Diagnosis of Idiopathic Pulmonary Fibrosis: Differential Diagnosis
Idiopathic pulmonary fibrosis (IPF) is a chronic, progressive, and fibrotic interstitial lung disease of unknown origin with a characteristic imaging and histologic pattern called usual interstitial pneumonia (UIP). The diagnosis of IPF is a complex procedure that requires the support of various spe...
| Main Authors: | , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
MDPI AG
2018-09-01
|
| Series: | Medical Sciences |
| Subjects: | |
| Online Access: | http://www.mdpi.com/2076-3271/6/3/73 |
| _version_ | 1819116141364117504 |
|---|---|
| author | Myriam Aburto Inmaculada Herráez David Iturbe Ana Jiménez-Romero |
| author_facet | Myriam Aburto Inmaculada Herráez David Iturbe Ana Jiménez-Romero |
| author_sort | Myriam Aburto |
| collection | DOAJ |
| description | Idiopathic pulmonary fibrosis (IPF) is a chronic, progressive, and fibrotic interstitial lung disease of unknown origin with a characteristic imaging and histologic pattern called usual interstitial pneumonia (UIP). The diagnosis of IPF is a complex procedure that requires the support of various specialists, who must integrate clinical, radiological, and histological data. The multidisciplinary team (MDT) has become the new gold standard to diagnose and manage the disease, increasing the accuracy and agreement of the diagnosis between different centers. It is mandatory to exclude nonspecific interstitial pneumonia or other diseases that can cause the UIP pattern, particularly drugs or exposure diseases, including chronic hypersensitivity pneumonitis or systemic autoimmune disease. The role of the MDT is also to decide who could need a biopsy or to review patient diagnoses at regular intervals in those with additional information or unexpected evolution. This review provides updated information to achieve a proper IPF diagnosis. |
| first_indexed | 2024-12-22T05:12:22Z |
| format | Article |
| id | doaj.art-14cf2a533de54f3281da4405645dddaa |
| institution | Directory Open Access Journal |
| issn | 2076-3271 |
| language | English |
| last_indexed | 2024-12-22T05:12:22Z |
| publishDate | 2018-09-01 |
| publisher | MDPI AG |
| record_format | Article |
| series | Medical Sciences |
| spelling | doaj.art-14cf2a533de54f3281da4405645dddaa2022-12-21T18:37:57ZengMDPI AGMedical Sciences2076-32712018-09-01637310.3390/medsci6030073medsci6030073Diagnosis of Idiopathic Pulmonary Fibrosis: Differential DiagnosisMyriam Aburto0Inmaculada Herráez1David Iturbe2Ana Jiménez-Romero3Department of Respiratory Medicine, Galdakao Hospital, 48960 Galdako, SpainDepartment of Radiology, University Hospital of León, 24071 León, SpainDepartment of Respiratory Medicine, Marques de Valdecilla University Hospital, 39008 Santander, SpainDepartment of Respiratory Medicine, El Bierzo Hospital, 24404 Ponferrada, SpainIdiopathic pulmonary fibrosis (IPF) is a chronic, progressive, and fibrotic interstitial lung disease of unknown origin with a characteristic imaging and histologic pattern called usual interstitial pneumonia (UIP). The diagnosis of IPF is a complex procedure that requires the support of various specialists, who must integrate clinical, radiological, and histological data. The multidisciplinary team (MDT) has become the new gold standard to diagnose and manage the disease, increasing the accuracy and agreement of the diagnosis between different centers. It is mandatory to exclude nonspecific interstitial pneumonia or other diseases that can cause the UIP pattern, particularly drugs or exposure diseases, including chronic hypersensitivity pneumonitis or systemic autoimmune disease. The role of the MDT is also to decide who could need a biopsy or to review patient diagnoses at regular intervals in those with additional information or unexpected evolution. This review provides updated information to achieve a proper IPF diagnosis.http://www.mdpi.com/2076-3271/6/3/73idiopathic pulmonary fibrosis lower caseusual interstitial pneumoniaeidiopathic interstitial pneumoniasurgical lung biopsytransbronchial cryobiopsydiagnosishigh-resolution computed tomographymultidisciplinary team |
| spellingShingle | Myriam Aburto Inmaculada Herráez David Iturbe Ana Jiménez-Romero Diagnosis of Idiopathic Pulmonary Fibrosis: Differential Diagnosis Medical Sciences idiopathic pulmonary fibrosis lower case usual interstitial pneumoniae idiopathic interstitial pneumonia surgical lung biopsy transbronchial cryobiopsy diagnosis high-resolution computed tomography multidisciplinary team |
| title | Diagnosis of Idiopathic Pulmonary Fibrosis: Differential Diagnosis |
| title_full | Diagnosis of Idiopathic Pulmonary Fibrosis: Differential Diagnosis |
| title_fullStr | Diagnosis of Idiopathic Pulmonary Fibrosis: Differential Diagnosis |
| title_full_unstemmed | Diagnosis of Idiopathic Pulmonary Fibrosis: Differential Diagnosis |
| title_short | Diagnosis of Idiopathic Pulmonary Fibrosis: Differential Diagnosis |
| title_sort | diagnosis of idiopathic pulmonary fibrosis differential diagnosis |
| topic | idiopathic pulmonary fibrosis lower case usual interstitial pneumoniae idiopathic interstitial pneumonia surgical lung biopsy transbronchial cryobiopsy diagnosis high-resolution computed tomography multidisciplinary team |
| url | http://www.mdpi.com/2076-3271/6/3/73 |
| work_keys_str_mv | AT myriamaburto diagnosisofidiopathicpulmonaryfibrosisdifferentialdiagnosis AT inmaculadaherraez diagnosisofidiopathicpulmonaryfibrosisdifferentialdiagnosis AT daviditurbe diagnosisofidiopathicpulmonaryfibrosisdifferentialdiagnosis AT anajimenezromero diagnosisofidiopathicpulmonaryfibrosisdifferentialdiagnosis |