Left atrial appendage aneurysm in pediatrics: Case study and literature review

Left atrial appendage aneurysm (LAAA) is a rare cardiac pathology that is often identified in adulthood. There are a myriad of presentations related to atrial appendage enlargement, but most are asymptomatic. Pediatric cases of LAAA are extremely rare. We report a case of an incidental giant LAAA fo...

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Main Authors: Kambiz Norozi, Mathushan Subasri, Luis Altamirano Diaz, Osami Honjo
Format: Article
Language:English
Published: Frontiers Media S.A. 2023-08-01
Series:Frontiers in Cardiovascular Medicine
Subjects:
Online Access:https://www.frontiersin.org/articles/10.3389/fcvm.2023.1211619/full
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author Kambiz Norozi
Kambiz Norozi
Kambiz Norozi
Kambiz Norozi
Kambiz Norozi
Mathushan Subasri
Mathushan Subasri
Mathushan Subasri
Luis Altamirano Diaz
Luis Altamirano Diaz
Luis Altamirano Diaz
Luis Altamirano Diaz
Osami Honjo
author_facet Kambiz Norozi
Kambiz Norozi
Kambiz Norozi
Kambiz Norozi
Kambiz Norozi
Mathushan Subasri
Mathushan Subasri
Mathushan Subasri
Luis Altamirano Diaz
Luis Altamirano Diaz
Luis Altamirano Diaz
Luis Altamirano Diaz
Osami Honjo
author_sort Kambiz Norozi
collection DOAJ
description Left atrial appendage aneurysm (LAAA) is a rare cardiac pathology that is often identified in adulthood. There are a myriad of presentations related to atrial appendage enlargement, but most are asymptomatic. Pediatric cases of LAAA are extremely rare. We report a case of an incidental giant LAAA found in a healthy 6-year-old boy. He was successfully treated with surgical resection. A review of the literature shows that the presentation of LAAA in pediatrics likely involves cardiac or respiratory symptoms but can also be incidental findings. Similar to adults, diagnosis requires cardiac imaging, with echocardiography being the mainstay. Surgical intervention is indicated in symptomatic and most asymptomatic patients to prevent complications. More research is warranted into the optimal timing of surgery and alternative surgical approaches for complex cases.
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spelling doaj.art-0ce08a4aa2e542ffa58b6c43a31a80b62023-08-10T21:19:59ZengFrontiers Media S.A.Frontiers in Cardiovascular Medicine2297-055X2023-08-011010.3389/fcvm.2023.12116191211619Left atrial appendage aneurysm in pediatrics: Case study and literature reviewKambiz Norozi0Kambiz Norozi1Kambiz Norozi2Kambiz Norozi3Kambiz Norozi4Mathushan Subasri5Mathushan Subasri6Mathushan Subasri7Luis Altamirano Diaz8Luis Altamirano Diaz9Luis Altamirano Diaz10Luis Altamirano Diaz11Osami Honjo12Department of Paediatrics, University of Western Ontario, London, ON, CanadaDivision of Pediatric Cardiology, Department of Paediatrics, London Health Sciences Centre, London, ON, CanadaPediatric Cardiopulmonary Research Laboratory, London Health Sciences Centre, London, ON, CanadaChildren Health Research Institute, London, ON, CanadaDepartment of Paediatric Cardiology, Medical School Hannover, Hannover, GermanyDivision of Pediatric Cardiology, Department of Paediatrics, London Health Sciences Centre, London, ON, CanadaPediatric Cardiopulmonary Research Laboratory, London Health Sciences Centre, London, ON, CanadaFaculty of Medicine and Health Sciences, McGill University, Montreal, QC, CanadaDepartment of Paediatrics, University of Western Ontario, London, ON, CanadaDivision of Pediatric Cardiology, Department of Paediatrics, London Health Sciences Centre, London, ON, CanadaPediatric Cardiopulmonary Research Laboratory, London Health Sciences Centre, London, ON, CanadaChildren Health Research Institute, London, ON, CanadaDepartment of Surgery, The Hospital for Sick Children, Toronto, ON, CanadaLeft atrial appendage aneurysm (LAAA) is a rare cardiac pathology that is often identified in adulthood. There are a myriad of presentations related to atrial appendage enlargement, but most are asymptomatic. Pediatric cases of LAAA are extremely rare. We report a case of an incidental giant LAAA found in a healthy 6-year-old boy. He was successfully treated with surgical resection. A review of the literature shows that the presentation of LAAA in pediatrics likely involves cardiac or respiratory symptoms but can also be incidental findings. Similar to adults, diagnosis requires cardiac imaging, with echocardiography being the mainstay. Surgical intervention is indicated in symptomatic and most asymptomatic patients to prevent complications. More research is warranted into the optimal timing of surgery and alternative surgical approaches for complex cases.https://www.frontiersin.org/articles/10.3389/fcvm.2023.1211619/fullleft atrial appendage aneurysmpediatric cardiologypediatric cardiac surgerycase reportliterature review
spellingShingle Kambiz Norozi
Kambiz Norozi
Kambiz Norozi
Kambiz Norozi
Kambiz Norozi
Mathushan Subasri
Mathushan Subasri
Mathushan Subasri
Luis Altamirano Diaz
Luis Altamirano Diaz
Luis Altamirano Diaz
Luis Altamirano Diaz
Osami Honjo
Left atrial appendage aneurysm in pediatrics: Case study and literature review
Frontiers in Cardiovascular Medicine
left atrial appendage aneurysm
pediatric cardiology
pediatric cardiac surgery
case report
literature review
title Left atrial appendage aneurysm in pediatrics: Case study and literature review
title_full Left atrial appendage aneurysm in pediatrics: Case study and literature review
title_fullStr Left atrial appendage aneurysm in pediatrics: Case study and literature review
title_full_unstemmed Left atrial appendage aneurysm in pediatrics: Case study and literature review
title_short Left atrial appendage aneurysm in pediatrics: Case study and literature review
title_sort left atrial appendage aneurysm in pediatrics case study and literature review
topic left atrial appendage aneurysm
pediatric cardiology
pediatric cardiac surgery
case report
literature review
url https://www.frontiersin.org/articles/10.3389/fcvm.2023.1211619/full
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