Obstructive Sleep Apnea in MPS

Obstructive Sleep Apnea in MPS

The mucopolysaccharidoses (MPSs) are a group of inherited, metabolic disorders characterized by progressive multisystem accumulation of partially degraded glycosaminoglycans. This manifests with multilevel airway obstruction, presenting with obstructive sleep apnea (OSA). We systematically reviewed...

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Bibliographic Details
Main Authors:	Abhijit Ricky Pal MBBChir, MA, MD, FRCS(ORL-HNS), Nailah Brown BSc, MPhil, Simon A. Jones MB ChB, MRCPCH, Brian W. Bigger PhD, Iain A. Bruce MB ChB, MD, FRCS(ORL-HNS)
Format:	Article
Language:	English
Published:	SciELO 2015-11-01
Series:	Journal of Inborn Errors of Metabolism and Screening
Online Access:	https://doi.org/10.1177/2326409815616392

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