Microphthalmia with pseudogliomatosis proliferation in the retina and orbital cyst

A 28-year-old systemically healthy male presented with a history of decreased vision in the right eye and a blind, undersized left eye since birth. On evaluation, the patient had typical inferonasal iris coloboma and retinochoroidal coloboma in the right eye and left disorganized microphthalmic glob...

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Main Authors: Bipasha Mukherjee, Daxa Sankadasariya, Kuldeep Bhadiyadara, S Krishnakumar
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2020-01-01
Series:TNOA Journal of Ophthalmic Science and Research
Subjects:
Online Access:http://www.tnoajosr.com/article.asp?issn=2589-4528;year=2020;volume=58;issue=1;spage=46;epage=48;aulast=Mukherjee
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author Bipasha Mukherjee
Daxa Sankadasariya
Kuldeep Bhadiyadara
S Krishnakumar
author_facet Bipasha Mukherjee
Daxa Sankadasariya
Kuldeep Bhadiyadara
S Krishnakumar
author_sort Bipasha Mukherjee
collection DOAJ
description A 28-year-old systemically healthy male presented with a history of decreased vision in the right eye and a blind, undersized left eye since birth. On evaluation, the patient had typical inferonasal iris coloboma and retinochoroidal coloboma in the right eye and left disorganized microphthalmic globe with colobomatous cyst and contracted socket. The patient underwent left eye injection of 0.25 ml ethanolamine oleate injected into the cyst after aspiration of the cyst contents. The patient had persistent colobomatous cyst, for which he underwent left eye excision of the microphthalmic globe with orbital cyst. Histopathological examination revealed thickened cyst wall, multiple nodules of dysplastic retinal tissues without proper lamination and extensive surrounding fibrosis, deposition of eosinophilic material around the blood vessels and retina, and multiple foci of calcification without atypia and mitosis. The diagnosis of a unilateral microphthalmic phthisical eye with pseudogliomatosis proliferation in the retina and in the orbital cyst was made.
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spelling doaj.art-0a521ff416aa4561833375e5e19de6372022-12-21T19:51:30ZengWolters Kluwer Medknow PublicationsTNOA Journal of Ophthalmic Science and Research2589-45282589-45362020-01-01581464810.4103/tjosr.tjosr_70_19Microphthalmia with pseudogliomatosis proliferation in the retina and orbital cystBipasha MukherjeeDaxa SankadasariyaKuldeep BhadiyadaraS KrishnakumarA 28-year-old systemically healthy male presented with a history of decreased vision in the right eye and a blind, undersized left eye since birth. On evaluation, the patient had typical inferonasal iris coloboma and retinochoroidal coloboma in the right eye and left disorganized microphthalmic globe with colobomatous cyst and contracted socket. The patient underwent left eye injection of 0.25 ml ethanolamine oleate injected into the cyst after aspiration of the cyst contents. The patient had persistent colobomatous cyst, for which he underwent left eye excision of the microphthalmic globe with orbital cyst. Histopathological examination revealed thickened cyst wall, multiple nodules of dysplastic retinal tissues without proper lamination and extensive surrounding fibrosis, deposition of eosinophilic material around the blood vessels and retina, and multiple foci of calcification without atypia and mitosis. The diagnosis of a unilateral microphthalmic phthisical eye with pseudogliomatosis proliferation in the retina and in the orbital cyst was made.http://www.tnoajosr.com/article.asp?issn=2589-4528;year=2020;volume=58;issue=1;spage=46;epage=48;aulast=Mukherjeecolobomatous cystmicrophthalmiapseudogliomatosis proliferation
spellingShingle Bipasha Mukherjee
Daxa Sankadasariya
Kuldeep Bhadiyadara
S Krishnakumar
Microphthalmia with pseudogliomatosis proliferation in the retina and orbital cyst
TNOA Journal of Ophthalmic Science and Research
colobomatous cyst
microphthalmia
pseudogliomatosis proliferation
title Microphthalmia with pseudogliomatosis proliferation in the retina and orbital cyst
title_full Microphthalmia with pseudogliomatosis proliferation in the retina and orbital cyst
title_fullStr Microphthalmia with pseudogliomatosis proliferation in the retina and orbital cyst
title_full_unstemmed Microphthalmia with pseudogliomatosis proliferation in the retina and orbital cyst
title_short Microphthalmia with pseudogliomatosis proliferation in the retina and orbital cyst
title_sort microphthalmia with pseudogliomatosis proliferation in the retina and orbital cyst
topic colobomatous cyst
microphthalmia
pseudogliomatosis proliferation
url http://www.tnoajosr.com/article.asp?issn=2589-4528;year=2020;volume=58;issue=1;spage=46;epage=48;aulast=Mukherjee
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AT daxasankadasariya microphthalmiawithpseudogliomatosisproliferationintheretinaandorbitalcyst
AT kuldeepbhadiyadara microphthalmiawithpseudogliomatosisproliferationintheretinaandorbitalcyst
AT skrishnakumar microphthalmiawithpseudogliomatosisproliferationintheretinaandorbitalcyst