33:37Z |
| format | Article |
| id | doaj.art-067ddc0f50704eada7ef0d6549d4c1ed |
| institution | Directory Open Access Journal |
| issn | 0974-2069 |
| language | English |
| last_indexed | 2024-12-19T03:33:37Z |
| publishDate | 2016-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Annals of Pediatric Cardiology |
| spelling | doaj.art-067ddc0f50704eada7ef0d6549d4c1ed2022-12-21T20:37:26ZengWolters Kluwer Medknow PublicationsAnnals of Pediatric Cardiology0974-20692016-01-019324424710.4103/0974-2069.189124Modified pediatric Bentall procedure: A novel technique in a rare caseGananjay G SalveSatish R JavaliBharat V DalviShivaprakash KrishnanaikAneurysms of ascending aorta are rarely seen in pediatric age group. Only few cases with Marfans syndrome have been reported in the literature. Preferred treatment for these children has been the standard Bentall procedure (aortic root replacement with composite graft prosthesis). We report a 4-year-old male child with huge aneurysm of ascending aorta and aortic root dilation with severe aortic regurgitation, having phenotypic features of Loeys-Dietz syndrome type I. He underwent Bentall procedure with a novel modification (medial trap-door technique for coronary reimplantation). Short-term result of this procedure is encouraging and he is asymptomatic for the last 14 months of follow-up.http://www.annalspc.com/article.asp?issn=0974-2069;year=2016;volume=9;issue=3;spage=244;epage=247;aulast=SalvePediatric BentallLoeys-Dietz syndromemedial trap-door technique |
| spellingShingle | Gananjay G Salve Satish R Javali Bharat V Dalvi Shivaprakash Krishnanaik Modified pediatric Bentall procedure: A novel technique in a rare case Annals of Pediatric Cardiology Pediatric Bentall Loeys-Dietz syndrome medial trap-door technique |
| title | Modified pediatric Bentall procedure: A novel technique in a rare case |
| title_full | Modified pediatric Bentall procedure: A novel technique in a rare case |
| title_fullStr | Modified pediatric Bentall procedure: A novel technique in a rare case |
| title_full_unstemmed | Modified pediatric Bentall procedure: A novel technique in a rare case |
| title_short | Modified pediatric Bentall procedure: A novel technique in a rare case |
| title_sort | modified pediatric bentall procedure a novel technique in a rare case |
| topic | Pediatric Bentall Loeys-Dietz syndrome medial trap-door technique |
| url | http://www.annalspc.com/article.asp?issn=0974-2069;year=2016;volume=9;issue=3;spage=244;epage=247;aulast=Salve |
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