High-grade primary pulmonary leiomyosarcoma

Primary sarcomas of the lung are rare and account for 0.5% of all primary lung tumors. There were approximately 300 cases described in the literature as of 2006. All histologic types of sarcoma were described, and the most common intrathoracic types reported were angiosarcoma, leiomyosarcoma, fibros...

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Main Authors: Rodrigo Afonso da Silva Sardenberg, Renato Cangnaci Neto, Fernanda Cavalcanti, Riad Naim Younes
Format: Article
Language:English
Published: Instituto Israelita de Ensino e Pesquisa Albert Einstein 2011-12-01
Series:Einstein (São Paulo)
Subjects:
Online Access:http://apps.einstein.br/revista/arquivos/PDF/1773-Einstein_v9n4_523-526_eng.pdf
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author Rodrigo Afonso da Silva Sardenberg
Renato Cangnaci Neto
Fernanda Cavalcanti
Riad Naim Younes
author_facet Rodrigo Afonso da Silva Sardenberg
Renato Cangnaci Neto
Fernanda Cavalcanti
Riad Naim Younes
author_sort Rodrigo Afonso da Silva Sardenberg
collection DOAJ
description Primary sarcomas of the lung are rare and account for 0.5% of all primary lung tumors. There were approximately 300 cases described in the literature as of 2006. All histologic types of sarcoma were described, and the most common intrathoracic types reported were angiosarcoma, leiomyosarcoma, fibrosarcoma, hemangiopericytoma, and rhabdomyosarcoma. The biological behavior of these tumors is not well-known due to their low frequency. Leiomyosarcomas represent one of the most common subtypes encountered in the lungs, and usually occur during the sixth decade, with male predominance. Although the frequency of metastatic disease is not related to tumor size, prognosis was reported to be poorer in high-grade tumors. In comparison with other sarcomas, survival after complete resection of pulmonary leiomyosarcoma was reported as longer. We report on a patient with primary leiomyosarcoma originating from the bronchus with complete resection and long-term follow-up.
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spelling doaj.art-07e8fc5241fc4fe288f93b6b10a1d44e2022-12-22T03:30:42ZengInstituto Israelita de Ensino e Pesquisa Albert EinsteinEinstein (São Paulo)1679-45082011-12-0194523526High-grade primary pulmonary leiomyosarcomaRodrigo Afonso da Silva SardenbergRenato Cangnaci NetoFernanda CavalcantiRiad Naim YounesPrimary sarcomas of the lung are rare and account for 0.5% of all primary lung tumors. There were approximately 300 cases described in the literature as of 2006. All histologic types of sarcoma were described, and the most common intrathoracic types reported were angiosarcoma, leiomyosarcoma, fibrosarcoma, hemangiopericytoma, and rhabdomyosarcoma. The biological behavior of these tumors is not well-known due to their low frequency. Leiomyosarcomas represent one of the most common subtypes encountered in the lungs, and usually occur during the sixth decade, with male predominance. Although the frequency of metastatic disease is not related to tumor size, prognosis was reported to be poorer in high-grade tumors. In comparison with other sarcomas, survival after complete resection of pulmonary leiomyosarcoma was reported as longer. We report on a patient with primary leiomyosarcoma originating from the bronchus with complete resection and long-term follow-up.http://apps.einstein.br/revista/arquivos/PDF/1773-Einstein_v9n4_523-526_eng.pdfLeiomyosarcomaLung neoplasmsSarcomaCase reports
spellingShingle Rodrigo Afonso da Silva Sardenberg
Renato Cangnaci Neto
Fernanda Cavalcanti
Riad Naim Younes
High-grade primary pulmonary leiomyosarcoma
Einstein (São Paulo)
Leiomyosarcoma
Lung neoplasms
Sarcoma
Case reports
title High-grade primary pulmonary leiomyosarcoma
title_full High-grade primary pulmonary leiomyosarcoma
title_fullStr High-grade primary pulmonary leiomyosarcoma
title_full_unstemmed High-grade primary pulmonary leiomyosarcoma
title_short High-grade primary pulmonary leiomyosarcoma
title_sort high grade primary pulmonary leiomyosarcoma
topic Leiomyosarcoma
Lung neoplasms
Sarcoma
Case reports
url http://apps.einstein.br/revista/arquivos/PDF/1773-Einstein_v9n4_523-526_eng.pdf
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AT renatocangnacineto highgradeprimarypulmonaryleiomyosarcoma
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AT riadnaimyounes highgradeprimarypulmonaryleiomyosarcoma