Rare Association of Antiphospholipid Antibody Syndrome, Systemic Lupus Erythematosus and Aortic Dissection: A Striking Presentation with Multi-Organ Failure?
Systemic lupus erythematosus is a chronic autoimmune disease with a wide variety of clinical presentations induced by different immunocomplexes and autoantibodies. Antiphospholipid antibody syndrome (APLAS) is a life-threatening clinical condition characterized by venous and arterial thromboses or p...
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| Format: | Article |
| Language: | English |
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SMC MEDIA SRL
2020-08-01
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| Series: | European Journal of Case Reports in Internal Medicine |
| Subjects: | |
| Online Access: | https://www.ejcrim.com/index.php/EJCRIM/article/view/1887 |
| _version_ | 1818161371108343808 |
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| author | Firdevs Ulutaş Veli Çobankara Aslı Bozdemir Uğur Karasu |
| author_facet | Firdevs Ulutaş Veli Çobankara Aslı Bozdemir Uğur Karasu |
| author_sort | Firdevs Ulutaş |
| collection | DOAJ |
| description | Systemic lupus erythematosus is a chronic autoimmune disease with a wide variety of clinical presentations induced by different immunocomplexes and autoantibodies. Antiphospholipid antibody syndrome (APLAS) is a life-threatening clinical condition characterized by venous and arterial thromboses or pregnancy morbidity in the presence of persistent moderate/high levels of antiphospholipid antibodies. Aortic dissection is rarely associated with APLAS and always requires prompt diagnosis and early treatment. We report a rare case with a striking presentation. The patient developed multi-organ failure due to lethal aortic dissection and the obstruction of abdominal and thoracic branch vessels. |
| first_indexed | 2024-12-11T16:16:42Z |
| format | Article |
| id | doaj.art-0af4caef0b4b433aa6099cb985b7f1f1 |
| institution | Directory Open Access Journal |
| issn | 2284-2594 |
| language | English |
| last_indexed | 2024-12-11T16:16:42Z |
| publishDate | 2020-08-01 |
| publisher | SMC MEDIA SRL |
| record_format | Article |
| series | European Journal of Case Reports in Internal Medicine |
| spelling | doaj.art-0af4caef0b4b433aa6099cb985b7f1f12022-12-22T00:58:56ZengSMC MEDIA SRLEuropean Journal of Case Reports in Internal Medicine2284-25942020-08-0110.12890/2020_0018871503Rare Association of Antiphospholipid Antibody Syndrome, Systemic Lupus Erythematosus and Aortic Dissection: A Striking Presentation with Multi-Organ Failure?Firdevs Ulutaş0Veli Çobankara1Aslı Bozdemir2Uğur Karasu3Department of Rheumatology, Pamukkale University Faculty of Medicine, Denizli, TurkeyDepartment of Rheumatology, Pamukkale University Faculty of Medicine, Denizli, TurkeyDepartment of Internal Medicine, Pamukkale University Faculty of Medicine, Denizli, TurkeyDepartment of Internal Medicine, Pamukkale University Faculty of Medicine, Denizli, TurkeySystemic lupus erythematosus is a chronic autoimmune disease with a wide variety of clinical presentations induced by different immunocomplexes and autoantibodies. Antiphospholipid antibody syndrome (APLAS) is a life-threatening clinical condition characterized by venous and arterial thromboses or pregnancy morbidity in the presence of persistent moderate/high levels of antiphospholipid antibodies. Aortic dissection is rarely associated with APLAS and always requires prompt diagnosis and early treatment. We report a rare case with a striking presentation. The patient developed multi-organ failure due to lethal aortic dissection and the obstruction of abdominal and thoracic branch vessels.https://www.ejcrim.com/index.php/EJCRIM/article/view/1887aortic dissectionantiphospholipid antibody syndrome |
| spellingShingle | Firdevs Ulutaş Veli Çobankara Aslı Bozdemir Uğur Karasu Rare Association of Antiphospholipid Antibody Syndrome, Systemic Lupus Erythematosus and Aortic Dissection: A Striking Presentation with Multi-Organ Failure? European Journal of Case Reports in Internal Medicine aortic dissection antiphospholipid antibody syndrome |
| title | Rare Association of Antiphospholipid Antibody Syndrome, Systemic Lupus Erythematosus and Aortic Dissection: A Striking Presentation with Multi-Organ Failure? |
| title_full | Rare Association of Antiphospholipid Antibody Syndrome, Systemic Lupus Erythematosus and Aortic Dissection: A Striking Presentation with Multi-Organ Failure? |
| title_fullStr | Rare Association of Antiphospholipid Antibody Syndrome, Systemic Lupus Erythematosus and Aortic Dissection: A Striking Presentation with Multi-Organ Failure? |
| title_full_unstemmed | Rare Association of Antiphospholipid Antibody Syndrome, Systemic Lupus Erythematosus and Aortic Dissection: A Striking Presentation with Multi-Organ Failure? |
| title_short | Rare Association of Antiphospholipid Antibody Syndrome, Systemic Lupus Erythematosus and Aortic Dissection: A Striking Presentation with Multi-Organ Failure? |
| title_sort | rare association of antiphospholipid antibody syndrome systemic lupus erythematosus and aortic dissection a striking presentation with multi organ failure |
| topic | aortic dissection antiphospholipid antibody syndrome |
| url | https://www.ejcrim.com/index.php/EJCRIM/article/view/1887 |
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