Síndroma de Ehlers-Danlos: Uma causa rara de pneumotórax espontâneo Ehlers-Danlos syndrome: A rare cause of spontaneous pneumothorax

Síndroma de Ehlers-Danlos: Uma causa rara de pneumotórax espontâneo Ehlers-Danlos syndrome: A rare cause of spontaneous pneumothorax

A síndroma de Ehlers-Danlos (cutis hyperelastica), constitui uma patologia do tecido conjuntivo caracterizada por alterações da pele, ligamentos e órgãos internos. Apresenta transmissão hereditária, em geral autossómica dominante. Afecta primordialmente a síntese do colagéneo, pelo que a pele e os v...

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Bibliographic Details
Main Authors:	Carlos Lopes, Alda Manique, Renato Sotto-Mayor, Jorge Cruz, Margarida Mendes de Almeida, João Cravino, A Bugalho de Almeida
Format:	Article
Language:	English
Published:	Elsevier 2006-07-01
Series:	Revista Portuguesa de Pneumologia
Subjects:	Síndroma de Ehlers-Danlos pneumotórax hipermobilidade articular Ehlers-Danlos Syndrome pneumothorax joint hypermobility
Online Access:	http://www.scielo.oces.mctes.pt/scielo.php?script=sci_arttext&pid=S0873-21592006000400010

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