Pure epithelioid angiomyolipoma of kidney in tuberous sclerosis patient: A case report and review of literature
The majority of renal angiomyolipoma (AML) is sporadic, and occasionally it occurs in the background of tuberous sclerosis complex. Epithelioid AML (EAML) is an uncommon variant, with uncertain behavior. We present a case of tuberous sclerosis with right large renal tumor. The tumor revealed epithel...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2016-01-01
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| Series: | Archives of Medicine and Health Sciences |
| Subjects: | |
| Online Access: | http://www.amhsjournal.org/article.asp?issn=2321-4848;year=2016;volume=4;issue=2;spage=222;epage=224;aulast=Naimi |
| _version_ | 1818156111813935104 |
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| author | Azar Naimi Maryam Riahinejad Fereshteh Mohammadizadeh Mehrdad Hosseinpour |
| author_facet | Azar Naimi Maryam Riahinejad Fereshteh Mohammadizadeh Mehrdad Hosseinpour |
| author_sort | Azar Naimi |
| collection | DOAJ |
| description | The majority of renal angiomyolipoma (AML) is sporadic, and occasionally it occurs in the background of tuberous sclerosis complex. Epithelioid AML (EAML) is an uncommon variant, with uncertain behavior. We present a case of tuberous sclerosis with right large renal tumor. The tumor revealed epithelioid cells accompanied by thick wall vessels and muscular bundles in all the sections; devoid of lipocytes. Immunohistochemistry confirmed the diagnosis of epithelioid perivascular epithelioid cell tumor. Pure EAML is a rare tumor with potential malignancy. Accurate diagnosis, especially differentiation it from renal cell carcinoma, is very important for proper management of the patient. |
| first_indexed | 2024-12-11T14:53:07Z |
| format | Article |
| id | doaj.art-0a84c69dffb44c95b7466b6ee92a5fc0 |
| institution | Directory Open Access Journal |
| issn | 2321-4848 |
| language | English |
| last_indexed | 2024-12-11T14:53:07Z |
| publishDate | 2016-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Archives of Medicine and Health Sciences |
| spelling | doaj.art-0a84c69dffb44c95b7466b6ee92a5fc02022-12-22T01:01:23ZengWolters Kluwer Medknow PublicationsArchives of Medicine and Health Sciences2321-48482016-01-014222222410.4103/2321-4848.196201Pure epithelioid angiomyolipoma of kidney in tuberous sclerosis patient: A case report and review of literatureAzar NaimiMaryam RiahinejadFereshteh MohammadizadehMehrdad HosseinpourThe majority of renal angiomyolipoma (AML) is sporadic, and occasionally it occurs in the background of tuberous sclerosis complex. Epithelioid AML (EAML) is an uncommon variant, with uncertain behavior. We present a case of tuberous sclerosis with right large renal tumor. The tumor revealed epithelioid cells accompanied by thick wall vessels and muscular bundles in all the sections; devoid of lipocytes. Immunohistochemistry confirmed the diagnosis of epithelioid perivascular epithelioid cell tumor. Pure EAML is a rare tumor with potential malignancy. Accurate diagnosis, especially differentiation it from renal cell carcinoma, is very important for proper management of the patient.http://www.amhsjournal.org/article.asp?issn=2321-4848;year=2016;volume=4;issue=2;spage=222;epage=224;aulast=NaimiEpithelioid angiomyolipomaperivascular epithelioid cell tumorrenaltuberous sclerosis |
| spellingShingle | Azar Naimi Maryam Riahinejad Fereshteh Mohammadizadeh Mehrdad Hosseinpour Pure epithelioid angiomyolipoma of kidney in tuberous sclerosis patient: A case report and review of literature Archives of Medicine and Health Sciences Epithelioid angiomyolipoma perivascular epithelioid cell tumor renal tuberous sclerosis |
| title | Pure epithelioid angiomyolipoma of kidney in tuberous sclerosis patient: A case report and review of literature |
| title_full | Pure epithelioid angiomyolipoma of kidney in tuberous sclerosis patient: A case report and review of literature |
| title_fullStr | Pure epithelioid angiomyolipoma of kidney in tuberous sclerosis patient: A case report and review of literature |
| title_full_unstemmed | Pure epithelioid angiomyolipoma of kidney in tuberous sclerosis patient: A case report and review of literature |
| title_short | Pure epithelioid angiomyolipoma of kidney in tuberous sclerosis patient: A case report and review of literature |
| title_sort | pure epithelioid angiomyolipoma of kidney in tuberous sclerosis patient a case report and review of literature |
| topic | Epithelioid angiomyolipoma perivascular epithelioid cell tumor renal tuberous sclerosis |
| url | http://www.amhsjournal.org/article.asp?issn=2321-4848;year=2016;volume=4;issue=2;spage=222;epage=224;aulast=Naimi |
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