Genetic atypical hemolytic uremic syndrome in children: a 20-year experience from a tertiary center

Genetic atypical hemolytic uremic syndrome in children: a 20-year experience from a tertiary center

Abstract Introduction: Atypical hemolytic uremic syndrome (aHUS) is a rare disorder characterized by the triad of microangiopathic hemolytic anemia, thrombocytopenia, and acute kidney injury, which primarily affects preschool-aged children. This study’s aim was to describe the clinical profile, man...

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Bibliographic Details
Main Authors:	Cristiana Maximiano, Andreia Silva, Inês Duro, Tiago Branco, Liane Correia-Costa, Ana Teixeira, Liliana Rocha, Teresa Costa, Paula Matos, Maria do Sameiro Faria, Conceição Mota, Alberto Caldas Afonso
Format:	Article
Language:	English
Published:	Sociedade Brasileira de Nefrologia 2021-05-01
Series:	Brazilian Journal of Nephrology
Subjects:	Atypical Hemolytic Uremic Syndrome Child Genetic Testing Thrombotic Microangiopathies
Online Access:	http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0101-28002021000300311&tlng=en

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