Proteinose alveolar congénita.
Pulmonary Alveolar Proteinosis (PAP) is a rare entity characterized by the intra-alveolar accumulation of proteinaceous PAS positive and diastase resistant material. Its pathogenesis remains unclear, although a surfactant protein B deficiency and changes in the granulocyte-macrophage colony stimulat...
Main Authors: | , , , |
---|---|
Format: | Article |
Language: | English |
Published: |
Ordem dos Médicos
2005-04-01
|
Series: | Acta Médica Portuguesa |
Online Access: | https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/1009 |