Síndrome de Wilson

Síndrome de Wilson

Objetivos: Este relato descreve um distúrbio genético raro, denominado de Síndrome de Wilson, herdado em caráter autossômico recessivo, com sintomas muito facilmente confundidos com outras doenças. A causa básica responsável pelas manifestações clínicas é o acúmulo de cobre em diversos compartimento...

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Bibliographic Details
Main Authors:	Alessandra dos Santos Danziger Silvério, Thaís dos Santos Couto, Juliana Marília Pereira de Oliveira
Format:	Article
Language:	Portuguese
Published:	Universidade de São Paulo 2018-09-01
Series:	Medicina
Subjects:	Doença de Wilson. Cobre. Degeneração hepatolenticular. Penicilamina.
Online Access:	http://www.revistas.usp.br/rmrp/article/view/150085

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