Adult Presentation of Dyke-Davidoff-Masson Syndrome: A Case Report
Dyke-Davidoff-Masson syndrome (DDMS) is a rare disease which is clinically characterized by hemiparesis, seizures, facial asymmetry, and mental retardation. The classical radiological findings are cerebral hemiatrophy, calvarial thickening, and hyperpneumatization of the frontal sinuses. This diseas...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Karger Publishers
2016-01-01
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| Series: | Case Reports in Neurology |
| Subjects: | |
| Online Access: | http://www.karger.com/Article/FullText/443521 |
| _version_ | 1819080911657893888 |
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| author | Ujjawal Roy Ajay Panwar Adreesh Mukherjee Debsadhan Biswas |
| author_facet | Ujjawal Roy Ajay Panwar Adreesh Mukherjee Debsadhan Biswas |
| author_sort | Ujjawal Roy |
| collection | DOAJ |
| description | Dyke-Davidoff-Masson syndrome (DDMS) is a rare disease which is clinically characterized by hemiparesis, seizures, facial asymmetry, and mental retardation. The classical radiological findings are cerebral hemiatrophy, calvarial thickening, and hyperpneumatization of the frontal sinuses. This disease is a rare entity, and it mainly presents in childhood. Adult presentation of DDMS is unusual and has been rarely reported in the medical literature. Key Messages: DDMS is a rare disease of childhood. However, it should be kept in mind as a diagnostic possibility in an adult who presents with a long duration of progressive hemiparesis with seizures and mental retardation. Cerebral hemiatrophy, calvarial thickening, and hyperpneumatization of the frontal sinuses are diagnostic for this illness on brain imaging. |
| first_indexed | 2024-12-21T19:52:24Z |
| format | Article |
| id | doaj.art-1099e5b4bd754165ae3236dc7c329973 |
| institution | Directory Open Access Journal |
| issn | 1662-680X |
| language | English |
| last_indexed | 2024-12-21T19:52:24Z |
| publishDate | 2016-01-01 |
| publisher | Karger Publishers |
| record_format | Article |
| series | Case Reports in Neurology |
| spelling | doaj.art-1099e5b4bd754165ae3236dc7c3299732022-12-21T18:52:10ZengKarger PublishersCase Reports in Neurology1662-680X2016-01-0181202610.1159/000443521443521Adult Presentation of Dyke-Davidoff-Masson Syndrome: A Case ReportUjjawal RoyAjay PanwarAdreesh MukherjeeDebsadhan BiswasDyke-Davidoff-Masson syndrome (DDMS) is a rare disease which is clinically characterized by hemiparesis, seizures, facial asymmetry, and mental retardation. The classical radiological findings are cerebral hemiatrophy, calvarial thickening, and hyperpneumatization of the frontal sinuses. This disease is a rare entity, and it mainly presents in childhood. Adult presentation of DDMS is unusual and has been rarely reported in the medical literature. Key Messages: DDMS is a rare disease of childhood. However, it should be kept in mind as a diagnostic possibility in an adult who presents with a long duration of progressive hemiparesis with seizures and mental retardation. Cerebral hemiatrophy, calvarial thickening, and hyperpneumatization of the frontal sinuses are diagnostic for this illness on brain imaging.http://www.karger.com/Article/FullText/443521Dyke-Davidoff-Masson syndromeCerebral hemiatrophyCalvarial thickening |
| spellingShingle | Ujjawal Roy Ajay Panwar Adreesh Mukherjee Debsadhan Biswas Adult Presentation of Dyke-Davidoff-Masson Syndrome: A Case Report Case Reports in Neurology Dyke-Davidoff-Masson syndrome Cerebral hemiatrophy Calvarial thickening |
| title | Adult Presentation of Dyke-Davidoff-Masson Syndrome: A Case Report |
| title_full | Adult Presentation of Dyke-Davidoff-Masson Syndrome: A Case Report |
| title_fullStr | Adult Presentation of Dyke-Davidoff-Masson Syndrome: A Case Report |
| title_full_unstemmed | Adult Presentation of Dyke-Davidoff-Masson Syndrome: A Case Report |
| title_short | Adult Presentation of Dyke-Davidoff-Masson Syndrome: A Case Report |
| title_sort | adult presentation of dyke davidoff masson syndrome a case report |
| topic | Dyke-Davidoff-Masson syndrome Cerebral hemiatrophy Calvarial thickening |
| url | http://www.karger.com/Article/FullText/443521 |
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