Hemimegalencephaly without seizures
Hemimegalencephaly is a rare malformation of the brain characterized by enlargement of one cerebral hemisphere. The classic clinical triad consists of intractable epilepsy, severe psychomotor delay and hemiparesis. We report a case of a six months old girl, with the radiological features of hemimega...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
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London Academic Publishing
2017-09-01
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| Series: | Romanian Neurosurgery |
| Subjects: | |
| Online Access: | https://www.journals.lapub.co.uk/index.php/roneurosurgery/article/view/1013 |
| _version_ | 1811280179859816448 |
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| author | Agrawal Atul Dutta Gautam Singh Daljit Sachdeva Deepashu Gupta Robin |
| author_facet | Agrawal Atul Dutta Gautam Singh Daljit Sachdeva Deepashu Gupta Robin |
| author_sort | Agrawal Atul |
| collection | DOAJ |
| description | Hemimegalencephaly is a rare malformation of the brain characterized by enlargement of one cerebral hemisphere. The classic clinical triad consists of intractable epilepsy, severe psychomotor delay and hemiparesis. We report a case of a six months old girl, with the radiological features of hemimegalencephaly but with a comparatively benign clinical course. She had mild developmental delay but with no paresis or seizures. Literature revealed only two reported cases of hemimegalencephaly without the presence of seizures. We discuss the clinical and radiological findings of this third reported case. |
| first_indexed | 2024-04-13T01:09:34Z |
| format | Article |
| id | doaj.art-0f2c5b40d2df4e77bda5fd97dbd5d129 |
| institution | Directory Open Access Journal |
| issn | 1220-8841 2344-4959 |
| language | English |
| last_indexed | 2024-04-13T01:09:34Z |
| publishDate | 2017-09-01 |
| publisher | London Academic Publishing |
| record_format | Article |
| series | Romanian Neurosurgery |
| spelling | doaj.art-0f2c5b40d2df4e77bda5fd97dbd5d1292022-12-22T03:09:13ZengLondon Academic PublishingRomanian Neurosurgery1220-88412344-49592017-09-01313Hemimegalencephaly without seizuresAgrawal AtulDutta GautamSingh DaljitSachdeva DeepashuGupta RobinHemimegalencephaly is a rare malformation of the brain characterized by enlargement of one cerebral hemisphere. The classic clinical triad consists of intractable epilepsy, severe psychomotor delay and hemiparesis. We report a case of a six months old girl, with the radiological features of hemimegalencephaly but with a comparatively benign clinical course. She had mild developmental delay but with no paresis or seizures. Literature revealed only two reported cases of hemimegalencephaly without the presence of seizures. We discuss the clinical and radiological findings of this third reported case.https://www.journals.lapub.co.uk/index.php/roneurosurgery/article/view/1013Brain malformations hemimegalencephalyseizures |
| spellingShingle | Agrawal Atul Dutta Gautam Singh Daljit Sachdeva Deepashu Gupta Robin Hemimegalencephaly without seizures Romanian Neurosurgery Brain malformations hemimegalencephaly seizures |
| title | Hemimegalencephaly without seizures |
| title_full | Hemimegalencephaly without seizures |
| title_fullStr | Hemimegalencephaly without seizures |
| title_full_unstemmed | Hemimegalencephaly without seizures |
| title_short | Hemimegalencephaly without seizures |
| title_sort | hemimegalencephaly without seizures |
| topic | Brain malformations hemimegalencephaly seizures |
| url | https://www.journals.lapub.co.uk/index.php/roneurosurgery/article/view/1013 |
| work_keys_str_mv | AT agrawalatul hemimegalencephalywithoutseizures AT duttagautam hemimegalencephalywithoutseizures AT singhdaljit hemimegalencephalywithoutseizures AT sachdevadeepashu hemimegalencephalywithoutseizures AT guptarobin hemimegalencephalywithoutseizures |