Low-grade fibromyxoid sarcoma arising in the mediastinum: Case report and review of the literature

Low-grade fibromyxoid sarcoma (LGFMS) is a rare tumor characterized by bland histological features and aggressive clinical course, it is a distinctive variant of fibrosarcoma with high metastasizing potential and sometimes a long interval between tumor presentation and metastasis, the most common an...

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Bibliographic Details
Main Authors: Rihab Aissaoui, MD, Siham Nasri, MD, Hajar Abdelouahab, MD, Hajar Mahjouba, MD, Narjisse Aichouni, MD, Said Afkir, MD, Hatim Kouismi, MD, Rachid Marouf, MD, Imane Kamaoui, MD, Imane Skiker, MD
Format: Article
Language:English
Published: Elsevier 2022-12-01
Series:Radiology Case Reports
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Online Access:http://www.sciencedirect.com/science/article/pii/S1930043322008019
Description
Summary:Low-grade fibromyxoid sarcoma (LGFMS) is a rare tumor characterized by bland histological features and aggressive clinical course, it is a distinctive variant of fibrosarcoma with high metastasizing potential and sometimes a long interval between tumor presentation and metastasis, the most common anatomic locations of occurrence are the lower extremities, thorax, inguinal area, and upper limbs, Here, we present the case of a 29-year-old patient with a deceptively benign-appearing mass arising in the mediastinum that had been discovered on computed tomography, a biopsy under cervicotomy was performed and histopathological examination revealed low-grade fibromyxoid sarcoma. In conclusion, LGFMS can arise in the mediastinum, and physicians should consider this entity as a differential diagnosis in the presence of such mass.
ISSN:1930-0433