Splenic Rupture Secondary to Metastatic Undifferentiated Pleomorphic Sarcoma of the Spleen: A Rare Presentation of an Exceptionally Rare Entity
Splenic malignancies are uncommonly encountered in routine practice, and they are often only detected incidentally, posing a clinical challenge. Primary malignant neoplasms of the spleen are rare, and sarcomas are by far the rarest. The undifferentiated pleomorphic sarcoma type is an exceptionally r...
| Main Authors: | , , |
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| Format: | Article |
| Language: | English |
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Karger Publishers
2022-08-01
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| Series: | Case Reports in Oncology |
| Subjects: | |
| Online Access: | https://beta.karger.com/Article/FullText/525486 |
| _version_ | 1818029193260171264 |
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| author | Maher Darwish Ahmad AlAbdulkareem Fawaz AlAbdulkareem |
| author_facet | Maher Darwish Ahmad AlAbdulkareem Fawaz AlAbdulkareem |
| author_sort | Maher Darwish |
| collection | DOAJ |
| description | Splenic malignancies are uncommonly encountered in routine practice, and they are often only detected incidentally, posing a clinical challenge. Primary malignant neoplasms of the spleen are rare, and sarcomas are by far the rarest. The undifferentiated pleomorphic sarcoma type is an exceptionally rare and aggressive type with only a handful of cases reported in literature thus far. Herein, we present the case of a 49-year-old, with a previous finding of a heterogeneous splenomegaly on imaging for an unrelated medical complaint, presenting with an acute abdomen secondary to a ruptured spleen. The diagnosis of high-grade primary undifferentiated pleomorphic sarcoma of the spleen was made, and with further investigations, suspicious hepatic lesions were identified and later confirmed to be metastases. |
| first_indexed | 2024-12-10T05:15:48Z |
| format | Article |
| id | doaj.art-0e9c3a944cae443e8929307eee355c05 |
| institution | Directory Open Access Journal |
| issn | 1662-6575 |
| language | English |
| last_indexed | 2024-12-10T05:15:48Z |
| publishDate | 2022-08-01 |
| publisher | Karger Publishers |
| record_format | Article |
| series | Case Reports in Oncology |
| spelling | doaj.art-0e9c3a944cae443e8929307eee355c052022-12-22T02:00:58ZengKarger PublishersCase Reports in Oncology1662-65752022-08-0115275075410.1159/000525486525486Splenic Rupture Secondary to Metastatic Undifferentiated Pleomorphic Sarcoma of the Spleen: A Rare Presentation of an Exceptionally Rare EntityMaher Darwish0Ahmad AlAbdulkareem1https://orcid.org/0000-0002-2525-6921Fawaz AlAbdulkareem2Department of Medicine, Mubarak AlKabeer Hospital, Jabriya, KuwaitKuwait Institute for Medical Specializations, Ministry of Health, Andalous, KuwaitFaculty of Medicine, Kuwait University, Jabriya, KuwaitSplenic malignancies are uncommonly encountered in routine practice, and they are often only detected incidentally, posing a clinical challenge. Primary malignant neoplasms of the spleen are rare, and sarcomas are by far the rarest. The undifferentiated pleomorphic sarcoma type is an exceptionally rare and aggressive type with only a handful of cases reported in literature thus far. Herein, we present the case of a 49-year-old, with a previous finding of a heterogeneous splenomegaly on imaging for an unrelated medical complaint, presenting with an acute abdomen secondary to a ruptured spleen. The diagnosis of high-grade primary undifferentiated pleomorphic sarcoma of the spleen was made, and with further investigations, suspicious hepatic lesions were identified and later confirmed to be metastases.https://beta.karger.com/Article/FullText/525486cancerspleenraresarcomas |
| spellingShingle | Maher Darwish Ahmad AlAbdulkareem Fawaz AlAbdulkareem Splenic Rupture Secondary to Metastatic Undifferentiated Pleomorphic Sarcoma of the Spleen: A Rare Presentation of an Exceptionally Rare Entity Case Reports in Oncology cancer spleen rare sarcomas |
| title | Splenic Rupture Secondary to Metastatic Undifferentiated Pleomorphic Sarcoma of the Spleen: A Rare Presentation of an Exceptionally Rare Entity |
| title_full | Splenic Rupture Secondary to Metastatic Undifferentiated Pleomorphic Sarcoma of the Spleen: A Rare Presentation of an Exceptionally Rare Entity |
| title_fullStr | Splenic Rupture Secondary to Metastatic Undifferentiated Pleomorphic Sarcoma of the Spleen: A Rare Presentation of an Exceptionally Rare Entity |
| title_full_unstemmed | Splenic Rupture Secondary to Metastatic Undifferentiated Pleomorphic Sarcoma of the Spleen: A Rare Presentation of an Exceptionally Rare Entity |
| title_short | Splenic Rupture Secondary to Metastatic Undifferentiated Pleomorphic Sarcoma of the Spleen: A Rare Presentation of an Exceptionally Rare Entity |
| title_sort | splenic rupture secondary to metastatic undifferentiated pleomorphic sarcoma of the spleen a rare presentation of an exceptionally rare entity |
| topic | cancer spleen rare sarcomas |
| url | https://beta.karger.com/Article/FullText/525486 |
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