Erdheim-Chester Disease with Perirenal Masses Containing Macroscopic Fat Tissue

Erdheim-Chester disease is a rare non-Langerhans-cell histiocytosis involving multiple organs. On histological evaluation, lipid-laden histiocyte aggregates in Erdheim-Chester disease is detected, but fat tissue in affected organs is not noted grossly on computed tomography. A 40-year-old man presen...

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Bibliographic Details
Main Authors: Jonghyun Byeon, Kyung Ah Kim, Seong Su Hwang, Soo Youn Park, Hyun A Kim
Format: Article
Language:English
Published: The Korean Society of Radiology 2015-02-01
Series:대한영상의학회지
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Online Access:https://doi.org/10.3348/jksr.2015.72.2.143
Description
Summary:Erdheim-Chester disease is a rare non-Langerhans-cell histiocytosis involving multiple organs. On histological evaluation, lipid-laden histiocyte aggregates in Erdheim-Chester disease is detected, but fat tissue in affected organs is not noted grossly on computed tomography. A 40-year-old man presented with bilateral perirenal masses containing fat tissue. He was diagnosed as perirenal involvement of Erdheim-Chester disease. This report describes a case of Erdheim-Chester disease with perirenal involvement that demonstrates unusual features.
ISSN:1738-2637
2288-2928