Perivascular Epithelioid Cell Tumor (PEComa) of the Uterine Cervix in a Patient with Tuberous Sclerosis Complex: A Literature Review
Perivascular epithelioid cell tumors (PEComa) are a rare type of mesenchymal tumor arising from perivascular epithelial cells. These tumor cells are a co-expression of both melanocytic and myogenic antigens, such as HMB 45 and smooth muscle actin, and at least in some patients, are located around ve...
Main Authors: | , , , |
---|---|
Format: | Article |
Language: | English |
Published: |
Federation of Turkish Pathology Societies
2018-01-01
|
Series: | Türk Patoloji Dergisi |
Subjects: | |
Online Access: | http://www.turkjpath.org/pdf.php3?id=1710 |
_version_ | 1828021313952808960 |
---|---|
author | Handan ÇELİK Mehmet KEFELİ Mehmet ÇETİNKAYA Levent YILDIZ |
author_facet | Handan ÇELİK Mehmet KEFELİ Mehmet ÇETİNKAYA Levent YILDIZ |
author_sort | Handan ÇELİK |
collection | DOAJ |
description | Perivascular epithelioid cell tumors (PEComa) are a rare type of mesenchymal tumor arising from perivascular epithelial cells. These tumor cells are a co-expression of both melanocytic and myogenic antigens, such as HMB 45 and smooth muscle actin, and at least in some patients, are located around vessels. PEComas has been reported at various sites, including visceral organs, soft tissue, the prostate gland and broad ligaments. In the female reproductive system, the uterine corpus is the most common site of involvement. Some cases are related to tuberous sclerosis complex. Cervical PEComa with tuberous sclerosis complex is presented in the case of a 41 year-old and the literature is reviewed. There have been only eight cases of cervical PEComas and only one other case associated with tuberous sclerosis complex reported to date. |
first_indexed | 2024-04-10T11:51:12Z |
format | Article |
id | doaj.art-0d67e4d5f8a248319ae33244a4972604 |
institution | Directory Open Access Journal |
issn | 1018-5615 1309-5730 |
language | English |
last_indexed | 2024-04-10T11:51:12Z |
publishDate | 2018-01-01 |
publisher | Federation of Turkish Pathology Societies |
record_format | Article |
series | Türk Patoloji Dergisi |
spelling | doaj.art-0d67e4d5f8a248319ae33244a49726042023-02-15T16:17:07ZengFederation of Turkish Pathology SocietiesTürk Patoloji Dergisi1018-56151309-57302018-01-01341828610.5146/tjpath.2014.01274Perivascular Epithelioid Cell Tumor (PEComa) of the Uterine Cervix in a Patient with Tuberous Sclerosis Complex: A Literature ReviewHandan ÇELİKMehmet KEFELİMehmet ÇETİNKAYALevent YILDIZ Perivascular epithelioid cell tumors (PEComa) are a rare type of mesenchymal tumor arising from perivascular epithelial cells. These tumor cells are a co-expression of both melanocytic and myogenic antigens, such as HMB 45 and smooth muscle actin, and at least in some patients, are located around vessels. PEComas has been reported at various sites, including visceral organs, soft tissue, the prostate gland and broad ligaments. In the female reproductive system, the uterine corpus is the most common site of involvement. Some cases are related to tuberous sclerosis complex. Cervical PEComa with tuberous sclerosis complex is presented in the case of a 41 year-old and the literature is reviewed. There have been only eight cases of cervical PEComas and only one other case associated with tuberous sclerosis complex reported to date.http://www.turkjpath.org/pdf.php3?id=1710Perivascular epithelioid cell neoplasmUterine cervical neoplasmTuberous sclerosis |
spellingShingle | Handan ÇELİK Mehmet KEFELİ Mehmet ÇETİNKAYA Levent YILDIZ Perivascular Epithelioid Cell Tumor (PEComa) of the Uterine Cervix in a Patient with Tuberous Sclerosis Complex: A Literature Review Türk Patoloji Dergisi Perivascular epithelioid cell neoplasm Uterine cervical neoplasm Tuberous sclerosis |
title | Perivascular Epithelioid Cell Tumor (PEComa) of the Uterine Cervix in a Patient with Tuberous Sclerosis Complex: A Literature Review |
title_full | Perivascular Epithelioid Cell Tumor (PEComa) of the Uterine Cervix in a Patient with Tuberous Sclerosis Complex: A Literature Review |
title_fullStr | Perivascular Epithelioid Cell Tumor (PEComa) of the Uterine Cervix in a Patient with Tuberous Sclerosis Complex: A Literature Review |
title_full_unstemmed | Perivascular Epithelioid Cell Tumor (PEComa) of the Uterine Cervix in a Patient with Tuberous Sclerosis Complex: A Literature Review |
title_short | Perivascular Epithelioid Cell Tumor (PEComa) of the Uterine Cervix in a Patient with Tuberous Sclerosis Complex: A Literature Review |
title_sort | perivascular epithelioid cell tumor pecoma of the uterine cervix in a patient with tuberous sclerosis complex a literature review |
topic | Perivascular epithelioid cell neoplasm Uterine cervical neoplasm Tuberous sclerosis |
url | http://www.turkjpath.org/pdf.php3?id=1710 |
work_keys_str_mv | AT handancelik perivascularepithelioidcelltumorpecomaoftheuterinecervixinapatientwithtuberoussclerosiscomplexaliteraturereview AT mehmetkefeli perivascularepithelioidcelltumorpecomaoftheuterinecervixinapatientwithtuberoussclerosiscomplexaliteraturereview AT mehmetcetinkaya perivascularepithelioidcelltumorpecomaoftheuterinecervixinapatientwithtuberoussclerosiscomplexaliteraturereview AT leventyildiz perivascularepithelioidcelltumorpecomaoftheuterinecervixinapatientwithtuberoussclerosiscomplexaliteraturereview |