Complex Ebstein's Anomaly in an 86-Year-Old Iranian Man: A Case Report

Ebstein's anomaly is defined as the significant apical displacement of the tricuspid valve causing tricuspid regurgitation. Although a variety of concomitant lesions have been previously described, we herein introduce an unusual presentation.  Our patient was an 86-year-old man with a primary p...

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Bibliographic Details
Main Authors: Bahieh Moradi, Farideh Roshanali
Format: Article
Language:English
Published: Tehran University of Medical Sciences 2017-03-01
Series:Journal of Tehran University Heart Center
Subjects:
Online Access:https://jthc.tums.ac.ir/index.php/jthc/article/view/678
Description
Summary:Ebstein's anomaly is defined as the significant apical displacement of the tricuspid valve causing tricuspid regurgitation. Although a variety of concomitant lesions have been previously described, we herein introduce an unusual presentation.  Our patient was an 86-year-old man with a primary presentation of typical chest pain in the setting of recently diagnosed coronary artery disease with concomitant Ebstein’s anomaly. We found mild-to-moderate tricuspid regurgitation, bicuspid aortic valve, persistent left superior vena cava, and patent foramen ovale. The patient had suffered from chest discomfort on exertion for 2 months with good functional capacity prior to diagnosis. Coronary angiography revealed two-vessel disease. The patient refused surgery. He was treated with medical anti-ischemic therapy. He had good exercise tolerance with relief of chest pain at the latest follow-up. The features demonstrated in this case report suggest that there may be several adult survivors of complex congenital heart diseases requiring individualized surgical treatment plans.
ISSN:1735-8620
2008-2371