Unilateral hypertrophic skin lesions, hemimegalencephaly, and meningioma: The many faces of Proteus syndrome
Proteus syndrome is a rare condition with a wide spectrum of abnormalities. It is characterized by hamartomatous malformations involving multiple organs. Serious complications may ensue, such as pulmonary embolism, cystic lung disease, and various neoplasms such as parotid adenomas, ovarian cystaden...
| Main Authors: | , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2015-01-01
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| Series: | Indian Dermatology Online Journal |
| Subjects: | |
| Online Access: | http://www.idoj.in/article.asp?issn=2229-5178;year=2015;volume=6;issue=5;spage=348;epage=351;aulast=Lal |
| _version_ | 1818959934207819776 |
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| author | Niharika R Lal Debabrata Bandyopadhyay Asim K Sarkar |
| author_facet | Niharika R Lal Debabrata Bandyopadhyay Asim K Sarkar |
| author_sort | Niharika R Lal |
| collection | DOAJ |
| description | Proteus syndrome is a rare condition with a wide spectrum of abnormalities. It is characterized by hamartomatous malformations involving multiple organs. Serious complications may ensue, such as pulmonary embolism, cystic lung disease, and various neoplasms such as parotid adenomas, ovarian cystadenomas, and meningiomas. We report here a case of Proteus syndrome in a 21-year-old woman who had facial hemihypertrophy, cerebriform plantar hyperplasia, hemimegalencephaly, and meningioma for the rarity of the entity. |
| first_indexed | 2024-12-20T11:49:31Z |
| format | Article |
| id | doaj.art-15a3d4d093d44089b22cdd93d4a12fb5 |
| institution | Directory Open Access Journal |
| issn | 2229-5178 |
| language | English |
| last_indexed | 2024-12-20T11:49:31Z |
| publishDate | 2015-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Indian Dermatology Online Journal |
| spelling | doaj.art-15a3d4d093d44089b22cdd93d4a12fb52022-12-21T19:41:49ZengWolters Kluwer Medknow PublicationsIndian Dermatology Online Journal2229-51782015-01-016534835110.4103/2229-5178.164477Unilateral hypertrophic skin lesions, hemimegalencephaly, and meningioma: The many faces of Proteus syndromeNiharika R LalDebabrata BandyopadhyayAsim K SarkarProteus syndrome is a rare condition with a wide spectrum of abnormalities. It is characterized by hamartomatous malformations involving multiple organs. Serious complications may ensue, such as pulmonary embolism, cystic lung disease, and various neoplasms such as parotid adenomas, ovarian cystadenomas, and meningiomas. We report here a case of Proteus syndrome in a 21-year-old woman who had facial hemihypertrophy, cerebriform plantar hyperplasia, hemimegalencephaly, and meningioma for the rarity of the entity.http://www.idoj.in/article.asp?issn=2229-5178;year=2015;volume=6;issue=5;spage=348;epage=351;aulast=LalCollagenomahemimegalencephalymeningiomaProteus syndrome |
| spellingShingle | Niharika R Lal Debabrata Bandyopadhyay Asim K Sarkar Unilateral hypertrophic skin lesions, hemimegalencephaly, and meningioma: The many faces of Proteus syndrome Indian Dermatology Online Journal Collagenoma hemimegalencephaly meningioma Proteus syndrome |
| title | Unilateral hypertrophic skin lesions, hemimegalencephaly, and meningioma: The many faces of Proteus syndrome |
| title_full | Unilateral hypertrophic skin lesions, hemimegalencephaly, and meningioma: The many faces of Proteus syndrome |
| title_fullStr | Unilateral hypertrophic skin lesions, hemimegalencephaly, and meningioma: The many faces of Proteus syndrome |
| title_full_unstemmed | Unilateral hypertrophic skin lesions, hemimegalencephaly, and meningioma: The many faces of Proteus syndrome |
| title_short | Unilateral hypertrophic skin lesions, hemimegalencephaly, and meningioma: The many faces of Proteus syndrome |
| title_sort | unilateral hypertrophic skin lesions hemimegalencephaly and meningioma the many faces of proteus syndrome |
| topic | Collagenoma hemimegalencephaly meningioma Proteus syndrome |
| url | http://www.idoj.in/article.asp?issn=2229-5178;year=2015;volume=6;issue=5;spage=348;epage=351;aulast=Lal |
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