Unilateral pulmonary artery agenesis: An unusual cause of hemoptysis
Introduction: Unilateral pulmonary artery agenesis (UPAA) is a rare congenital malformation of the pulmonary artery due to agenesis of the sixth aortic arch during embryogenesis. Diagnosis can be challenging due to variable clinical presentations. Case: A 29-year-old female at third trimester of twi...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
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Elsevier
2023-01-01
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| Series: | Respiratory Medicine Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2213007123000291 |
| _version_ | 1797832269102055424 |
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| author | Yen Shen Wong Zakhirati Zainol Abidin Aisya Natasya Musa Roqiah Fatmawati Abdul Kadir Bushra Johari |
| author_facet | Yen Shen Wong Zakhirati Zainol Abidin Aisya Natasya Musa Roqiah Fatmawati Abdul Kadir Bushra Johari |
| author_sort | Yen Shen Wong |
| collection | DOAJ |
| description | Introduction: Unilateral pulmonary artery agenesis (UPAA) is a rare congenital malformation of the pulmonary artery due to agenesis of the sixth aortic arch during embryogenesis. Diagnosis can be challenging due to variable clinical presentations. Case: A 29-year-old female at third trimester of twin pregnancy presented with massive hemoptysis. Computed tomography angiogram (CTA) showed unilateral absence of the right pulmonary artery with multiple dilated tortuous bronchial arteries supplying the right lung. Selective embolization of the bronchial artery was performed post-partum. Conclusion: Clinicians should have a high clinical suspicion of collateral artery bleeding in patients who present with unexplained hemoptysis and typical UPAA radiographic findings. |
| first_indexed | 2024-04-09T14:06:11Z |
| format | Article |
| id | doaj.art-11607810c13a410eb2c43e29d3e60ace |
| institution | Directory Open Access Journal |
| issn | 2213-0071 |
| language | English |
| last_indexed | 2024-04-09T14:06:11Z |
| publishDate | 2023-01-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Respiratory Medicine Case Reports |
| spelling | doaj.art-11607810c13a410eb2c43e29d3e60ace2023-05-07T04:16:46ZengElsevierRespiratory Medicine Case Reports2213-00712023-01-0143101834Unilateral pulmonary artery agenesis: An unusual cause of hemoptysisYen Shen Wong0Zakhirati Zainol Abidin1Aisya Natasya Musa2Roqiah Fatmawati Abdul Kadir3Bushra Johari4Faculty of Medicine, Universiti Teknologi MARA, Sungai Buloh, Malaysia; Corresponding author.Department of Radiology, Hospital Selayang, Batu Caves, MalaysiaFaculty of Medicine, Universiti Teknologi MARA, Sungai Buloh, MalaysiaDepartment of Radiology, Universiti Teknologi MARA, Sungai Buloh, MalaysiaDepartment of Radiology, Universiti Teknologi MARA, Sungai Buloh, MalaysiaIntroduction: Unilateral pulmonary artery agenesis (UPAA) is a rare congenital malformation of the pulmonary artery due to agenesis of the sixth aortic arch during embryogenesis. Diagnosis can be challenging due to variable clinical presentations. Case: A 29-year-old female at third trimester of twin pregnancy presented with massive hemoptysis. Computed tomography angiogram (CTA) showed unilateral absence of the right pulmonary artery with multiple dilated tortuous bronchial arteries supplying the right lung. Selective embolization of the bronchial artery was performed post-partum. Conclusion: Clinicians should have a high clinical suspicion of collateral artery bleeding in patients who present with unexplained hemoptysis and typical UPAA radiographic findings.http://www.sciencedirect.com/science/article/pii/S2213007123000291Unilateral pulmonary artery agenesisHemoptysisBronchial artery aneurysm |
| spellingShingle | Yen Shen Wong Zakhirati Zainol Abidin Aisya Natasya Musa Roqiah Fatmawati Abdul Kadir Bushra Johari Unilateral pulmonary artery agenesis: An unusual cause of hemoptysis Respiratory Medicine Case Reports Unilateral pulmonary artery agenesis Hemoptysis Bronchial artery aneurysm |
| title | Unilateral pulmonary artery agenesis: An unusual cause of hemoptysis |
| title_full | Unilateral pulmonary artery agenesis: An unusual cause of hemoptysis |
| title_fullStr | Unilateral pulmonary artery agenesis: An unusual cause of hemoptysis |
| title_full_unstemmed | Unilateral pulmonary artery agenesis: An unusual cause of hemoptysis |
| title_short | Unilateral pulmonary artery agenesis: An unusual cause of hemoptysis |
| title_sort | unilateral pulmonary artery agenesis an unusual cause of hemoptysis |
| topic | Unilateral pulmonary artery agenesis Hemoptysis Bronchial artery aneurysm |
| url | http://www.sciencedirect.com/science/article/pii/S2213007123000291 |
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