Hypertrophic Cardiomyopathy with masked Atrioventricular Block. Report of 2 cases
Background. Hypertrophic cardiomyopathy is the most common genetic cardiac disorder in Algeria, although syncope is often caused by ventricular arrhythmias or left outflow tract obstruction, it may also, be related to complete atrioventricular block; the latter is rarely reported in the literat...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | Arabic |
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Association de la Recherche Pharmaceutique & d'Enrichissement des connaissances (ARPEC)
2021-06-01
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| Series: | Batna Journal of Medical Sciences |
| Subjects: | |
| Online Access: | https://batnajms.net/wp-content/uploads/Archives/2021/1/17_BJMS_8_1_Zouzou.pdf |
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| author | Hanane Zouzou Fatseh Mohamedi Imed Alloune Hinda Bourmouche Toufik Boudjelal |
| author_facet | Hanane Zouzou Fatseh Mohamedi Imed Alloune Hinda Bourmouche Toufik Boudjelal |
| author_sort | Hanane Zouzou |
| collection | DOAJ |
| description | Background. Hypertrophic cardiomyopathy is the
most common genetic cardiac disorder in Algeria,
although syncope is often caused by ventricular
arrhythmias or left outflow tract obstruction, it may
also, be related to complete atrioventricular block; the
latter is rarely reported in the literature, the
diagnosis is not so obvious and should be thoroughly
researched in presence of syncope. We report two
cases of patients with hypertrophic cardiomyopathy
and atrioventricular block revealed by syncope.
Cases’ presentation. We reported two patients who
presented hypertrophic cardiomyopathy, with
recurrent syncope; one patient presented accessory
the pathway which masked the complete atrio
ventricular block and the other patient presented
alternating occurrence of right bundle branch block
and left bundle branch block at the ECG monitoring
over a 48 hours. Echocardiography showed
hypertrophy of left ventricular walls, but no left
ventricular outflow tract gradient was detected.
Extensive fibrosis especially in the septum was
detected by late gadolinium enhancement. The two
patients were implanted with dual-chamber
pacemakers. During follow up, one patient had
developed refractory heart failure and died in 2014.
Conclusions. Accessory pathway may mask complete
atrioventricular block, also alternating bundle branch
block could be the only proof of complete
atrioventricular block. Fibrosis is the principal
the substrate of reentry phenomenon, but septal fibrosis
can also damage the atrioventricular conduction system.
Non-obstructive hypertrophic cardiomyopathy could
be related to fibrosis, and/or asynchrony. |
| first_indexed | 2024-12-11T15:16:39Z |
| format | Article |
| id | doaj.art-0c05d7cbb21e462e86c123bc2ea1ab1e |
| institution | Directory Open Access Journal |
| issn | 2437-0665 |
| language | Arabic |
| last_indexed | 2024-12-11T15:16:39Z |
| publishDate | 2021-06-01 |
| publisher | Association de la Recherche Pharmaceutique & d'Enrichissement des connaissances (ARPEC) |
| record_format | Article |
| series | Batna Journal of Medical Sciences |
| spelling | doaj.art-0c05d7cbb21e462e86c123bc2ea1ab1e2022-12-22T01:00:33ZaraAssociation de la Recherche Pharmaceutique & d'Enrichissement des connaissances (ARPEC)Batna Journal of Medical Sciences2437-06652021-06-0181889110.48087/BJMScr.2021.8117Hypertrophic Cardiomyopathy with masked Atrioventricular Block. Report of 2 casesHanane Zouzou0 Fatseh Mohamedi1Imed Alloune2Hinda Bourmouche3Toufik Boudjelal4Cardiology Department, Batna University Hospital - AlgeriaCardiology Department, Batna University Hospital - AlgeriaCardiology Department, Batna University Hospital - AlgeriaCardiology Department, Batna University Hospital - AlgeriaCardiology Department, Batna University Hospital - AlgeriaBackground. Hypertrophic cardiomyopathy is the most common genetic cardiac disorder in Algeria, although syncope is often caused by ventricular arrhythmias or left outflow tract obstruction, it may also, be related to complete atrioventricular block; the latter is rarely reported in the literature, the diagnosis is not so obvious and should be thoroughly researched in presence of syncope. We report two cases of patients with hypertrophic cardiomyopathy and atrioventricular block revealed by syncope. Cases’ presentation. We reported two patients who presented hypertrophic cardiomyopathy, with recurrent syncope; one patient presented accessory the pathway which masked the complete atrio ventricular block and the other patient presented alternating occurrence of right bundle branch block and left bundle branch block at the ECG monitoring over a 48 hours. Echocardiography showed hypertrophy of left ventricular walls, but no left ventricular outflow tract gradient was detected. Extensive fibrosis especially in the septum was detected by late gadolinium enhancement. The two patients were implanted with dual-chamber pacemakers. During follow up, one patient had developed refractory heart failure and died in 2014. Conclusions. Accessory pathway may mask complete atrioventricular block, also alternating bundle branch block could be the only proof of complete atrioventricular block. Fibrosis is the principal the substrate of reentry phenomenon, but septal fibrosis can also damage the atrioventricular conduction system. Non-obstructive hypertrophic cardiomyopathy could be related to fibrosis, and/or asynchrony. https://batnajms.net/wp-content/uploads/Archives/2021/1/17_BJMS_8_1_Zouzou.pdfconvulsive syncopesudden cardiac deathalternating bundle branch blockaccessory pathway |
| spellingShingle | Hanane Zouzou Fatseh Mohamedi Imed Alloune Hinda Bourmouche Toufik Boudjelal Hypertrophic Cardiomyopathy with masked Atrioventricular Block. Report of 2 cases Batna Journal of Medical Sciences convulsive syncope sudden cardiac death alternating bundle branch block accessory pathway |
| title | Hypertrophic Cardiomyopathy with masked Atrioventricular Block. Report of 2 cases |
| title_full | Hypertrophic Cardiomyopathy with masked Atrioventricular Block. Report of 2 cases |
| title_fullStr | Hypertrophic Cardiomyopathy with masked Atrioventricular Block. Report of 2 cases |
| title_full_unstemmed | Hypertrophic Cardiomyopathy with masked Atrioventricular Block. Report of 2 cases |
| title_short | Hypertrophic Cardiomyopathy with masked Atrioventricular Block. Report of 2 cases |
| title_sort | hypertrophic cardiomyopathy with masked atrioventricular block report of 2 cases |
| topic | convulsive syncope sudden cardiac death alternating bundle branch block accessory pathway |
| url | https://batnajms.net/wp-content/uploads/Archives/2021/1/17_BJMS_8_1_Zouzou.pdf |
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