Erdheim-Chester Disease with Perirenal Masses Containing Macroscopic Fat Tissue
Erdheim-Chester disease is a rare non-Langerhans-cell histiocytosis involving multiple organs. On histological evaluation, lipid-laden histiocyte aggregates in Erdheim-Chester disease is detected, but fat tissue in affected organs is not noted grossly on computed tomography. A 40-year-old man presen...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
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The Korean Society of Radiology
2015-02-01
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| Series: | 대한영상의학회지 |
| Subjects: | |
| Online Access: | https://doi.org/10.3348/jksr.2015.72.2.143 |
| _version_ | 1818368506624737280 |
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| author | Jonghyun Byeon Kyung Ah Kim Seong Su Hwang Soo Youn Park Hyun A Kim |
| author_facet | Jonghyun Byeon Kyung Ah Kim Seong Su Hwang Soo Youn Park Hyun A Kim |
| author_sort | Jonghyun Byeon |
| collection | DOAJ |
| description | Erdheim-Chester disease is a rare non-Langerhans-cell histiocytosis involving multiple organs. On histological evaluation, lipid-laden histiocyte aggregates in Erdheim-Chester disease is detected, but fat tissue in affected organs is not noted grossly on computed tomography. A 40-year-old man presented with bilateral perirenal masses containing fat tissue. He was diagnosed as perirenal involvement of Erdheim-Chester disease. This report describes a case of Erdheim-Chester disease with perirenal involvement that demonstrates unusual features. |
| first_indexed | 2024-12-13T23:09:02Z |
| format | Article |
| id | doaj.art-082327502f91471eaf875db138dc327b |
| institution | Directory Open Access Journal |
| issn | 1738-2637 2288-2928 |
| language | English |
| last_indexed | 2024-12-13T23:09:02Z |
| publishDate | 2015-02-01 |
| publisher | The Korean Society of Radiology |
| record_format | Article |
| series | 대한영상의학회지 |
| spelling | doaj.art-082327502f91471eaf875db138dc327b2022-12-21T23:28:09ZengThe Korean Society of Radiology대한영상의학회지1738-26372288-29282015-02-01722143146https://doi.org/10.3348/jksr.2015.72.2.143Erdheim-Chester Disease with Perirenal Masses Containing Macroscopic Fat TissueJonghyun ByeonKyung Ah KimSeong Su HwangSoo Youn ParkHyun A KimErdheim-Chester disease is a rare non-Langerhans-cell histiocytosis involving multiple organs. On histological evaluation, lipid-laden histiocyte aggregates in Erdheim-Chester disease is detected, but fat tissue in affected organs is not noted grossly on computed tomography. A 40-year-old man presented with bilateral perirenal masses containing fat tissue. He was diagnosed as perirenal involvement of Erdheim-Chester disease. This report describes a case of Erdheim-Chester disease with perirenal involvement that demonstrates unusual features.https://doi.org/10.3348/jksr.2015.72.2.143erdheim-chester diseasenon-langerhans-cell histiocytosiskidneyretroperitoneal fibrosis |
| spellingShingle | Jonghyun Byeon Kyung Ah Kim Seong Su Hwang Soo Youn Park Hyun A Kim Erdheim-Chester Disease with Perirenal Masses Containing Macroscopic Fat Tissue 대한영상의학회지 erdheim-chester disease non-langerhans-cell histiocytosis kidney retroperitoneal fibrosis |
| title | Erdheim-Chester Disease with Perirenal Masses Containing Macroscopic Fat Tissue |
| title_full | Erdheim-Chester Disease with Perirenal Masses Containing Macroscopic Fat Tissue |
| title_fullStr | Erdheim-Chester Disease with Perirenal Masses Containing Macroscopic Fat Tissue |
| title_full_unstemmed | Erdheim-Chester Disease with Perirenal Masses Containing Macroscopic Fat Tissue |
| title_short | Erdheim-Chester Disease with Perirenal Masses Containing Macroscopic Fat Tissue |
| title_sort | erdheim chester disease with perirenal masses containing macroscopic fat tissue |
| topic | erdheim-chester disease non-langerhans-cell histiocytosis kidney retroperitoneal fibrosis |
| url | https://doi.org/10.3348/jksr.2015.72.2.143 |
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