C1-inhibitor/C1-inhibitor antibody complexes in acquired angioedema due to C1-inhibitor deficiency
Abstract Background Autoantibodies against C1-inhibitor (C1-INH-Ab) have a diagnostic value in acquired angioedema due to C1-inhibitor deficiency (C1-INH-AAE), even though antibodies can circulate in complexes, which can be undetectable by proven methods. Our aim was to measure C1-INH/C1-INH-Ab comp...
Main Authors: | Zsofia Polai, Erika Kajdacsi, Laszlo Cervenak, Zsuzsanna Balla, Szabolcs Benedek, Lilian Varga, Henriette Farkas |
---|---|
Format: | Article |
Language: | English |
Published: |
BMC
2023-02-01
|
Series: | Orphanet Journal of Rare Diseases |
Subjects: | |
Online Access: | https://doi.org/10.1186/s13023-023-02625-5 |
Similar Items
-
Long term follow-up of complement parameters to improve the management of acquired angioedema due to C1-inhibitor deficiency
by: Zsofia Polai, et al.
Published: (2022-11-01) -
The Role of Bradykinin Receptors in Hereditary Angioedema Due to C1-Inhibitor Deficiency
by: Wojciech Dyga, et al.
Published: (2022-09-01) -
Editorial: C1 inhibitor deficiency and angioedema
by: Henriette Farkas, et al.
Published: (2022-11-01) -
Hypersensitivity reactions amongst Hungarian Patients with Hereditary Angioedema due to C1-Inhibitor Deficiency
by: Hanga Réka Horváth, MD, et al.
Published: (2023-11-01) -
Clinical Characteristics and Management of Angioedema Attacks in Polish Adult Patients with Hereditary Angioedema Due to C1-Inhibitor Deficiency
by: Katarzyna Piotrowicz-Wójcik, et al.
Published: (2021-11-01)