Pneumonectomy in a child with congenital bronchiectasis: A case report and review of literature

Williams-Campbell syndrome was first described in 1960 as a rare form of bronchiectasis. Its pathogenesis is characterized by the absence of or markedly diminished bronchial cartilage. We describe a case of a 4-year-old male child in whom respiratory symptoms developed in neonatal period and were fo...

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Main Authors: Shankar Gowri, Kothari Paras, Sarda Dinesh, Kulkarni Bharati, Kalgutkar Alka
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2006-01-01
Series:Annals of Thoracic Medicine
Subjects:
Online Access:http://www.thoracicmedicine.org/article.asp?issn=1817-1737;year=2006;volume=1;issue=2;spage=81;epage=83;aulast=Shankar
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author Shankar Gowri
Kothari Paras
Sarda Dinesh
Kulkarni Bharati
Kalgutkar Alka
author_facet Shankar Gowri
Kothari Paras
Sarda Dinesh
Kulkarni Bharati
Kalgutkar Alka
author_sort Shankar Gowri
collection DOAJ
description Williams-Campbell syndrome was first described in 1960 as a rare form of bronchiectasis. Its pathogenesis is characterized by the absence of or markedly diminished bronchial cartilage. We describe a case of a 4-year-old male child in whom respiratory symptoms developed in neonatal period and were found to have histopathological changes consistent with Williams-Campbell syndrome. A brief review of literature has been discussed.
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spelling doaj.art-1360014ed963475288f28914e622f87a2022-12-21T19:08:08ZengWolters Kluwer Medknow PublicationsAnnals of Thoracic Medicine1817-17372006-01-01128183Pneumonectomy in a child with congenital bronchiectasis: A case report and review of literatureShankar GowriKothari ParasSarda DineshKulkarni BharatiKalgutkar AlkaWilliams-Campbell syndrome was first described in 1960 as a rare form of bronchiectasis. Its pathogenesis is characterized by the absence of or markedly diminished bronchial cartilage. We describe a case of a 4-year-old male child in whom respiratory symptoms developed in neonatal period and were found to have histopathological changes consistent with Williams-Campbell syndrome. A brief review of literature has been discussed.http://www.thoracicmedicine.org/article.asp?issn=1817-1737;year=2006;volume=1;issue=2;spage=81;epage=83;aulast=ShankarCartilage deficiencycongenital bronchiectasispneumonectomy
spellingShingle Shankar Gowri
Kothari Paras
Sarda Dinesh
Kulkarni Bharati
Kalgutkar Alka
Pneumonectomy in a child with congenital bronchiectasis: A case report and review of literature
Annals of Thoracic Medicine
Cartilage deficiency
congenital bronchiectasis
pneumonectomy
title Pneumonectomy in a child with congenital bronchiectasis: A case report and review of literature
title_full Pneumonectomy in a child with congenital bronchiectasis: A case report and review of literature
title_fullStr Pneumonectomy in a child with congenital bronchiectasis: A case report and review of literature
title_full_unstemmed Pneumonectomy in a child with congenital bronchiectasis: A case report and review of literature
title_short Pneumonectomy in a child with congenital bronchiectasis: A case report and review of literature
title_sort pneumonectomy in a child with congenital bronchiectasis a case report and review of literature
topic Cartilage deficiency
congenital bronchiectasis
pneumonectomy
url http://www.thoracicmedicine.org/article.asp?issn=1817-1737;year=2006;volume=1;issue=2;spage=81;epage=83;aulast=Shankar
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AT sardadinesh pneumonectomyinachildwithcongenitalbronchiectasisacasereportandreviewofliterature
AT kulkarnibharati pneumonectomyinachildwithcongenitalbronchiectasisacasereportandreviewofliterature
AT kalgutkaralka pneumonectomyinachildwithcongenitalbronchiectasisacasereportandreviewofliterature