Epignathus Leading to Fatal Airway Obstruction in a Neonate

Teratomas are benign tumours containing cells from ectodermal, mesodermal and endodermal layers with an incidence of about 1 in every 4,000 births. Their commonest site is sacro-coccygeal region, followed by anterior mediastinum. The incidence of teratomas localised to the head and neck region is...

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Main Authors: Shruti Sudhir Jadhav, Charusheela Sujit Korday, Sushma Malik, Vivek Kishor Shah, Shilpa Kapil Lad
Format: Article
Language:English
Published: JCDR Research and Publications Private Limited 2017-01-01
Series:Journal of Clinical and Diagnostic Research
Subjects:
Online Access:https://jcdr.net/articles/PDF/9283/24956_CE[Ra1]_F(DK)_PF1(HJ_RK)_PFA_NC(DK)_PF2(SH_DK).pdf
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author Shruti Sudhir Jadhav
Charusheela Sujit Korday
Sushma Malik
Vivek Kishor Shah
Shilpa Kapil Lad
author_facet Shruti Sudhir Jadhav
Charusheela Sujit Korday
Sushma Malik
Vivek Kishor Shah
Shilpa Kapil Lad
author_sort Shruti Sudhir Jadhav
collection DOAJ
description Teratomas are benign tumours containing cells from ectodermal, mesodermal and endodermal layers with an incidence of about 1 in every 4,000 births. Their commonest site is sacro-coccygeal region, followed by anterior mediastinum. The incidence of teratomas localised to the head and neck region is around 2–9% of all cases. Epignathus is a rare congenital oropharyngeal teratoma originating from the base of the skull. Here we present a rare case of oropharyngeal teratoma in a neonate who was referred to our institute with an ill-defined oral mass protruding through a cleft in the hard palate. Computed tomography scan showed a contrast-enhanced solid mass with areas of calcification and fat extending to oropharynx and nasal cavity with hard palate defect suggestive of a teratoma. Unfortunately, the patient succumbed due to respiratory compromise before the biopsy could be done. Postmortem histopathological examination confirmed diagnosis of benign teratoma consisting of mature tissue.
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spelling doaj.art-0f15f2ab431e46cc8391d98c956d1c8c2022-12-22T03:11:17ZengJCDR Research and Publications Private LimitedJournal of Clinical and Diagnostic Research2249-782X0973-709X2017-01-01111SD04SD0510.7860/JCDR/2017/24956.9283Epignathus Leading to Fatal Airway Obstruction in a NeonateShruti Sudhir Jadhav0Charusheela Sujit Korday1Sushma Malik2Vivek Kishor Shah3Shilpa Kapil Lad4Ex-Assistant Professor, Neonatology Division, Department of Pediatrics, TN Medical College and BYL Nair Hospital, Mumbai, Maharashtra, India.Ex-Associate Professor, Neonatology Division, Department of Pediatrics, TN Medical College and BYL Nair Hospital, Mumbai, Maharashtra, India.Professor and Incharge Neonatology, Neonatology Division, Department of Pediatrics, TN Medical College and BYL Nair Hospital, Mumbai, Maharashtra, India.Ex-Resident, Neonatology Division, Department of Pediatrics, TN Medical College and BYL Nair Hospital, Mumbai, Maharashtra, India.Associate Professor, Department of Pathology, TN Medical College and BYL Nair Hospital, Mumbai, Maharashtra, India.Teratomas are benign tumours containing cells from ectodermal, mesodermal and endodermal layers with an incidence of about 1 in every 4,000 births. Their commonest site is sacro-coccygeal region, followed by anterior mediastinum. The incidence of teratomas localised to the head and neck region is around 2–9% of all cases. Epignathus is a rare congenital oropharyngeal teratoma originating from the base of the skull. Here we present a rare case of oropharyngeal teratoma in a neonate who was referred to our institute with an ill-defined oral mass protruding through a cleft in the hard palate. Computed tomography scan showed a contrast-enhanced solid mass with areas of calcification and fat extending to oropharynx and nasal cavity with hard palate defect suggestive of a teratoma. Unfortunately, the patient succumbed due to respiratory compromise before the biopsy could be done. Postmortem histopathological examination confirmed diagnosis of benign teratoma consisting of mature tissue.https://jcdr.net/articles/PDF/9283/24956_CE[Ra1]_F(DK)_PF1(HJ_RK)_PFA_NC(DK)_PF2(SH_DK).pdfcleft palatecongenital teratomaoropharyngeal teratoma
spellingShingle Shruti Sudhir Jadhav
Charusheela Sujit Korday
Sushma Malik
Vivek Kishor Shah
Shilpa Kapil Lad
Epignathus Leading to Fatal Airway Obstruction in a Neonate
Journal of Clinical and Diagnostic Research
cleft palate
congenital teratoma
oropharyngeal teratoma
title Epignathus Leading to Fatal Airway Obstruction in a Neonate
title_full Epignathus Leading to Fatal Airway Obstruction in a Neonate
title_fullStr Epignathus Leading to Fatal Airway Obstruction in a Neonate
title_full_unstemmed Epignathus Leading to Fatal Airway Obstruction in a Neonate
title_short Epignathus Leading to Fatal Airway Obstruction in a Neonate
title_sort epignathus leading to fatal airway obstruction in a neonate
topic cleft palate
congenital teratoma
oropharyngeal teratoma
url https://jcdr.net/articles/PDF/9283/24956_CE[Ra1]_F(DK)_PF1(HJ_RK)_PFA_NC(DK)_PF2(SH_DK).pdf
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