Supravalvular aortic stenosis with sudden cardiac death
Sudden cardiac death (SCD) most commonly results from previously undiagnosed congenital, acquired, or hereditary cardiac diseases. Congenital aortic valvular, subvalvular, and supravalvular disease with left ventricular outflow tract obstruction is an important preventable cause of sudden death. Thi...
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Format: | Article |
Language: | English |
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Wolters Kluwer Medknow Publications
2015-01-01
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Series: | Annals of Pediatric Cardiology |
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Online Access: | http://www.annalspc.com/article.asp?issn=0974-2069;year=2015;volume=8;issue=2;spage=134;epage=136;aulast=Vaideeswar |
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author | Pradeep Vaideeswar Preet Regi |
author_facet | Pradeep Vaideeswar Preet Regi |
author_sort | Pradeep Vaideeswar |
collection | DOAJ |
description | Sudden cardiac death (SCD) most commonly results from previously undiagnosed congenital, acquired, or hereditary cardiac diseases. Congenital aortic valvular, subvalvular, and supravalvular disease with left ventricular outflow tract obstruction is an important preventable cause of sudden death. This report documents sudden death presumably due to acute myocardial ischemia in a young male with an undiagnosed supravalvular aortic stenosis (SVAS) due to a rare association of isolation of coronary sinuses of Valsalva. Congenital supravalvular pulmonary stenosis and mitral valvular dysplasia were also present. |
first_indexed | 2024-12-21T07:43:35Z |
format | Article |
id | doaj.art-106d86a0901942fc98426b91344bd072 |
institution | Directory Open Access Journal |
issn | 0974-2069 |
language | English |
last_indexed | 2024-12-21T07:43:35Z |
publishDate | 2015-01-01 |
publisher | Wolters Kluwer Medknow Publications |
record_format | Article |
series | Annals of Pediatric Cardiology |
spelling | doaj.art-106d86a0901942fc98426b91344bd0722022-12-21T19:11:16ZengWolters Kluwer Medknow PublicationsAnnals of Pediatric Cardiology0974-20692015-01-018213413610.4103/0974-2069.157027Supravalvular aortic stenosis with sudden cardiac deathPradeep VaideeswarPreet RegiSudden cardiac death (SCD) most commonly results from previously undiagnosed congenital, acquired, or hereditary cardiac diseases. Congenital aortic valvular, subvalvular, and supravalvular disease with left ventricular outflow tract obstruction is an important preventable cause of sudden death. This report documents sudden death presumably due to acute myocardial ischemia in a young male with an undiagnosed supravalvular aortic stenosis (SVAS) due to a rare association of isolation of coronary sinuses of Valsalva. Congenital supravalvular pulmonary stenosis and mitral valvular dysplasia were also present.http://www.annalspc.com/article.asp?issn=0974-2069;year=2015;volume=8;issue=2;spage=134;epage=136;aulast=VaideeswarCongenital aortic stenosiselastin arteriopathysupravalvular aortic stenosissudden cardiac deathsinus of Valsalva isolation |
spellingShingle | Pradeep Vaideeswar Preet Regi Supravalvular aortic stenosis with sudden cardiac death Annals of Pediatric Cardiology Congenital aortic stenosis elastin arteriopathy supravalvular aortic stenosis sudden cardiac death sinus of Valsalva isolation |
title | Supravalvular aortic stenosis with sudden cardiac death |
title_full | Supravalvular aortic stenosis with sudden cardiac death |
title_fullStr | Supravalvular aortic stenosis with sudden cardiac death |
title_full_unstemmed | Supravalvular aortic stenosis with sudden cardiac death |
title_short | Supravalvular aortic stenosis with sudden cardiac death |
title_sort | supravalvular aortic stenosis with sudden cardiac death |
topic | Congenital aortic stenosis elastin arteriopathy supravalvular aortic stenosis sudden cardiac death sinus of Valsalva isolation |
url | http://www.annalspc.com/article.asp?issn=0974-2069;year=2015;volume=8;issue=2;spage=134;epage=136;aulast=Vaideeswar |
work_keys_str_mv | AT pradeepvaideeswar supravalvularaorticstenosiswithsuddencardiacdeath AT preetregi supravalvularaorticstenosiswithsuddencardiacdeath |