Supravalvular aortic stenosis with sudden cardiac death

Sudden cardiac death (SCD) most commonly results from previously undiagnosed congenital, acquired, or hereditary cardiac diseases. Congenital aortic valvular, subvalvular, and supravalvular disease with left ventricular outflow tract obstruction is an important preventable cause of sudden death. Thi...

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Main Authors: Pradeep Vaideeswar, Preet Regi
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2015-01-01
Series:Annals of Pediatric Cardiology
Subjects:
Online Access:http://www.annalspc.com/article.asp?issn=0974-2069;year=2015;volume=8;issue=2;spage=134;epage=136;aulast=Vaideeswar
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author Pradeep Vaideeswar
Preet Regi
author_facet Pradeep Vaideeswar
Preet Regi
author_sort Pradeep Vaideeswar
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description Sudden cardiac death (SCD) most commonly results from previously undiagnosed congenital, acquired, or hereditary cardiac diseases. Congenital aortic valvular, subvalvular, and supravalvular disease with left ventricular outflow tract obstruction is an important preventable cause of sudden death. This report documents sudden death presumably due to acute myocardial ischemia in a young male with an undiagnosed supravalvular aortic stenosis (SVAS) due to a rare association of isolation of coronary sinuses of Valsalva. Congenital supravalvular pulmonary stenosis and mitral valvular dysplasia were also present.
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spelling doaj.art-106d86a0901942fc98426b91344bd0722022-12-21T19:11:16ZengWolters Kluwer Medknow PublicationsAnnals of Pediatric Cardiology0974-20692015-01-018213413610.4103/0974-2069.157027Supravalvular aortic stenosis with sudden cardiac deathPradeep VaideeswarPreet RegiSudden cardiac death (SCD) most commonly results from previously undiagnosed congenital, acquired, or hereditary cardiac diseases. Congenital aortic valvular, subvalvular, and supravalvular disease with left ventricular outflow tract obstruction is an important preventable cause of sudden death. This report documents sudden death presumably due to acute myocardial ischemia in a young male with an undiagnosed supravalvular aortic stenosis (SVAS) due to a rare association of isolation of coronary sinuses of Valsalva. Congenital supravalvular pulmonary stenosis and mitral valvular dysplasia were also present.http://www.annalspc.com/article.asp?issn=0974-2069;year=2015;volume=8;issue=2;spage=134;epage=136;aulast=VaideeswarCongenital aortic stenosiselastin arteriopathysupravalvular aortic stenosissudden cardiac deathsinus of Valsalva isolation
spellingShingle Pradeep Vaideeswar
Preet Regi
Supravalvular aortic stenosis with sudden cardiac death
Annals of Pediatric Cardiology
Congenital aortic stenosis
elastin arteriopathy
supravalvular aortic stenosis
sudden cardiac death
sinus of Valsalva isolation
title Supravalvular aortic stenosis with sudden cardiac death
title_full Supravalvular aortic stenosis with sudden cardiac death
title_fullStr Supravalvular aortic stenosis with sudden cardiac death
title_full_unstemmed Supravalvular aortic stenosis with sudden cardiac death
title_short Supravalvular aortic stenosis with sudden cardiac death
title_sort supravalvular aortic stenosis with sudden cardiac death
topic Congenital aortic stenosis
elastin arteriopathy
supravalvular aortic stenosis
sudden cardiac death
sinus of Valsalva isolation
url http://www.annalspc.com/article.asp?issn=0974-2069;year=2015;volume=8;issue=2;spage=134;epage=136;aulast=Vaideeswar
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AT preetregi supravalvularaorticstenosiswithsuddencardiacdeath