Progressive Systemic Sclerosis and its Dental Implications: A Case Report
Scleroderma is a complex autoimmune rheumatic disease characterised by the widespread fibrosis of skin and visceral organs, dysregulation of immune system and vasculopathy. The aetiology of this disease remains unknown till now. It is known to exist in two forms namely localised and generalised/pr...
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JCDR Research and Publications Private Limited
2021-10-01
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| Series: | Journal of Clinical and Diagnostic Research |
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| Online Access: | https://jcdr.net/articles/PDF/15482/49445_CE[Ra1]_F[SH]_PF1(SC_SS)_PFA(Pr_KM)_PN(KM).pdf |
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| author | Gor Vani Udaybhai harshitha erraguntala M swarna Maithreai G Navya Reddy kiran kumar sadula |
| author_facet | Gor Vani Udaybhai harshitha erraguntala M swarna Maithreai G Navya Reddy kiran kumar sadula |
| author_sort | Gor Vani Udaybhai |
| collection | DOAJ |
| description | Scleroderma is a complex autoimmune rheumatic disease characterised by the widespread fibrosis of skin and visceral organs,
dysregulation of immune system and vasculopathy. The aetiology of this disease remains unknown till now. It is known to exist in
two forms namely localised and generalised/progressive. It is known to affect females more commonly than males, and also shows
a wide range of oral and paraoral manifestations including xerostomia, periodontal disease, restricted mouth opening, burning
mouth syndrome, dysphagia, gastroesophageal reflux. Here, authors presents a case of 76-year-old female patient presented with
the chief complaint of dry mouth, restricted mouth opening, burning sensation in mouth and reduced taste perception for the past
seven years. On the basis of gastrointestinal disorder, Raynaud’s phenomenon, fish mouth appearance and various other extraoral
and intraoral features a diagnosis of Progressive Systemic Sclerosis (PSS) was made. The present case also emphasised upon
the crucial role of a general dentist in diagnosing such rare systemic diseases. This disease is known to carry a significant burden
in the form of pain and disability which potentially limits the proper functioning of major internal organs and results in various life
limiting complications. Thus, early diagnosis with appropriate investigations followed by specialist and multidisciplinary approach
to treatment, is the key for the successful management of disease. |
| first_indexed | 2024-12-13T21:16:08Z |
| format | Article |
| id | doaj.art-09af3f4680df40b0b96cfdf21cb401cf |
| institution | Directory Open Access Journal |
| issn | 2249-782X 0973-709X |
| language | English |
| last_indexed | 2024-12-13T21:16:08Z |
| publishDate | 2021-10-01 |
| publisher | JCDR Research and Publications Private Limited |
| record_format | Article |
| series | Journal of Clinical and Diagnostic Research |
| spelling | doaj.art-09af3f4680df40b0b96cfdf21cb401cf2022-12-21T23:31:14ZengJCDR Research and Publications Private LimitedJournal of Clinical and Diagnostic Research2249-782X0973-709X2021-10-011510ZD12ZD1410.7860/JCDR/2021/49445.15482Progressive Systemic Sclerosis and its Dental Implications: A Case ReportGor Vani Udaybhai0harshitha erraguntala1M swarna Maithreai2G Navya Reddy3kiran kumar sadula4Lecturer, Narsinhbhai Patel Dental College and Hospital, Sankalchand Patel University, Visnagar, Gujarat, India.Intern, Department of Dentistry, Meenakshi Ammal Dental College and Hospital, Chennai, Tamil Nadu, India.. Intern, Department of Dentistry, Gsl Dental College and Hospital, Rajamahendravaram, Andhra Pradesh, India.Intern, Department of Dentistry, Mnr Dental College and Hospital, Sangareddy, Telangana, India.Junior Consultant, Department of Dental, Smile Time Dental, Hyderabad, Telangana, India.Scleroderma is a complex autoimmune rheumatic disease characterised by the widespread fibrosis of skin and visceral organs, dysregulation of immune system and vasculopathy. The aetiology of this disease remains unknown till now. It is known to exist in two forms namely localised and generalised/progressive. It is known to affect females more commonly than males, and also shows a wide range of oral and paraoral manifestations including xerostomia, periodontal disease, restricted mouth opening, burning mouth syndrome, dysphagia, gastroesophageal reflux. Here, authors presents a case of 76-year-old female patient presented with the chief complaint of dry mouth, restricted mouth opening, burning sensation in mouth and reduced taste perception for the past seven years. On the basis of gastrointestinal disorder, Raynaud’s phenomenon, fish mouth appearance and various other extraoral and intraoral features a diagnosis of Progressive Systemic Sclerosis (PSS) was made. The present case also emphasised upon the crucial role of a general dentist in diagnosing such rare systemic diseases. This disease is known to carry a significant burden in the form of pain and disability which potentially limits the proper functioning of major internal organs and results in various life limiting complications. Thus, early diagnosis with appropriate investigations followed by specialist and multidisciplinary approach to treatment, is the key for the successful management of disease.https://jcdr.net/articles/PDF/15482/49445_CE[Ra1]_F[SH]_PF1(SC_SS)_PFA(Pr_KM)_PN(KM).pdfconnective tissue diseasefibrosisreduced mouth openingsclerodermaxerostomia |
| spellingShingle | Gor Vani Udaybhai harshitha erraguntala M swarna Maithreai G Navya Reddy kiran kumar sadula Progressive Systemic Sclerosis and its Dental Implications: A Case Report Journal of Clinical and Diagnostic Research connective tissue disease fibrosis reduced mouth opening scleroderma xerostomia |
| title | Progressive Systemic Sclerosis and its Dental Implications: A Case Report |
| title_full | Progressive Systemic Sclerosis and its Dental Implications: A Case Report |
| title_fullStr | Progressive Systemic Sclerosis and its Dental Implications: A Case Report |
| title_full_unstemmed | Progressive Systemic Sclerosis and its Dental Implications: A Case Report |
| title_short | Progressive Systemic Sclerosis and its Dental Implications: A Case Report |
| title_sort | progressive systemic sclerosis and its dental implications a case report |
| topic | connective tissue disease fibrosis reduced mouth opening scleroderma xerostomia |
| url | https://jcdr.net/articles/PDF/15482/49445_CE[Ra1]_F[SH]_PF1(SC_SS)_PFA(Pr_KM)_PN(KM).pdf |
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