TWO-STAGE SURGICAL TREATMENT OF A CHILD OF ONE YEAR FROM CONGENITAL HEART DISEASE AND BILIARY CIRRHOSIS
Aim: Clinical case of successful two-stage surgical treatment of a 1-year-old child with congenital heart disease and biliary cirrhosis is represented in this article. At the first day of life laparotomy was performed because of high intestinal obstruction. Kasai procedure and Roux-en-Y choledochoje...
| Main Authors: | , , , , , , , , , , |
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| Format: | Article |
| Language: | Russian |
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Federal Research Center of Transplantology and Artificial Organs named after V.I.Shumakov
2014-05-01
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| Series: | Vestnik Transplantologii i Iskusstvennyh Organov |
| Subjects: | |
| Online Access: | https://journal.transpl.ru/vtio/article/view/64 |
| _version_ | 1797872117507686400 |
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| author | S. V. Gautier A. S. Ivanov V. N. Poptsov O. M. Tsirulnikova S. V. Glamazda A. S. Rodionov A. V. Lebedeva H. M. Hizroev D. G. Ahaladze M. K. Lugovskiy I. V. Zhilkin |
| author_facet | S. V. Gautier A. S. Ivanov V. N. Poptsov O. M. Tsirulnikova S. V. Glamazda A. S. Rodionov A. V. Lebedeva H. M. Hizroev D. G. Ahaladze M. K. Lugovskiy I. V. Zhilkin |
| author_sort | S. V. Gautier |
| collection | DOAJ |
| description | Aim: Clinical case of successful two-stage surgical treatment of a 1-year-old child with congenital heart disease and biliary cirrhosis is represented in this article. At the first day of life laparotomy was performed because of high intestinal obstruction. Kasai procedure and Roux-en-Y choledochojejunostomy were per- formed on 12th day and at the end of second month of life, respectively. Liver biopsy showed the signs of biliary cirrhosis. At the same time ventricular septal defect and atrial septal defect with pulmonary hyper- tension were diagnosed. The first step of treatment was the surgical septal defects closure. No complications during procedure, cardiopulmonary bypass and post-operative period were registered. There were no nega- tive effects on liver function after cardiac surgery. 11 months later living-donor liver transplantation was performed without any complications. Patient was discharged at 35th post-transplant day with stable graft function. |
| first_indexed | 2024-04-10T00:54:48Z |
| format | Article |
| id | doaj.art-0f31a63d9e8640d0a4bdd030571b99cb |
| institution | Directory Open Access Journal |
| issn | 1995-1191 |
| language | Russian |
| last_indexed | 2024-04-10T00:54:48Z |
| publishDate | 2014-05-01 |
| publisher | Federal Research Center of Transplantology and Artificial Organs named after V.I.Shumakov |
| record_format | Article |
| series | Vestnik Transplantologii i Iskusstvennyh Organov |
| spelling | doaj.art-0f31a63d9e8640d0a4bdd030571b99cb2023-03-13T10:37:18ZrusFederal Research Center of Transplantology and Artificial Organs named after V.I.ShumakovVestnik Transplantologii i Iskusstvennyh Organov1995-11912014-05-01161414610.15825/1995-1191-2014-1-41-467TWO-STAGE SURGICAL TREATMENT OF A CHILD OF ONE YEAR FROM CONGENITAL HEART DISEASE AND BILIARY CIRRHOSISS. V. Gautier0A. S. Ivanov1V. N. Poptsov2O. M. Tsirulnikova3S. V. Glamazda4A. S. Rodionov5A. V. Lebedeva6H. M. Hizroev7D. G. Ahaladze8M. K. Lugovskiy9I. V. Zhilkin10«V.I. Shumakov Federal Research Center of Transplantology and Artificial Organs», Moscow, Russian Federation I.M. Sechenov First Moscow State Medical University. Chair of Transplantology and Artificial organs, Moscow, Russian FederationDivision of surgery of congenital heart diseases at the same centerDivision of emergency care and anesthesiology at the same centerI.M. Sechenov First Moscow State Medical University. Chair of Transplantology and Artificial organs, Moscow, Russian Federation Department of Clinical Transplantation at the same centerDivision of surgery of congenital heart diseases at the same centerDivision of surgery of congenital heart diseases at the same centerDivision of surgery of congenital heart diseases at the same centerDivision of abdominal surgery and Transplantation at the same centerDivision of abdominal surgery and Transplantation at the same centerDivision of surgery of congenital heart diseases at the same centerDivision of abdominal surgery and Transplantation at the same centerAim: Clinical case of successful two-stage surgical treatment of a 1-year-old child with congenital heart disease and biliary cirrhosis is represented in this article. At the first day of life laparotomy was performed because of high intestinal obstruction. Kasai procedure and Roux-en-Y choledochojejunostomy were per- formed on 12th day and at the end of second month of life, respectively. Liver biopsy showed the signs of biliary cirrhosis. At the same time ventricular septal defect and atrial septal defect with pulmonary hyper- tension were diagnosed. The first step of treatment was the surgical septal defects closure. No complications during procedure, cardiopulmonary bypass and post-operative period were registered. There were no nega- tive effects on liver function after cardiac surgery. 11 months later living-donor liver transplantation was performed without any complications. Patient was discharged at 35th post-transplant day with stable graft function.https://journal.transpl.ru/vtio/article/view/64ventricular septal defect, atrial septal defect, liver transplantation, biliary cirrhosis, cardiopulmonary bypass |
| spellingShingle | S. V. Gautier A. S. Ivanov V. N. Poptsov O. M. Tsirulnikova S. V. Glamazda A. S. Rodionov A. V. Lebedeva H. M. Hizroev D. G. Ahaladze M. K. Lugovskiy I. V. Zhilkin TWO-STAGE SURGICAL TREATMENT OF A CHILD OF ONE YEAR FROM CONGENITAL HEART DISEASE AND BILIARY CIRRHOSIS Vestnik Transplantologii i Iskusstvennyh Organov ventricular septal defect, atrial septal defect, liver transplantation, biliary cirrhosis, cardiopulmonary bypass |
| title | TWO-STAGE SURGICAL TREATMENT OF A CHILD OF ONE YEAR FROM CONGENITAL HEART DISEASE AND BILIARY CIRRHOSIS |
| title_full | TWO-STAGE SURGICAL TREATMENT OF A CHILD OF ONE YEAR FROM CONGENITAL HEART DISEASE AND BILIARY CIRRHOSIS |
| title_fullStr | TWO-STAGE SURGICAL TREATMENT OF A CHILD OF ONE YEAR FROM CONGENITAL HEART DISEASE AND BILIARY CIRRHOSIS |
| title_full_unstemmed | TWO-STAGE SURGICAL TREATMENT OF A CHILD OF ONE YEAR FROM CONGENITAL HEART DISEASE AND BILIARY CIRRHOSIS |
| title_short | TWO-STAGE SURGICAL TREATMENT OF A CHILD OF ONE YEAR FROM CONGENITAL HEART DISEASE AND BILIARY CIRRHOSIS |
| title_sort | two stage surgical treatment of a child of one year from congenital heart disease and biliary cirrhosis |
| topic | ventricular septal defect, atrial septal defect, liver transplantation, biliary cirrhosis, cardiopulmonary bypass |
| url | https://journal.transpl.ru/vtio/article/view/64 |
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