Anesthetic experience of a patient with Ohtahara syndrome -A case report-

Ohtahara syndrome (OS) is a rare epileptic encephalopathy that is characterized by an abnormal electroencephalogram (EEG) and intractable seizures in the neonatal and early infantile period. The patient of this reported case was delivered normally at 39 weeks of gestation without any complication. O...

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Main Authors: Eun Mi Choi, Kyeong Tae Min, Jin Sun Cho, Seung Ho Choi
Format: Article
Language:English
Published: Korean Society of Anesthesiologists 2011-02-01
Series:Korean Journal of Anesthesiology
Subjects:
Online Access:http://ekja.org/upload/pdf/kjae-60-124.pdf
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author Eun Mi Choi
Kyeong Tae Min
Jin Sun Cho
Seung Ho Choi
author_facet Eun Mi Choi
Kyeong Tae Min
Jin Sun Cho
Seung Ho Choi
author_sort Eun Mi Choi
collection DOAJ
description Ohtahara syndrome (OS) is a rare epileptic encephalopathy that is characterized by an abnormal electroencephalogram (EEG) and intractable seizures in the neonatal and early infantile period. The patient of this reported case was delivered normally at 39 weeks of gestation without any complication. One week after birth, seizures that were refractory to anticonvulsants started with repetitive clustered tonic spasms. The child had no abnormal findings on the initial laboratory investigations. But he was diagnosed with OS according to the frequent tonic spasms, an abnormal EEG pattern of suppression-burst and magnetic resonance imaging of cortical dysplasia. He was planned to undergo an operation for brain lesion. This report describes our experience with the general anesthetic management when we performed craniotomy and right hemispherotomy for a patient with OS.
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spelling doaj.art-13ca34349a8b4337bcad2c4a5411131d2022-12-21T23:07:27ZengKorean Society of AnesthesiologistsKorean Journal of Anesthesiology2005-64192005-75632011-02-0160212412710.4097/kjae.2011.60.2.1247078Anesthetic experience of a patient with Ohtahara syndrome -A case report-Eun Mi Choi0Kyeong Tae Min1Jin Sun Cho2Seung Ho Choi3Department of Anesthesiology and Pain Medicine, Hallym University College of Medicine, Chuncheon, Korea.Department of Anesthesiology and Pain Medicine, Anesthesia and Pain Research Institute, Yonsei University College of Medicine, Seoul, Korea.Department of Anesthesiology and Pain Medicine, Anesthesia and Pain Research Institute, Yonsei University College of Medicine, Seoul, Korea.Department of Anesthesiology and Pain Medicine, Anesthesia and Pain Research Institute, Yonsei University College of Medicine, Seoul, Korea.Ohtahara syndrome (OS) is a rare epileptic encephalopathy that is characterized by an abnormal electroencephalogram (EEG) and intractable seizures in the neonatal and early infantile period. The patient of this reported case was delivered normally at 39 weeks of gestation without any complication. One week after birth, seizures that were refractory to anticonvulsants started with repetitive clustered tonic spasms. The child had no abnormal findings on the initial laboratory investigations. But he was diagnosed with OS according to the frequent tonic spasms, an abnormal EEG pattern of suppression-burst and magnetic resonance imaging of cortical dysplasia. He was planned to undergo an operation for brain lesion. This report describes our experience with the general anesthetic management when we performed craniotomy and right hemispherotomy for a patient with OS.http://ekja.org/upload/pdf/kjae-60-124.pdfinfantile epileptic syndromeohtahara syndromesuppression-burst
spellingShingle Eun Mi Choi
Kyeong Tae Min
Jin Sun Cho
Seung Ho Choi
Anesthetic experience of a patient with Ohtahara syndrome -A case report-
Korean Journal of Anesthesiology
infantile epileptic syndrome
ohtahara syndrome
suppression-burst
title Anesthetic experience of a patient with Ohtahara syndrome -A case report-
title_full Anesthetic experience of a patient with Ohtahara syndrome -A case report-
title_fullStr Anesthetic experience of a patient with Ohtahara syndrome -A case report-
title_full_unstemmed Anesthetic experience of a patient with Ohtahara syndrome -A case report-
title_short Anesthetic experience of a patient with Ohtahara syndrome -A case report-
title_sort anesthetic experience of a patient with ohtahara syndrome a case report
topic infantile epileptic syndrome
ohtahara syndrome
suppression-burst
url http://ekja.org/upload/pdf/kjae-60-124.pdf
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AT seunghochoi anestheticexperienceofapatientwithohtaharasyndromeacasereport