Ayurvedic management of spondyloepiphyseal dysplasia tarda, a rare hereditary disorder

Spondyloepiphyseal dysplasia tarda (SEDT) is a rare genetic disease in which patient suffers from short stature, short trunk and neck with disproportionately long arms, coxa vara, skeletal features such as barrel shaped chest, kyphosis, scoliosis and early arthropathy. Only limited medical and surgi...

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Main Authors: Sarvesh Kumar Singh, Kshipra Rajoria
Format: Article
Language:English
Published: Elsevier 2016-10-01
Series:Journal of Ayurveda and Integrative Medicine
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S0975947616300456
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author Sarvesh Kumar Singh
Kshipra Rajoria
author_facet Sarvesh Kumar Singh
Kshipra Rajoria
author_sort Sarvesh Kumar Singh
collection DOAJ
description Spondyloepiphyseal dysplasia tarda (SEDT) is a rare genetic disease in which patient suffers from short stature, short trunk and neck with disproportionately long arms, coxa vara, skeletal features such as barrel shaped chest, kyphosis, scoliosis and early arthropathy. Only limited medical and surgical management is available in modern medicine. A 15 years old male suffering from SEDT and diagnosed as Vata vyadhi was treated with Panchakarma therapy and selected Ayurvedic oral medicines. Ayurvedic treatment was directed to ameliorate the orthopaedic clinical conditions in this case. Panchakarma procedures such as Shalishastika pinda svedana for a month and Mustadi yapana basti for 16 days were given along with oral Ayurvedic medicines. Same Panchakarma procedures were repeated after an interval of 2 months. A combination of Ayurvedic oral medicines such as Trayodashanga guggulu-500 mg twice a day, Dashmool kvatha (decoction of roots of 10 herbs) 40 ml twice a day, Eranda paka 10 g twice a day, Shiva gutika-500 mg twice a day and Dashmoolarista-20 ml (with equal water) twice a day were prescribed. Eight scales based Medical outcome study (MOS) – 36 item short form – health surveys was assessed for outcome which shows good improvement. Kyphosis, scoliosis and pain were moderately reduced. Clinical experience of this case indicates that Ayurvedic herbs along with Panchakarma can play a major role in the management of hereditary disorder SEDT.
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spelling doaj.art-1069b9bc49284c92abddea3507d8a1a52022-12-22T02:02:28ZengElsevierJournal of Ayurveda and Integrative Medicine0975-94762016-10-017424925410.1016/j.jaim.2016.10.002Ayurvedic management of spondyloepiphyseal dysplasia tarda, a rare hereditary disorderSarvesh Kumar Singh0Kshipra Rajoria1P.G. Department of Panchakarma, National Institute of Ayurveda, Jaipur, 302002, Rajasthan, IndiaS.S.S.B. Ayurvedic College and Hospital, Jaipur, 303603, Rajasthan, IndiaSpondyloepiphyseal dysplasia tarda (SEDT) is a rare genetic disease in which patient suffers from short stature, short trunk and neck with disproportionately long arms, coxa vara, skeletal features such as barrel shaped chest, kyphosis, scoliosis and early arthropathy. Only limited medical and surgical management is available in modern medicine. A 15 years old male suffering from SEDT and diagnosed as Vata vyadhi was treated with Panchakarma therapy and selected Ayurvedic oral medicines. Ayurvedic treatment was directed to ameliorate the orthopaedic clinical conditions in this case. Panchakarma procedures such as Shalishastika pinda svedana for a month and Mustadi yapana basti for 16 days were given along with oral Ayurvedic medicines. Same Panchakarma procedures were repeated after an interval of 2 months. A combination of Ayurvedic oral medicines such as Trayodashanga guggulu-500 mg twice a day, Dashmool kvatha (decoction of roots of 10 herbs) 40 ml twice a day, Eranda paka 10 g twice a day, Shiva gutika-500 mg twice a day and Dashmoolarista-20 ml (with equal water) twice a day were prescribed. Eight scales based Medical outcome study (MOS) – 36 item short form – health surveys was assessed for outcome which shows good improvement. Kyphosis, scoliosis and pain were moderately reduced. Clinical experience of this case indicates that Ayurvedic herbs along with Panchakarma can play a major role in the management of hereditary disorder SEDT.http://www.sciencedirect.com/science/article/pii/S0975947616300456Ayurvedic managementMustadi yapana bastiShalishastika pinda svedanaSpondyloepiphyseal dysplasia tardaVata vyadhi
spellingShingle Sarvesh Kumar Singh
Kshipra Rajoria
Ayurvedic management of spondyloepiphyseal dysplasia tarda, a rare hereditary disorder
Journal of Ayurveda and Integrative Medicine
Ayurvedic management
Mustadi yapana basti
Shalishastika pinda svedana
Spondyloepiphyseal dysplasia tarda
Vata vyadhi
title Ayurvedic management of spondyloepiphyseal dysplasia tarda, a rare hereditary disorder
title_full Ayurvedic management of spondyloepiphyseal dysplasia tarda, a rare hereditary disorder
title_fullStr Ayurvedic management of spondyloepiphyseal dysplasia tarda, a rare hereditary disorder
title_full_unstemmed Ayurvedic management of spondyloepiphyseal dysplasia tarda, a rare hereditary disorder
title_short Ayurvedic management of spondyloepiphyseal dysplasia tarda, a rare hereditary disorder
title_sort ayurvedic management of spondyloepiphyseal dysplasia tarda a rare hereditary disorder
topic Ayurvedic management
Mustadi yapana basti
Shalishastika pinda svedana
Spondyloepiphyseal dysplasia tarda
Vata vyadhi
url http://www.sciencedirect.com/science/article/pii/S0975947616300456
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