IgA Vasculitis involving four systems
Henoch-Schonlein Purpura (HSP) is a systemic vasculitis that infrequently occurs in adults. While rheumatological and gastrointestinal complications are common, lung involvement is a rare complication. We report the case of a 70 year-old female that presented to the hospital with purpuric lesions o...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Sociedade Galega de Medicina Interna
2022-12-01
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| Series: | Galicia Clínica |
| Subjects: | |
| Online Access: | https://galiciaclinica.info/publicacion.asp?f=2633 |
| _version_ | 1828056210094424064 |
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| author | Joana Diogo Carolina Coelho Rita Monteiro Ângela Ghiletchi |
| author_facet | Joana Diogo Carolina Coelho Rita Monteiro Ângela Ghiletchi |
| author_sort | Joana Diogo |
| collection | DOAJ |
| description | Henoch-Schonlein Purpura (HSP) is a systemic vasculitis that infrequently occurs in adults.
While rheumatological and gastrointestinal complications are common, lung involvement is a rare complication. We report the case of a 70 year-old female that presented to the hospital with purpuric lesions on her legs. During her hospital stay she developed respiratory distress, and the computed tomography (CT) scan showed evidence of Diffuse Alveolar Hemorrhage (DAH). She also had renal dysfunction, and the renal biopsy confirmed the presence of leukocytoclastic vasculitis on histology, consistent with HSP. The patient was initiated on steroids, in addition to supportive management, leading to the resolution of her symptoms.
This case is unique, as it presents a rare complication of HSP, with pulmonary disease, causing DAH. Furthermore, adult onset HSP is also an uncommon occurrence.
It is very important to recognize DAH early in HSP, as it holds a high mortality rate. |
| first_indexed | 2024-04-10T20:52:01Z |
| format | Article |
| id | doaj.art-171d00d7c8284a848267451e6c5c62ab |
| institution | Directory Open Access Journal |
| issn | 0304-4866 1989-3922 |
| language | English |
| last_indexed | 2024-04-10T20:52:01Z |
| publishDate | 2022-12-01 |
| publisher | Sociedade Galega de Medicina Interna |
| record_format | Article |
| series | Galicia Clínica |
| spelling | doaj.art-171d00d7c8284a848267451e6c5c62ab2023-01-23T09:15:37ZengSociedade Galega de Medicina InternaGalicia Clínica0304-48661989-39222022-12-01834485010.22546/67/26332633IgA Vasculitis involving four systemsJoana Diogo0Carolina Coelho1Rita Monteiro2Ângela Ghiletchi3Centro Hospitalar Universitário Lisboa CentralCentro Hospitalar Universitário Lisboa CentralCentro Hospitalar Universitário Lisboa CentralCentro Hospitalar Universitário Lisboa CentralHenoch-Schonlein Purpura (HSP) is a systemic vasculitis that infrequently occurs in adults. While rheumatological and gastrointestinal complications are common, lung involvement is a rare complication. We report the case of a 70 year-old female that presented to the hospital with purpuric lesions on her legs. During her hospital stay she developed respiratory distress, and the computed tomography (CT) scan showed evidence of Diffuse Alveolar Hemorrhage (DAH). She also had renal dysfunction, and the renal biopsy confirmed the presence of leukocytoclastic vasculitis on histology, consistent with HSP. The patient was initiated on steroids, in addition to supportive management, leading to the resolution of her symptoms. This case is unique, as it presents a rare complication of HSP, with pulmonary disease, causing DAH. Furthermore, adult onset HSP is also an uncommon occurrence. It is very important to recognize DAH early in HSP, as it holds a high mortality rate.https://galiciaclinica.info/publicacion.asp?f=2633purpura henoch–schönleinadultohemorragia alveolar difusaterapia con corticosteroidesvasculitis |
| spellingShingle | Joana Diogo Carolina Coelho Rita Monteiro Ângela Ghiletchi IgA Vasculitis involving four systems Galicia Clínica purpura henoch–schönlein adulto hemorragia alveolar difusa terapia con corticosteroides vasculitis |
| title | IgA Vasculitis involving four systems |
| title_full | IgA Vasculitis involving four systems |
| title_fullStr | IgA Vasculitis involving four systems |
| title_full_unstemmed | IgA Vasculitis involving four systems |
| title_short | IgA Vasculitis involving four systems |
| title_sort | iga vasculitis involving four systems |
| topic | purpura henoch–schönlein adulto hemorragia alveolar difusa terapia con corticosteroides vasculitis |
| url | https://galiciaclinica.info/publicacion.asp?f=2633 |
| work_keys_str_mv | AT joanadiogo igavasculitisinvolvingfoursystems AT carolinacoelho igavasculitisinvolvingfoursystems AT ritamonteiro igavasculitisinvolvingfoursystems AT angelaghiletchi igavasculitisinvolvingfoursystems |