Congenital megalourethra with delayed obstructive symptoms

Congenital megalourethra is a congenital non-obstructive dilation of the male urethra often associated with VACTERL anomaly malformations. We report a case of TE fistula associated congenital megalourethra with symptoms presenting approximately 2 months postpartum. At the time of referral, patient h...

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Main Authors: Sohum K. Patel, Ross Simon, Diana Cardona-Grau, Mark A. Rich, Hubert S. Swana
Format: Article
Language:English
Published: Elsevier 2019-08-01
Series:Journal of Pediatric Surgery Case Reports
Online Access:http://www.sciencedirect.com/science/article/pii/S221357661830335X
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author Sohum K. Patel
Ross Simon
Diana Cardona-Grau
Mark A. Rich
Hubert S. Swana
author_facet Sohum K. Patel
Ross Simon
Diana Cardona-Grau
Mark A. Rich
Hubert S. Swana
author_sort Sohum K. Patel
collection DOAJ
description Congenital megalourethra is a congenital non-obstructive dilation of the male urethra often associated with VACTERL anomaly malformations. We report a case of TE fistula associated congenital megalourethra with symptoms presenting approximately 2 months postpartum. At the time of referral, patient had distal penile flaccidity and poorly developed corpora. Imaging and cystoscopy showed development of hydronephrosis with significant sediment in the bladder. Attempts at retrograde catheterization failed, thus a Blocksum vesicostomy was required. This demonstrates the importance of serial physical examinations and ultrasound surveillance in patients with megalourethra.
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spelling doaj.art-10a5f2f47c9c4108a8cf2727e649c2632022-12-22T03:31:00ZengElsevierJournal of Pediatric Surgery Case Reports2213-57662019-08-0147Congenital megalourethra with delayed obstructive symptomsSohum K. Patel0Ross Simon1Diana Cardona-Grau2Mark A. Rich3Hubert S. Swana4University of Central Florida College of Medicine, 6850 Lake Nona Blvd, Orlando, FL 32827, United States; Corresponding author.University of South Florida Morsani College of Medicine, 12901 Bruce B Downs Blvd, Tampa, FL 33612, United StatesOrlando Health Arnold Palmer Hospital for Children, 92 W Miller St, Orlando, FL 32806, United StatesOrlando Health Arnold Palmer Hospital for Children, 92 W Miller St, Orlando, FL 32806, United StatesOrlando Health Arnold Palmer Hospital for Children, 92 W Miller St, Orlando, FL 32806, United StatesCongenital megalourethra is a congenital non-obstructive dilation of the male urethra often associated with VACTERL anomaly malformations. We report a case of TE fistula associated congenital megalourethra with symptoms presenting approximately 2 months postpartum. At the time of referral, patient had distal penile flaccidity and poorly developed corpora. Imaging and cystoscopy showed development of hydronephrosis with significant sediment in the bladder. Attempts at retrograde catheterization failed, thus a Blocksum vesicostomy was required. This demonstrates the importance of serial physical examinations and ultrasound surveillance in patients with megalourethra.http://www.sciencedirect.com/science/article/pii/S221357661830335X
spellingShingle Sohum K. Patel
Ross Simon
Diana Cardona-Grau
Mark A. Rich
Hubert S. Swana
Congenital megalourethra with delayed obstructive symptoms
Journal of Pediatric Surgery Case Reports
title Congenital megalourethra with delayed obstructive symptoms
title_full Congenital megalourethra with delayed obstructive symptoms
title_fullStr Congenital megalourethra with delayed obstructive symptoms
title_full_unstemmed Congenital megalourethra with delayed obstructive symptoms
title_short Congenital megalourethra with delayed obstructive symptoms
title_sort congenital megalourethra with delayed obstructive symptoms
url http://www.sciencedirect.com/science/article/pii/S221357661830335X
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AT markarich congenitalmegalourethrawithdelayedobstructivesymptoms
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